Umbhali: William Ramirez
Umhla Wokudalwa: 18 Eyomsintsi 2021
Hlaziya Umhla: 1 Eyekhala 2024
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Ifestile ye-Aortopulmonary sisiphene sentliziyo esinqabileyo apho kukho umngxuma odibanisa umthambo omkhulu othatha igazi usuka entliziyweni uye emzimbeni (i-aorta) kunye nalowo uthatha igazi lisuka entliziyweni liye emiphungeni (umthambo wemiphunga). Imeko yinto yokuzalwa, oko kuthetha ukuba ikhoyo xa kuzalwa.

Ngokwesiqhelo, igazi lihamba ngemithambo yemiphunga ukuya emiphungeni, apho lithatha khona ioksijini. Emva koko igazi libuyela entliziyweni lize lifakwe kwi-aorta nakulo lonke umzimba.

Iintsana ezinefestile ye-aortopulmonary zinomngxuma phakathi kwe-aorta kunye ne-pulmonary artery. Ngenxa yalo mngxuma, igazi eliphuma kwi-aorta lihamba liye emithanjeni ye-pulmonary, kwaye ngenxa yoko igazi elininzi lihamba liye emiphungeni. Oku kubangela uxinzelelo lwegazi oluphezulu emiphungeni (imeko ebizwa ngokuba yi-pulmonary hypertension) kunye nokuhluleka kwentliziyo. Eyona nto inkulu isiphako, kokukhona igazi elinako ukungena kwimithambo ye-pulmonary.


Imeko yenzeka xa i-aorta kunye nomthambo wamaphaphu ungohluli ngokwesiqhelo njengoko umntwana ekhula esibelekweni.

Ifestile yeAortopulmonary inqabile. Ibalelwa ngaphantsi kwe-1% yazo zonke iziphene zentliziyo yokuzalwa.

Le meko inokwenzeka yodwa okanye nezinye iziphene zentliziyo ezinje:

  • Tetralogy yoBuxoki
  • I-atresia yePulmonary
  • Truncus arteriosus
  • Isiphene se-Atrial septal
  • Ipatent ductus arteriosus
  • Ukuphazanyiswa yi-aortic arch

Amashumi amahlanu eepesenti abantu awanazo ezinye iziphene zentliziyo.

Ukuba isiphako sincinci, akunakubangela zimpawu. Nangona kunjalo, uninzi lweziphene lukhulu.

Iimpawu zingabandakanya:

  • Ukukhula okulibazisekileyo
  • Ukumelwa yintliziyo
  • Ukucaphuka
  • Ukutya okungalunganga kunye nokusilela kokufumana ubunzima
  • Ukuphefumla ngokukhawuleza
  • Ukubetha kwentliziyo okukhawulezayo
  • Izifo zokuphefumula

Umboneleli wezempilo uhlala esiva isandi esingaqhelekanga sentliziyo (ukumbombozela) xa umamele intliziyo yomntwana ene-stethoscope.


Umboneleli unoku-odola iimvavanyo ezinje:

  • I-catheterization yentliziyo - ityhubhu ebhityileyo efakwe kwimithambo yegazi kunye / okanye imithambo ejikeleze intliziyo ukujonga intliziyo kunye nemithambo yegazi kunye nokulinganisa ngokuthe ngqo uxinzelelo entliziyweni nasemiphungeni.
  • I-x-ray yesifuba.
  • Echocardiogram.
  • I-MRI yentliziyo.

Imeko ihlala ifuna utyando lwentliziyo oluvulekileyo ukulungisa isiphako. Ugqirha kufuneka lwenziwe ngokukhawuleza emva kokuba kufunyenwe isifo. Kwiimeko ezininzi, oku kuxa umntwana eselusana.

Ngexesha lenkqubo, umatshini wentliziyo-wemiphunga uthatha indawo yentliziyo yomntwana. Ugqirha uvula i-aorta kwaye avale isiphene ngesiqwenga esenziwe ngesiqwenga sesingxobo esivala intliziyo (i-pericardium) okanye into eyenziwe ngumntu.

Utyando lokulungisa i-aortopulmonary window luyaphumelela kwiimeko ezininzi. Ukuba isiphene siphathwa ngokukhawuleza, umntwana akufuneki abe neziphumo ezihlala zihleli.

Ukulibazisa unyango kunokukhokelela kwiingxaki ezinje:

  • Ukusilela kwentliziyo
  • Uxinzelelo lwegazi kwimiphunga okanye isifo se-Eisenmenger
  • Ukufa

Fowunela umnikezeli wakho ukuba umntwana wakho uneempawu zewindow. Ngokukhawuleza ukuba le meko ifunyanwe kwaye inyangwe, ngcono isifo somntwana.


Akukho ndlela yaziwayo yokuthintela iwindow ye-aortopulmonary.

Isiphene septopulmonary septal; Ukuvuthwa kweAortopulmonary; Isiphene sentliziyo yento yokuzalwa - iwindow ye-aortopulmonary; Isiphene sokuzalwa kwentliziyo- iwindow ye-aortopulmonary

  • Ifestile yeAortopulmonary

I-Fraser CD, iKane LC. Isifo sentliziyo. Ku: Townsend CM, Beauchamp RD, Evers BM, Mattox KL, eds. Incwadi yeSabiston yoNyango. Umhla we-20. IPhiladelphia, PA: Elsevier; Ngo-2017: isahluko 58.

I-Qureshi AM, iGowda ST, uJustino H, uSpicer DE, kunye noAnderson RH. Olunye ulungiso lweempembelelo zokuphuma kwentliziyo. Ku: Wernovsky G, Anderson RH, Kumar K, et al, ii-eds. Anderson's Cardiology yabantwana. Ngomhla we-4. IPhiladelphia, PA: Elsevier; 2020: isahl 51.

IWebb GD, i-Smallhorn JF, iTherrien J, iRedington AN. Isifo sentliziyo esibelekwe kumntu omkhulu nakwisigulana sabantwana. Ku: Zipes DP, Libby P, Bonow RO, Mann DL, Tomaselli GF, Braunwald E, ii-eds. Isifo sentliziyo seBraunwald: Incwadi yesifundo seMpilo yeNtliziyo. Ngomhla we-11. IPhiladelphia, PA: Elsevier; I-2019: isahluko 75.

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