Isifo somntu esiqinileyo

Umxholo

• Iimpawu
• Unyango

Kwisifo esingqongqo somntu, umntu unokuba ngqongqo kakhulu ezinokuzibonakalisa emzimbeni wonke okanye kwimilenze kuphela, umzekelo. Xa ezi zichaphazelekayo, umntu unokuhamba njengejoni kuba akakwazi ukushukumisa izihlunu namalungu akhe kakuhle.

Esi sisifo esizenzekelayo esihlala sibonakalisa phakathi kweminyaka engama-40 nengama-50 ubudala kwaye sikwabizwa ngokuba sisifo seMersch-Woltmann okanye ngesiNgesi, iStiff-man syndrome. Kuphela malunga ne-5% yamatyala enzeka ebuntwaneni okanye ebusheni.

Isifo esiqinileyo somntu sinokubonakalisa ngeendlela ezi-6 ezahlukeneyo:

1. Ifom yeklasi apho ichaphazela kuphela ummandla we-lumbar kunye nemilenze;
2. Uhlobo olwahlukileyo xa lilinganiselwe kwilungu elinye nje elinendawo yokuma okanye yokubuyela umva;
3. Uhlobo oluqhelekileyo xa ukuqina kwenzeka kuwo wonke umzimba ngenxa ye-encephalomyelitis ezenzekelayo;
4. Xa kukho ukuphazamiseka kwentshukumo esebenzayo;
5. Nge-dystonia kunye neparkinsonism ngokubanzi kunye
6. Ngofuzo lwe-spastic paraparesis.

Ngokwesiqhelo umntu onalesi sifo akanayo kuphela esi sifo, kodwa unezinye izifo ezizimelayo ezinje ngohlobo lweswekile 1, isifo sedlala lengqula okanye i-vitiligo, umzekelo.

Esi sifo sinokunyangeka ngonyango oluboniswe ngugqirha kodwa unyango lungatya ixesha.

Iimpawu

Iimpawu zesifo somntu esiqinileyo ziqatha kwaye zibandakanya:

• Ukuqhubela phambili kwezihlunu zemisipha ezinesivumelwano esincinci kwimisipha ethile ngaphandle kokuba umntu abe nakho ukulawula, kunye
• Ukuqina okuphawulweyo kwezihlunu ezinokubangela ukophuka kwemicu yemisipha, ukususwa kunye nokuqhekeka kwethambo.

Ngenxa yezi mpawu umntu unokuba ne-hyperlordosis kunye neentlungu kumqolo, ngakumbi xa izihlunu zangasemva zichaphazelekile kwaye zinokuwa rhoqo ngenxa yokuba engakwazi ukuhamba nokulinganisa ngokufanelekileyo.

Ukuqina kokuqina kwemisipha kuhlala kuvela emva kwexesha loxinzelelo njengomsebenzi omtsha okanye ukwenza imisebenzi esidlangalaleni, kwaye ukuqina kwemisipha akwenzeki ngexesha lokulala kunye neziphene ezingalweni nasemilenzeni zixhaphakile ngenxa yobukho bezi spasms, ukuba isifo asinyangwa.

Ngaphandle kokonyuka kwethoni yemisipha kwimimandla echaphazelekayo, i-tendon reflexes ziqhelekile kwaye ke isifo singenziwa kuvavanyo lwegazi olujonga ii-antibodies ezithile kunye ne-electromyography. I-X-ray, ii-MRIs kunye ne-CT scan kufuneka zi-odolwe ukuba zingabandakanyi ukubakho kwezinye izifo.

Unyango

Unyango lomntu oqinileyo kufuneka lwenziwe ngokusetyenziswa kweziyobisi ezinje nge-baclofen, vecuronium, immunoglobulin, gabapentin kunye ne-diazepam eboniswe yi-neurologist. Ngamanye amaxesha, kunokuba yimfuneko ukuhlala e-ICU ukuze kuqinisekiswe ukusebenza kakuhle kwemiphunga nentliziyo ngexesha lesifo kwaye ixesha lonyango lingahluka ukusuka kwiiveki ukuya kwiinyanga.

Ukufakwa kwegazi kunye nokusetyenziswa kwe-anti-CD20 monoclonal antibody (rituximab) nayo ingabonakaliswa kwaye ibe neziphumo ezilungileyo. Uninzi lwabantu olufunyenwe sesi sifo luyanyangeka xa lufumana unyango.