Uvavanyo lweSerum phenylalanine

Ukuvavanywa kweserum phenylalanine kuvavanyo lwegazi ukujonga iimpawu zesifo se-phenylketonuria (PKU). Uvavanyo lufumanisa amanqanaba aphezulu ngokungaqhelekanga e-amino acid ebizwa ngokuba yi-phenylalanine.

Uvavanyo luhlala lusenziwa njengenxalenye yovavanyo oluqhelekileyo ngaphambi kokuba usana luphume esibhedlele. Ukuba umntwana akazalwanga esibhedlele, uvavanyo kufuneka lwenziwe kwiiyure zokuqala ezingama-48 ukuya kwezingama-72 zobomi.

Indawo yolusu losana, amaxesha amaninzi isithende, icocwa ngombulali wentsholongwane kwaye yagqobhoza ngenaliti ebukhali okanye i-lancet. Amaconsi egazi amathathu abekwa kwizangqa ezintathu zovavanyo kwisiqwengana sephepha. Umqhaphu okanye ibhandeji inokusetyenziswa kwindawo yokugqobhoza ukuba isopha emva kokuba kuthathwe amathontsi egazi.

Iphepha lokuvavanya lithathwa elabhoratri, apho lixutywe nohlobo lwebhakteriya efuna i-phenylalanine ukukhula. Enye into ethintela i-phenylalanine ekuphenduleni ngayo nayiphi na enye into iyongezwa.

Uvavanyo olusandul 'ukuzalwa lokuvavanywa linqaku elinxulumene noko.

Ngoncedo lokulungiselela usana lwakho kuvavanyo, jonga uvavanyo lweentsana okanye ukulungiswa kwenkqubo (ukuzalwa ukuya kunyaka-1).

Xa kufakwa inaliti ukutsala igazi, ezinye iintsana ziye zive iintlungu eziphakathi, ngelixa ezinye ziziva ngathi zihlaba nje okanye zihlaba. Emva koko, kunokubakho ukuthotywa okuthile. Iintsana zinikwa isixa esincinci samanzi eswekile, esele ibonakalisile ukunciphisa ukubola okuhambelana nokuhlatywa kolusu.

Olu vavanyo lwenzelwa ukukrola iintsana ze-PKU, imeko enqabileyo eyenzekayo xa umzimba ungenanto ifunekayo yokonakalisa i-amino acid phenylalanine.

Ukuba i-PKU ayifumaneki kwangethuba, ukonyusa amanqanaba e-phenylalanine kusana kuya kubangela ukukhubazeka kwengqondo. Xa kufunyenwe kwangethuba, utshintsho kwindlela yokutya lunokunceda ukuthintela iziphumo ebezingalindelekanga zePKU.

Iziphumo zovavanyo eziqhelekileyo zithetha ukuba amanqanaba e-phenylalanine aqhelekileyo kwaye umntwana akanayo iPKU.

Amaxabiso esiqhelo ahluka kancinci phakathi kweelebhu ezahlukeneyo. Thetha nomboneleli wakho wezempilo malunga nentsingiselo yeziphumo zovavanyo lomntwana wakho.

Ukuba iziphumo zovavanyo zovavanyo aziqhelekanga, iPKU inokwenzeka. Olunye uvavanyo luya kwenziwa ukuba amanqanaba e-phenylalanine egazini lomntwana wakho aphezulu kakhulu.

Umngcipheko wokutsalwa kwegazi mncinci, kodwa kubandakanya:

• Ukopha kakhulu
• Ukufa isiqaqa okanye ukuziva ungenantloko
• I-Hematoma (igazi eliqokelela phantsi kwesikhumba)
• Usulelo (umngcipheko omncinci nangaliphi na ixesha ulusu lwaphukile)
• Ukugqobhoza okuninzi ukufumana imithambo

Phenylalanine - uvavanyo lwegazi; I-PKU-phenylalanine

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