Iimpawu zePulmonary Arterial Hypertension
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Umxholo
- Ukulibaziseka kweempawu
- Ukuqonda iimpawu zokuqala
- Ukuqhawukelwa ngumphefumlo
- Ukudinwa kunye nesiyezi
- Ukudumba kwamalungu
- Imilebe eblue
- Ukubetha kwentliziyo kunye nesifuba esingaqhelekanga
- Iimpawu ezahlukileyo zabantu abahlukeneyo
- Thetha nogqirha wakho
Uxinzelelo lwegazi lwe-pulmonary arterial
Uxinzelelo lwegazi lwe-pulmonary arterial (PAH) luhlobo olunqabileyo loxinzelelo lwegazi oluphezulu. Iyenzeka kwimithambo yemiphunga, ephuma entliziyweni yakho nasemiphungeni yakho yonke.
Imithambo ethintelweyo kunye nemxinwa ithintela intliziyo yakho ekumpomeni igazi elaneleyo. Xa ukuqina kwenzeka, intliziyo kuya kufuneka isebenze nzima ukubuyekeza. Oku kubangela uxinzelelo lwegazi kwimithambo yemiphunga kunye nasentliziyweni ukunyuka okumangalisayo.
Njengoko imeko iya isiba mandundu kwaye uxinzelelo luba lukhulu, unokuqala ukufumana iimpawu neempawu ezahlukeneyo.
Ukulibaziseka kweempawu
Kungathatha iinyanga, nokuba yiminyaka, ngaphambi kokuba imithambo kunye nokuxinana kwimithambo kube nzima ngokwaneleyo ukuba uxinzelelo olubonakalayo luqale ukwakha. Ngenxa yeso sizathu, i-PAH inokuqhubela phambili iminyaka eliqela ngaphambi kokuba iimpawu zibonakale.
Iimpawu ze-PAH nazo azichongi ngokukhawuleza ukuba zibangelwa yi-PAH. Ngamanye amagama, uninzi lweempawu ziqhelekile kwezinye iimeko. Okubi nangakumbi kukuba ungabakhupha ngokulula, njengoko bekhula kancinci ngokuthe chu, kunokuba bakhawuleze. Oku kwenza ukuba kube lula ukuxilongwa.
Ukuqonda iimpawu zokuqala
Iimpawu zokuqala ze-PAH, ngakumbi ukuphefumla kancinci kunye nokudinwa, kunokukwenza ukuba ucinge ukuba uphelelwe yimilo nje. Emva kwayo yonke loo nto, akuqhelekanga ukuphuma kumoya emva kokukhwela kwizitepsi ezininzi, nokuba ubusebenza ngokomzimba yonke imihla. Ngenxa yeso sizathu, abantu abaninzi abazihoyi iimpawu ze-PAH kwaye bayeke isifo siqhubeke ngaphandle konyango. Oku kwenza imeko ibe mandundu kwaye inokubulala.
Ukuqhawukelwa ngumphefumlo
Olunye lweempawu zokuqala ze-PAH unokuzibona ukuphefumla okufutshane. Imithambo kunye nemithambo yegazi ethwala igazi lingene ngemiphunga lenza ukuba kuphefumle kube lula. Inkqubo ye-inhale-exhale ikunceda ukhawuleze ungenise umoya otyebileyo we-oksijini kwaye ukhuphe umoya ophelileyo we-oxygen. I-PAH inokwenza ukuba inkqubo ehlelwe kakuhle ibe nzima ngakumbi, kwaye isebenze. Imisebenzi ebikade ilula- ukunyuka izinyuko, ukuhamba ibhloko, ukucoca indlu- kunokuba nzima ngakumbi kwaye kukushiye uphefumla ngokukhawuleza.
Ukudinwa kunye nesiyezi
Xa imiphunga yakho ingakwazi ukufumana igazi elaneleyo ukuba lisebenze ngokufanelekileyo, oko kuthetha ukuba umzimba wakho nengqondo yakho ayifumani oksijini yaneleyo nayo. Umzimba wakho udinga ioksijini ukwenza yonke imisebenzi yawo. Ngaphandle kwayo, ngekhe uqhubeke ngesiqhelo. Imilenze yakho iya kudinwa ngokukhawuleza emva kokuhamba. Ingqondo yakho kunye nokuqhutywa kwengcinga kuya kubonakala ngathi kuhamba kancinci, kusebenza ngakumbi. Ngokubanzi, uya kuziva ukhathele ngaphambili kwaye ngokulula ngakumbi.
Ukungabikho kweoksijini kwingqondo kukonyusa umngcipheko wokuba nesiyezi okanye ukutyhafa (syncope).
Ukudumba kwamalungu
I-PAH inokubangela ukudumba, okanye i-edema, emaqatheni akho, emilenzeni nasezinyaweni. Ukudumba kwenzeka xa izintso zakho zingakwazi ukugungxula inkunkuma emzimbeni wakho. Ukugcinwa kolwelo kuya kusanda kusenokwenzeka ukuba une-PAH.
Imilebe eblue
Intliziyo yakho impompa iiseli ezibomvu ze-oksijini emzimbeni wakho ukunceda ukuhambisa yonke imisebenzi kunye nemisebenzi oyifunayo. Xa inani leoksijini kwiiseli zakho ezibomvu lingonelanga ngenxa ye-PAH, amalungu omzimba wakho awunakufumana ioksijini abayifunayo. Amanqanaba eoksijini asezantsi eluswini nasemilebeni kunokubangela umbala oluhlaza. Le meko ibizwa ngokuba yi-cyanosis.
Ukubetha kwentliziyo kunye nesifuba esingaqhelekanga
Ukunyuka koxinzelelo entliziyweni kwenza ukuba izihlunu zentliziyo zisebenze nzima kunokuba befanele. Ngokuhamba kwexesha, ezi zihlunu ziba buthathaka. Intliziyo ebuthathaka ayinakubetha ngokunjalo okanye rhoqo njengoko ibisenza njalo. Ekugqibeleni, oku kunokubangela ukubetha kwentliziyo okungalunganga, ukubetha komdyarho, okanye ukubetha kwentliziyo.
Ukunyusa uxinzelelo lwegazi entliziyweni kunye nemithambo kunokubangela iintlungu zesifuba okanye uxinzelelo. Intliziyo esebenze kakhulu inokubangela iintlungu zesifuba okanye uxinzelelo lwesifuba.
Iimpawu ezahlukileyo zabantu abahlukeneyo
Umntu ngamnye one-PAH uya kuba neempawu ezahlukileyo ezahlukeneyo. Ubukrakra beempawu ziya kwahluka kumntu nomntu. Uhambo lomntu omnye lokuba nokunyanga i-PAH akuyi kuba luncedo komnye umntu kuba indlela ene-PAH kunye nokhetho lonyango lubodwa.
Nangona kunjalo, unokufumana inkxaso kwabanye abane-PAH, ufunde kumava abo, kwaye ulolonge indlela yakho yokunyanga i-PAH ngokufanelekileyo. Funda ngakumbi ngamayeza asetyenziselwa ukunyanga i-PAH.
Thetha nogqirha wakho
Ugqirha wakho unokukunceda uchonge unobangela weempawu zakho.
Ugqirha wakho uyakukucela ukuba ufumane uthotho lweemvavanyo zokuphelisa ezinye zeemposiso ezingezizo ezichazwe apha ngasentla. Uya kuqala ngovavanyo lomzimba, i-X-ray yesifuba, uvavanyo lwegazi, i-electrocardiogram (ECG), kunye ne-echocardiogram. Ukuba barhanela i-PAH, kuya kuthi ke kunikwe olunye uthotho lweemvavanyo ukuze kuchongwe imeko ngokuchanekileyo.
Musa ukulinda ukuba ufumana iimpawu ze-PAH. Ngokude ulinde, ezi zimpawu zinokuba zibi kakhulu. Ekugqibeleni, i-PAH inokukuthintela ekwenzeni yonke imisebenzi yomzimba. Iimpawu ezongezelelweyo ziba lula njengoko isifo siqhubeka.
Ukuba ufumana naziphi na kwezi mpawu okanye ukrokrela ukuba une-PAH, yenza idinga lokuya kugqirha. Ngokudibeneyo, ninokuchonga-kwaye nonyango-olu hlobo lunqabileyo loxinzelelo lwegazi.