Uvavanyo lweHemoglobinuria

Uvavanyo lwe-Hemoglobinuria luvavanyo lomchamo olujonga i-hemoglobin kumchamo.

Isampulu yomchamo ococekileyo iyafuneka. Indlela yokubambisa ecocekileyo isetyenziselwa ukunqanda iintsholongwane ezivela kwilungu lobudoda okanye kwilungu lobufazi ekungeneni kwisampulu yomchamo. Ukuqokelela umchamo wakho, unokufumana ikiti yokubamba ecocekileyo ekhethekileyo evela kumboneleli wakho wezempilo enesisombululo sokucoca kunye nokusula okunyumba. Landela imiyalelo ngokuchanekileyo ukuze iziphumo zichaneke.

Akukho lungiselelo lukhethekileyo luyimfuneko kolu vavanyo. Ukuba ingqokelela ithathwa kusana, iibhegi ezimbalwa zokuqokelela zinokufuneka.

Uvavanyo lubandakanya kuphela ukuchama okuqhelekileyo. Akukho buhlungu.

IHemoglobin yimolekyuli eqhotyoshelwe kwiiseli ezibomvu zegazi. IHemoglobin inceda ukuhambisa ioksijini kunye nekhabhon dioksi emzimbeni.

Iiseli ezibomvu zegazi zinobomi obuqhelekileyo beentsuku ezili-120. Emva kweli xesha, baqhekezwa baba ziinxalenye ezinokwenza iseli ebomvu ebomvu. Oku kuqhekeka kwenzeka kwipeni, umongo wethambo, kunye nesibindi. Ukuba iiseli ezibomvu zegazi ziyehla kwimithambo yegazi, iinxalenye zazo zihamba ngokukhululekileyo kwigazi.

Ukuba inqanaba lehemoglobin egazini liphezulu kakhulu, ihemoglobin iqala ukubonakala kumchamo. Oku kubizwa ngokuba yihemoglobinuria.

Olu vavanyo lunokusetyenziselwa ukunceda ekuchongeni izizathu ze-hemoglobinuria.

Ngokwesiqhelo, ihemoglobin ayiveli kumchamo.

IHemoglobinuria inokuba sisiphumo sayo nayiphi na kwezi zinto zilandelayo:

• Ukuphazamiseka kwizintso okubizwa ngokuba yi-acute glomerulonephritis
• Ukutsha
• Ukutyumza ukwenzakala
• I-hemolytic uremic syndrome (HUS), isifo esenzeka xa usulelo kwinkqubo yokwetyisa luvelisa izinto ezinetyhefu
• Usulelo lwezintso
• Ithumba lezintso
• Isifo seengcongconi
• I-Paroxysmal nocturnal hemoglobinuria, isifo apho iiseli ezibomvu zegazi zehla ngaphambi kwexesha eliqhelekileyo
• I-Paroxysmal cold hemoglobinuria, isifo apho amajoni omzimba avelisa izilwa-buhlungu ezitshabalalisa iiseli ezibomvu zegazi
• Isifo seanemia
• I-Thalassemia, isifo apho umzimba wenza ifom engaqhelekanga okanye inani elaneleyo le-hemoglobin
• I-Thrombotic thrombocytopenic purpura (TTP)
• Ukusabela kotofelo
• Isifo sephepha

Umchamo - hemoglobin

• Isampuli yomchamo

Landry DW, Bazari H. Indlela eya kwisigulana esinesifo sezintso. Ku: IGoldman L, iSchafer AI, ii-eds. Amayeza eGoldman-Cecil. Ngomhla wama-26. IPhiladelphia, PA: Elsevier; 2020: isahluko 106.

URiley RS, uMcPherson RA. Uvavanyo olusisiseko lomchamo. Ku: McPherson RA, Pincus MR, ii-eds. Ukuchongwa kweKlinikhi kaHenry kunye noLawulo ngeendlela zeLebhu. Umhla we-23. ISt Louis, MO: Elsevier; Ngo-2017: isahluko 28.