Umbhali: William Ramirez
Umhla Wokudalwa: 21 Eyomsintsi 2021
Hlaziya Umhla: 1 Eyekhala 2024
Anonim
Thrombotic Thrombocytopenic Purpura: A Patient’s Journey
Ividiyo: Thrombotic Thrombocytopenic Purpura: A Patient’s Journey

I-Thrombocytopenia yiyo nayiphi na ingxaki apho kukho inani eliphantsi ngokungaqhelekanga leeplatelets. Iiplatelets ngamalungu egazi anceda igazi ukuba lijiye. Le meko ngamanye amaxesha inxulunyaniswa nokopha okungaqhelekanga.

I-Thrombocytopenia ihlala yahlulwa yaziimbangela ezi-3 eziphambili zeeplatelet ezisezantsi:

  1. Akukho platelet zaneleyo zenziwe kumongo wethambo
  2. Ukonyuka kweplatelets egazini
  3. Ukonyuka kweplatelets kwipeni okanye kwisibindi

Umongo wakho wethambo awunakukwenza iiplatelet ezaneleyo ukuba unayo nayiphi na kwezi meko zilandelayo:

  • I-aplastic anemia (ukuphazamiseka apho umongo wethambo ungenzi ngokwaneleyo iiseli zegazi)
  • Umhlaza kumongo wethambo, njengeleukemia
  • I-Cirrhosis (ukusilela kwesibindi)
  • Ukusilela komntu
  • Usulelo kumongo wethambo (kunqabile kakhulu)
  • Isifo seMyelodysplastic (umongo wethambo awenzi ngokwaneleyo iiseli zegazi okanye wenze iiseli ezinesiphene)
  • Ukusilela kweVitamin B12

Ukusetyenziswa kwamachiza athile kunokukhokelela kwimveliso esezantsi yeeplatelets kumongo wethambo. Owona mzekelo uqhelekileyo kunyango lwe-chemotherapy.


Ezi meko zilandelayo zempilo zibangela ukonakala kweeplatelets:

  • Ukuphazamiseka apho iiproteni ezilawula ukujiya kwegazi ziye zisebenze ngakumbi, amaxesha amaninzi ngexesha lokugula kakhulu (DIC)
  • Inani eliphantsi leplatelet
  • Ipeni eyandisiweyo
  • Ukuphazamiseka apho amajoni omzimba atshabalalisa iiplatelets (ITP)
  • Ukuphazamiseka okubangela ukuba amahlwili egazi enze imithambo yegazi encinci, ebangela inani eliphantsi leplatelet (TTP)

Awunakho ukuba naziphi na iimpawu. Okanye unokuba neempawu eziqhelekileyo, ezinje:

  • Ukopha emlonyeni nasezintsinini
  • Ukuthuthuzela
  • Iimpumlo
  • I-Rash (khomba amabala abomvu abizwa ngokuba yi-petechiae)

Ezinye iimpawu zixhomekeke kwisizathu.

Umboneleli wakho wezempilo uya kwenza uvavanyo lomzimba kwaye abuze malunga nembali yakho yonyango kunye neempawu. Olu vavanyo lulandelayo lunokwenziwa:

  • Gcwalisa ubalo lwegazi (CBC)
  • Uvavanyo lokunqanda igazi (PTT kunye ne-PT)

Olunye uvavanyo olunokukunceda ekuchongeni le meko kubandakanya umnqweno wethambo okanye i-biopsy.


Unyango luxhomekeke kwisizathu sale meko. Ngamanye amaxesha, ukongezwa kweeplatelets kungafuneka unqande ukopha.

Iziphumo zixhomekeke kukuphazamiseka okubangela ukubalwa kweplatelet esezantsi.

Ukopha kakhulu (ukopha) yeyona ngxaki iphambili. Ukopha kunokubakho kwingqondo okanye kwithumbu lesisu.

Fowunela umnikezeli wakho ukuba ukopha ngokungachazwanga okanye ukugruzuka.

Ukuthintela kuxhomekeke kwisizathu esithile.

Inani eliphantsi leplatelet - thrombocytopenia

Abrams CS. I-Thrombocytopenia. Ku: IGoldman L, iSchafer AI, ii-eds. Amayeza eGoldman-Cecil. Ngomhla wama-26. IPhiladelphia, PA: Elsevier; 2020: isahluko 163.

UArnold DM, uMphathiswa weZeller, uSmith JW, uNazy I. Izifo zenombolo yeplatelet: i-immune thrombocytopenia, neonatal alloimmune thrombocytopenia, kunye ne-posttransfusion purpura. Ku: Hoffman R, Benz EJ, Silberstein LE, et al, ii-eds. I-Hematology: Imigaqo esisiseko kunye nokuziqhelanisa. Umhla wesi-7. IPhiladelphia, PA: Elsevier; I-2018: isahluko 131.

IWarkentin TE. I-Thrombocytopenia ebangelwa yintshabalalo yeplatelet, hypersplenism, okanye ihemodilution. Ku: Hoffman R, Benz EJ, Silberstein LE, et al, ii-eds. I-Hematology: Imigaqo esisiseko kunye nokuziqhelanisa. Umhla wesi-7. IPhiladelphia, PA: Elsevier; I-2018: isahluko 132.


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