Yintoni kunye nendlela yokuchonga isifo se-Ohtahara

Umxholo

• Indlela yokuqinisekisa ukuxilongwa
• Unyango lwenziwa njani
• Yintoni ebangela isifo

I-Ohtahara syndrome luhlobo olunqabileyo lwesifo sokuwa esihlala sivela kwiintsana ezingaphantsi kweenyanga ezintathu ubudala, kwaye ke ikwabizwa ngokuba yi-infantile epileptic encephalopathy.

Ukuxhuzula kokuqala kolu hlobo lokuxhuzula kuhlala kwenzeka kwinyanga ezintathu zokugqibela zokukhulelwa, kusesesibelekweni, kodwa kunokubonakala ngeentsuku ezili-10 zokuqala zobomi bosana, zibonakaliswa yimisipha engazibandakanyiyo eshiya imilenze neengalo ziqinile imizuzwana ethile.

Nangona lungekho unyango, unyango lunokwenziwa ngokusetyenziswa kwamachiza, i-physiotherapy kunye nokutya okwaneleyo ukuthintela ukuqala kweengxaki kunye nokuphucula umgangatho wobomi bomntwana.

Indlela yokuqinisekisa ukuxilongwa

Ngamanye amaxesha isifo sika-Ohtahara sinokuchongwa ngugqirha wezilwanyana kuphela ngokujonga iimpawu kunye nokuvavanya imbali yomntwana.

Nangona kunjalo, ugqirha unokuyalela i-electroencephalogram, eluvavanyo olungenabuhlungu, olulinganisa ukusebenza kwengqondo ngexesha lokubanjwa. Funda ngakumbi malunga nokuba olu vavanyo lwenziwa njani.

Unyango lwenziwa njani

Uhlobo lokuqala lonyango oluboniswe ngugqirha wabantwana, ngesiqhelo, kukusetyenziswa kwamayeza alwa nesathuthwane, afana neClonazepam okanye iTopiramate, ukuzama ukulawula ukuqala kweengxaki, nangona kunjalo, la mayeza angabonisa iziphumo ezincinci kwaye, ke, zisacetyiswa ezinye iindlela zonyango, kubandakanya:

• Ukusetyenziswa kwecorticosteroids, kunye ne-corticotrophin okanye i-prednisone: ukunciphisa inani lokuxhuzula kwabanye abantwana;
• Utyando lwesifo sokuwa: isetyenziswa ebantwaneni apho ukuxhuzula kubangelwa yindawo ethile yengqondo kwaye kwenziwa ngokususwa kwaloo ndawo, okoko nje kungabalulekanga ekusebenzeni kwengqondo;
• Ukutya ukutya kwe ketogenic: inokusetyenziswa kuwo onke amatyala ukuncedisana nonyango kwaye kubandakanya ukuphelisa ukutya okunee-carbohydrate ekutyeni, okunje ngesonka okanye ipasta, ukuze kulawulwe ukuqala kokubanjwa. Jonga okokutya kuvunyelwe kwaye kungavunyelwe kolu hlobo lokutya.

Nangona unyango lubaluleke kakhulu ekuphuculeni umgangatho wobomi bomntwana, zininzi iimeko apho isifo sika-Ohtahara siba mandundu ngokuhamba kwexesha, sibangela ukulibaziseka ekukhuleni kwengqondo kunye nophuhliso lweemoto. Ngenxa yolu hlobo lweengxaki, ixesha lokuphila liphantsi, malunga neminyaka emi-2.

Yintoni ebangela isifo

Unobangela wesifo sika-Ohtahara kunzima ukufumanisa kwiimeko ezininzi, nangona kunjalo, izinto ezimbini eziphambili ezibonakala ngathi zivela kwimvelaphi yesi sifo kukutshintsha kwemfuza ngexesha lokukhulelwa nokungalunganga kwengqondo.

Ke, ukuzama ukunciphisa umngcipheko wolu hlobo lwesifo, umntu kufuneka aphephe ukukhulelwa emva kweminyaka eyi-35 kwaye alandele zonke iingcebiso zikagqirha, ezinjengokuphepha ukusela utywala, ukungatshayi, ukuthintela ukusetyenziswa kwamachiza anganyanzelwanga kunye nokuthatha inxaxheba. kuthethwano lwaphambi kokubeleka, umzekelo. Qonda zonke izizathu ezinokukhokelela ekukhulelweni okuyingozi.