Isifo sehemoglobin C

Isifo seHemoglobin C sisifo segazi esidluliswa kwiintsapho. Kukhokelela kuhlobo lwe-anemia, eyenzeka xa iiseli ezibomvu zegazi zehla ngaphambi kwexesha eliqhelekileyo.
IHemoglobin C luhlobo olungaqhelekanga lwehemoglobin, iprotein ekwiiseli ezibomvu zegazi ezithwala ioksijini. Luhlobo lwehemoglobinopathy. Esi sifo sibangelwa yingxaki yemfuza ebizwa ngokuba yi-beta globin.
Esi sifo sihlala sivela kubantu base-Afrika baseMelika. Kungenzeka ukuba unesifo se-hemoglobin C ukuba umntu osapho lwakho unaso.
Uninzi lwabantu alunazo iimpawu. Ngamanye amaxesha, i-jaundice inokwenzeka. Abanye abantu banokuphuhlisa i-gallstones efuna ukunyangwa.
Uvavanyo lomzimba lunokubonisa ipeni eyandisiweyo.
Uvavanyo olunokwenziwa lunokubandakanya:
- Gcwalisa ubalo lwegazi
- IHemoglobin electrophoresis
- Umda wegazi smear
- Ihemoglobin yegazi
Kwiimeko ezininzi, akukho nyango lufunekayo. Ukongezwa kwe-acid ye-Folic kunokunceda umzimba wakho uvelise iiseli ezibomvu zegazi kunye nokuphucula iimpawu ze-anemia.
Abantu abanesifo sehemoglobin C banokulindela ukuphila ubomi obuqhelekileyo.
Iingxaki zinokubandakanya:
- Ukunqongophala kwegazi
- Isifo senyongo
- Ukwandiswa kwepeni
Tsalela umnxeba umboneleli wakho ukuba unempawu zesifo sehemoglobin C.
Unokufuna ukufumana iingcebiso ngemfuzo ukuba usemngciphekweni omkhulu wale meko kwaye ucinga ngokufumana umntwana.
Iklinikhi yehemoglobin C
Iiseli zegazi
Isifo seseli sikaHoward J. Sickle kunye nezinye iihemoglobinopathies. Ku: IGoldman L, iSchafer AI, ii-eds. Amayeza eGoldman-Cecil. Ngomhla wama-26. IPhiladelphia, PA: Elsevier; 2020: isahl. 154.
USmith-Whitley K, Kwiatkowski JL. IHemoglobinopathies. Ku: Kliegman RM, St Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, ii-eds. Incwadi kaNelson yeNcwadi yePediatrics. Umhla wama-21. IPhiladelphia, PA: Elsevier; 2020: isahluko 489.
UWilson CS, uVergara-Lluri ME, uBrynes RK. Uvavanyo lwe-anemia, leukopenia, kunye ne-thrombocytopenia. Ku: Jaffe ES, Arber DA, Campo E, Harris NL, Quintanilla-Martinez L, ii-eds. IHematopathology. Ngomhla wesi-2. IPhiladelphia, PA: Elsevier; I-2017: isahluko 11.