Yenzinyani

I-Arachnodactyly yimeko apho iminwe inde, inde, kwaye igobile. Zibukeka njengemilenze yesigcawu (arachnid).
Iminwe emide, ebhityileyo inokuba yinto eqhelekileyo kwaye ingadibani nazo naziphi na iingxaki zonyango. Kwezinye iimeko, nangona kunjalo, "iminwe yesigcawu" inokuba luphawu lwesifo esisisiseko.
Izizathu zingabandakanya:
- Ukunyanga amalungu omzimba
- Isifo seMarfan
- Ezinye iingxaki ezinqabileyo zemfuza
Qaphela: Ukuba neminwe emide, ebhityileyo kunokuba yinto eqhelekileyo.
Abanye abantwana bazalwa nge-arachnodactyly. Inokubonakala ngakumbi ngokuhamba kwexesha. Thetha nomboneleli wakho wezempilo ukuba umntwana wakho uneminwe emide, emincinci kwaye unenkxalabo yokuba imeko enokubakho inokubakho.
Umboneleli uya kwenza uvavanyo lomzimba. Uya kubuzwa imibuzo malunga nembali yonyango. Oku kubandakanya:
- Uqale nini ukuqaphela ukuba iminwe imile ngoluhlobo?
- Ngaba ikhona imbali yosapho yokufa kwangoko? Ngaba ikhona imbali yosapho eyaziwayo yokuphazamiseka kwilifa?
- Zeziphi ezinye iimpawu ezikhoyo? Ukhe waqaphela ezinye izinto ezingaqhelekanga?
Uvavanyo lokuchonga akusoloko luyimfuneko ngaphandle kokuba kurhaneleka ukuba kukho ingxaki yelifa.
IDolichostenomelia; Iminwe yesigcawu; I-Achromachia
UDoyle Al, uDoyle JJ, uDietz HC. Isifo seMarfan. Ku: Kliegman RM, St Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, ii-eds. Incwadi kaNelson yeNcwadi yePediatrics. Umhla wama-21. IPhiladelphia, PA: Elsevier; 2020: isahluko 722.
IHering JA. Ii-syndromes ezinxulumene namathambo. Ku: Hering JA, ed. I-Tachdjian's Pediatric Orthopedics. Umhla we-5. IPhiladelphia, PA: Elsevier Saunders; I-2014: isahluko 41.