Polycythemia - usana olusanda kuzalwa

I-Polycythemia inokwenzeka xa kukho iiseli ezibomvu zegazi (RBCs) ezininzi kwigazi lomntwana.

Ipesenti ye-RBCs egazini lomntwana ibizwa ngokuba yi "hematocrit." Xa oku kungaphezulu kwama-65%, i-polycythemia ikhona.

I-Polycythemia inokubangelwa ziimeko ezikhula ngaphambi kokuzalwa. Oku kunokubandakanya:

• Ukulibaziseka ekubambeni intambo
• Isifo seswekile kunina wokuzalwa komntwana
• Izifo ezizuze njengelifa kunye neengxaki zemfuza
• Ioksijini encinci kakhulu efikelela kwizicubu zomzimba (hypoxia)
• I-twin-twin syndrome (eyenzeka xa igazi lisuka kwelinye iwele liye kwelinye)

Ii-RBCs ezongezelelweyo zinokucothisa okanye zithintele ukuhamba kwegazi kweyona mithambo incinci yegazi. Oku kubizwa ngokuba yi-hyperviscosity. Oku kunokukhokelela ekufeni kwethishu ngenxa yokungabikho kweoksijini. Oku kuhamba kwegazi kuthintelwe kunokuchaphazela onke amalungu, kubandakanya izintso, imiphunga kunye nengqondo.

Iimpawu zingabandakanya:

• Ubuthongo obukhulu
• Iingxaki zokondla
• Ukuxhuzula

Kunokubakho iimpawu zokuphefumla, ukungaphumeleli kwezintso, iswekile esezantsi yegazi, okanye isifo sejaundice esisanda kuzalwa.

Ukuba umntwana uneempawu zehyperviscosity, kuya kwenziwa uvavanyo lwegazi ukubala inani lee-RBCs. Olu vavanyo lubizwa ngokuba yi-hematocrit.

Olunye uvavanyo lunokubandakanya:

• Iigesi zegazi ukujonga inqanaba leoksijini egazini
• Iswekile yegazi (iswekile) ukujonga iswekile esezantsi yegazi
• Igazi urea nitrogen (BUN), into eyenzekayo xa iprotein isophuka
• Uyilo
• Uhlalutyo lomchamo
• Bilirubin

Umntwana uya kubekwa esweni ngenxa yeengxaki zehyperviscosity. Ulwelo lunokunikwa ngomthambo. Ukongezwa kotshintshiselwano ngevolumu ngamanye amaxesha kusenziwa kwezinye iimeko. Nangona kunjalo, akukho bungqina bokuba oku kuyasebenza. Kubaluleke kakhulu ukunyanga oyena nobangela we-polycythemia.

Imbonakalo ilungile kwiintsana ezinehyperviscosity ethambileyo. Iziphumo ezilungileyo zinokwenzeka nakwiintsana ezifumana unyango lwe-hyperviscosity. Imbonakalo iya kuxhomekeka ikakhulu kwisizathu sale meko.

Abanye abantwana banokuba notshintsho oluncinci lokukhula. Abazali kufuneka banxibelelane nomboneleli wabo wezempilo ukuba bacinga ukuba umntwana wabo ubonakalisa iimpawu zokulibaziseka kophuhliso.

Iingxaki zinokubandakanya:

• Ukufa kwamathambo emathumbu (i-necrotizing enterocolitis)
• Ukunciphisa ukulawulwa kwemoto
• Ukungaphumeleli kwezintso
• Ukuxhuzula
• Ukubetha

Polycythemia engakhulelwa; Hyperviscosity - usana olusandul 'ukuzalwa

• Iiseli zegazi

IKliegman RM, iSt. Geme JW, iBlum NJ, i-Shah SS, iTasker RC, uWilson KM. Ukuphazamiseka kwegazi. Ku: Kliegman RM, St Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, ii-eds. Incwadi kaNelson yeNcwadi yePediatrics. Umhla wama-21. IPhiladelphia, PA: Elsevier; 2020: isahluko 124.

U-Letterio J, Pateva I, Petrosiute A, Ahuja S. Hematologic kunye neengxaki ze-oncologic kwimveku engekazalwa. Ku: UMartin RJ, uFanaroff AA, uWalsh MC, ii-eds. UFanaroff kunye noMartin's Neonatal-Perinatal Medicine. Ngomhla we-11. IPhiladelphia, PA: Elsevier; 2020: isahl. 79.

UTashi T, uPrchal JT. IPolycythemia. Ku: Lanzkowsky P, Lipton JM, Fish JD, ii-eds. Incwadana yemigaqo kaLanzkowsky yePediatric Hematology kunye neOncology. Umhla wesi-6. ICambridge, MA: Elsevier Academic Press; 2016: isahluko 12.