Umbhali: Charles Brown
Umhla Wokudalwa: 2 Eyomdumba 2021
Hlaziya Umhla: 15 Eyethupha 2025
Anonim
Isifo seMaffucci - Zempilo
Isifo seMaffucci - Zempilo

Umxholo

Isifo seMaffucci sisifo esinqabileyo esichaphazela ulusu kunye namathambo, sibangela amathumba kwi-cartilage, ukukhubazeka emathanjeni kunye nokubonakala kwamathumba amnyama esikhumbeni okubangelwa kukukhula ngokungaqhelekanga kwemithambo yegazi.

Kwi Unobangela wesifo seMaffucci zizofuzo kwaye zichaphazela amadoda nabafazi ngokulinganayo. Ngokubanzi, iimpawu zesifo zikhula ebuntwaneni malunga neminyaka emi-4-5 ubudala.

THE Isifo sikaMaffucci asinyangi, nangona kunjalo, abaguli banokufumana unyango ukunciphisa iimpawu zesi sifo kunye nokuphucula umgangatho wobomi babo.

Iimpawu zeMaffucci Syndrome

Iimpawu eziphambili zeMaffucci syndrome zezi:

  • Izilonda zeBenign kwi-cartilage yezandla, iinyawo kunye namathambo amade engalo nemilenze;
  • Amathambo aba buthathaka kwaye anokuqhekeka ngokulula;
  • Ukunciphisa amathambo;
  • Hemangiomas, ezibandakanya amathumba amnyama amnyama okanye aluhlaza eluswini;
  • Mfutshane;
  • Ukungabikho kwemisipha.

Abantu abane-Maffucci Syndrome banokuhlakulela umhlaza wamathambo, ngakumbi kwikakayi, kodwa nakwi-ovarian okanye umhlaza wesibindi.


O ukuxilongwa kwesifo iMaffucci kwenziwa ngokuhlolwa komzimba kunye nohlalutyo lweempawu ezibonakaliswa zizigulana.

Unyango lweMaffucci's Syndrome

Unyango lwe-Maffucci's Syndrome luquka ukunciphisa iimpawu zesi sifo ngotyando ukulungisa iziphene zamathambo okanye izongezo ukunceda ukukhula komntwana.

Abantu abachaphazeleka sesi sifo kufuneka babonane rhoqo nogqirha wamathambo ukuvavanya utshintsho emathanjeni, ukukhula komhlaza wethambo kunye nokunyanga ukwaphuka okwenzeka ngenxa yesi sifo. Ugqirha wesikhumba kufuneka abonisane naye ukuvavanya inkangeleko kunye nokukhula kwe-hemangiomas kulusu.

Kubalulekile ukuba izigulana zenze iimviwo zomzimba rhoqo, iiradiografi okanye iikhompyuter zeskena sekhompyuter.

Imifanekiso yeMaffucci's Syndrome

Umthombo:Amaziko oLawulo lweZifo noThintelo

Ifoto 1: Ubukho bamathumba amancinci kumalungu eminwe abonakala ngayo eMaffucci's Syndrome;


Ifoto yesi-2: IHemangioma kulusu lwesigulana esineMaffucci syndrome.

Ikhonkco eliluncedo:

  • IHemangioma
  • IProteus Syndrome

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