I-Retinitis pigmentosa

I-Retinitis pigmentosa sisifo samehlo apho kukho umonakalo kwi-retina. Iretina ngumaleko weethishu ngasemva kweliso langaphakathi. Olu luhlu luguqula imifanekiso ekhanyayo iye kwiimpawu zemithambo-luvo ize iyithumele kwingqondo.

I-Retinitis pigmentosa inokuhamba kwiintsapho. Ukuphazamiseka kunokubangelwa ziziphene zemfuza.

Iiseli ezilawula umbono wasebusuku (iintonga) kunokwenzeka ukuba zichaphazeleke. Nangona kunjalo, kwezinye iimeko, iiseli ze-retinal cone zonakaliswe kakhulu. Uphawu oluphambili lwesi sifo bubukho beedipozithi ezimnyama kwi-retina.

Umngcipheko oyintloko yimbali yosapho ye-retinitis pigmentosa. Yimeko enqabileyo echaphazela malunga ne-1 kubantu abangama-4,000 e-United States.

Iimpawu zihlala zivela ebuntwaneni. Nangona kunjalo, iingxaki zombono ezinzima azisoloko zikhula ngaphambi kokuba ube mdala.

• Ukuhla kombono ebusuku okanye ukukhanya okuncinci. Iimpawu zokuqala zinokubandakanya ukuba nexesha elinzima lokuhamba ebumnyameni.
• Ukulahleka kwecala (kwipheripherali) umbono, obangela "umbono wetonela."
• Ukuphulukana nombono ophakathi (kwiimeko eziphambili). Oku kuya kuchaphazela amandla okufunda.

Uvavanyo lokuvavanya i-retina:

• Umbono wombala
• Uviwo lwe-retina yi-ophthalmoscopy emva kokuba abafundi behlisiwe
• I-fluorescein angiography
• Uxinzelelo lwangaphakathi
• Ukulinganiswa komsebenzi wombane kwi-retina (i-electroretinogram)
• Impendulo yomfundi
• Uvavanyo lokurhoxisa
• Ukufotwa kweRetinal
• Uvavanyo lombono osecaleni (uvavanyo lwentsimi ebonakalayo)
• Sika uviwo lwesibane
• Ubunzima bokubonakalayo

Akukho lunyango lusebenzayo kule meko. Ukunxiba iiglasi zelanga ukukhusela i-retina ekukhanyeni kwelanga kunokunceda ukugcina umbono.

Olunye uphononongo lubonisa ukuba unyango lwee-antioxidants (ezinjengeedosi eziphezulu zevithamini A palmitate) zinokusicothisa isifo. Nangona kunjalo, ukuthatha idosi ephezulu yevithamini A kunokubangela iingxaki zesibindi. Izibonelelo zonyango kufuneka zilinganiswe ngokuchasene nomngcipheko wesibindi.

Uvavanyo lwezonyango luyaqhubeka kuvavanyo lonyango lwe-retinitis pigmentosa, kubandakanya nokusetyenziswa kwe-DHA, eyi-omega-3 fatty acid.

Olunye unyango, olufana nokufakwa kwe-microchip kwi-retina esebenza njengekhamera yevidiyo encinci, bakumanqanaba okuqala ophuhliso. Olu nyango lunokuba luncedo ekunyangeni ubumfama obunxulunyaniswa ne-RP kunye nezinye iimeko zamehlo ezinzima.

Ingcali yombono inokukunceda uqhelane nelahleko yombono. Yenza utyelelo rhoqo kugqirha wokhathalelo lwamehlo, onokuthi abone ikati okanye ukudumba kwethambo. Zombini ezi ngxaki zinokunyangwa.

Ukuphazamiseka kuya kuqhubeka ukuqhubela phambili kancinci. Ukufama ngokupheleleyo akuqhelekanga.

Ukulahleka kombono kunye nokulahleka kombono kuya kwenzeka ekuhambeni kwexesha.

Abantu abane-retinitis pigmentosa bahlala bekhula besebancinci. Banokuphucula ukudumba kweretina (macular edema). I-Cataract ingasuswa ukuba inegalelo ekulahlekelweni kombono.

Nxibelelana nomboneleli wakho wezempilo ukuba unengxaki ngombono wasebusuku okanye uvelisa ezinye iimpawu zesi sifo.

Ukucebisa ngemfuza kunye nokuvavanywa kunokunceda ekuboneni ukuba ingaba abantwana bakho basemngciphekweni wesi sifo.

RP; Ukulahleka kombono-RP; Ukuphulukana nombono ebusuku - RP; Intonga yesifo seDystrophy; Ukuphulukana nombono wepheripher - RP; Ubumfama ebusuku

• Iliso
• Uvavanyo lwesibane

UCioffi GA, uLiebmann JM. Izifo zenkqubo yokubonakalayo. Ku: IGoldman L, iSchafer AI, ii-eds. Amayeza eGoldman-Cecil. Ngomhla wama-26. IPhiladelphia, PA: Elsevier; 2020: isahluko 395.

ICukras CA, uZein WM, uCaruso RC, uSieving PA. Ukuqhubela phambili kunye 'nokuma' njengelifa lokuhla komzimba. Ku: Yanoff M, Duker JS, ii-eds. Ophthalmology. Umhla we-5. IPhiladelphia, PA: Elsevier; I-2019: isahl. 6.14.

UGregory-Evans K, uWeleber RG, uPennesi ME. I-Retinitis pigmentosa kunye neengxaki ezidibeneyo. Ku: Schachat AP, Sadda SR, Hinton DR, Wilkinson CP, Wiedemann P, ii-eds. URetina kaRyan. Umhla wesi-6. IPhiladelphia, PA: Elsevier; I-2018: isahluko 42.

U-Olitisky SE, uMarsh JD. Ukuphazamiseka kweretina kunye ne-vitreous. Ku: Kliegman RM, St Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, ii-eds. Incwadi kaNelson yeNcwadi yePediatrics. Umhla wama-21. IPhiladelphia, PA: Elsevier; 2020: isahluko 648.