Umbhali: Robert Simon
Umhla Wokudalwa: 19 Isilimela 2021
Hlaziya Umhla: 1 Eyekhala 2024
Anonim
I-Cerebellar Ataxia eyiyo (ACA) - Zempilo
I-Cerebellar Ataxia eyiyo (ACA) - Zempilo

Umxholo

Yintoni iacute cerebellar ataxia?

I-acute cerebellar ataxia (ACA) sisifo esenzeka xa i-cerebellum ivutha okanye yonakaliswe. I-cerebellum yindawo yengqondo ejongene nokulawula ukuhamba kunye nokulungelelaniswa kwemisipha.

Igama elithile ataxia ibhekisa kukungabikho kolawulo olucocekileyo lweentshukumo zokuzithandela. Ngamandla kuthetha ukuba i-ataxia iza ngokukhawuleza, ngokulandelelana kwemizuzu ukuya kusuku okanye ezimbini. I-ACA ikwabizwa ngokuba yi-cerebellitis.

Abantu abane-ACA bahlala belahleka kokulungelelanisa kwaye banokuba nobunzima ekwenzeni imisebenzi yemihla ngemihla. Imeko exhaphakileyo ichaphazela abantwana, ngakumbi abo baphakathi kweminyaka emi-2 ukuya kweli-7. Nangona kunjalo, ngamanye amaxesha ichaphazela nabantu abadala.

Yintoni ebangela i-acety cerebellar ataxia?

Iintsholongwane kunye nezinye izifo ezichaphazela inkqubo yeemvakalelo zinokwenzakalisa i-cerebellum. Oku kubandakanya:

  • iqhwiqhwi
  • imasisi
  • uqwilikana
  • hepatitis A
  • Usulelo olubangelwa ziintsholongwane zikaEpstein-Barr kunye neCoxsackie
  • Intsholongwane yeNayile

I-ACA inokuthatha iiveki ukuvela emva kosulelo lwentsholongwane.


Ezinye izizathu ze-ACA zibandakanya:

  • ukopha kwi-cerebellum
  • Ukubonakaliswa kwimekyuri, ukukhokela kunye nezinye iityhefu
  • usulelo lwebhaktiriya, njengesifo seLyme
  • ukwenzakala entloko
  • ukusilela kweevithamini ezithile, ezinje nge-B-12, B-1 (thiamine), kunye no-E

Zithini iimpawu zecacusebellar ataxia ebukhali?

Iimpawu ze-ACA zibandakanya:

  • Ulungelelwaniso olungalunganga kwi-torso okanye iingalo kunye nemilenze
  • ukukhubeka rhoqo
  • indlela engazinzanga
  • ukungalawuleki okanye ukuphinda-phinda ukuhamba kwamehlo
  • unengxaki yokutya kunye nokwenza eminye imisebenzi yeemoto entle
  • intetho engacacanga
  • utshintsho kwizwi
  • intloko ebuhlungu
  • isiyezi

Ezi mpawu zinxulunyaniswa nezinye iimeko ezininzi ezichaphazela inkqubo yeemvakalelo. Kubalulekile ukuba ubone ugqirha wakho ukuze bakwazi ukwenza uxilongo olufanelekileyo.

Ichaphazeleka njani i-acute cerebellar ataxia?

Ugqirha wakho uya kuqhuba iimvavanyo ezininzi ukumisela ukuba unayo i-ACA kunye nokufumana unobangela wesifo. Olu vavanyo lunokubandakanya uvavanyo lomzimba oluqhelekileyo kunye novavanyo lweeurological ezahlukeneyo. Ugqirha wakho unokuvavanya:


  • ukuva
  • imemori
  • ukulinganisela nokuhamba
  • umbono
  • Uxinzelelo
  • Ingqondo
  • ulungelelaniso

Ukuba awuzange wosulelwe yintsholongwane kutshanje, ugqirha wakho uya kujonga neempawu zezinye iimeko kunye nokuphazamiseka okuhlala kukhokelela kwi-ACA.

Kukho inani leemvavanyo ugqirha wakho anokuzisebenzisa ukuvavanya iimpawu zakho, kubandakanya:

  • Isifundo sokuqhutywa kwemithambo. Isifundo sokuqhutywa kwemithambo-luvo simisela ukuba ingaba imithambo-luvo yakho isebenza ngokuchanekileyo na.
  • Umbane wombane (EMG). I-electromyogram irekhoda kwaye ivavanye umsebenzi wombane kwimisipha yakho.
  • Impompo yomqolo. Impompo yomqolo ivumela ugqirha wakho ukuba avavanye i-cerebrospinal fluid yakho (CSF), ejikeleze intambo yomqolo kunye nengqondo.
  • Gcwalisa ubalo lwegazi (ICBC). Inani elipheleleyo legazi limisela ukuba ngaba kukho nakuphi na ukuncipha okanye ukonyuka kwinani lakho leeseli zegazi. Oku kunokunceda ugqirha wakho avavanye impilo yakho iphela.
  • CT okanye IMRI iskena. Ugqirha wakho unokujonga ukonakala kwengqondo usebenzisa olu vavanyo lokucinga. Banikezela ngemifanekiso eneenkcukacha zobuchopho bakho, ukuvumela ugqirha wakho ukuba ajonge ngakumbi kwaye avavanye nawuphi na umonakalo kwingqondo ngokulula.
  • Uhlalutyo lomchamo kwaye Ultrasound. Olu lolunye uvavanyo olunokwenziwa ngugqirha wakho.

Ngaba inyangwa njani i-acute cerebellar ataxia?

Unyango lwe-ACA alusoloko luyimfuneko. Xa intsholongwane ibangela i-ACA, ukubuyiswa ngokupheleleyo kuhlala kulindelwe ngaphandle konyango. I-ACA yentsholongwane ihamba ngokubanzi kwiiveki ezimbalwa ngaphandle kwonyango.


Nangona kunjalo, unyango luhlala ludinga ukuba intsholongwane ayiyiyo imbangela ye-ACA yakho. Unyango oluthile luya kwahluka ngokuxhomekeke kwisizathu, kwaye lunokuhlala iiveki, iminyaka, okanye nobomi bonke. Nazi ezinye iindlela zonyango ezinokubakho:

  • Unokufuna utyando ukuba imeko yakho sisiphumo sokopha kwi-cerebellum.
  • Unokufuna i-antibiotics ukuba unentsholongwane.
  • Abacoci begazi banokukunceda ukuba ukubetha kubangele i-ACA yakho.
  • Unokuthatha amayeza ukunyanga ukudumba kwe-cerebellum, njenge-steroids.
  • Ukuba ityhefu ngumthombo we-ACA, nciphisa okanye ususe ukubonwa kwakho kwityhefu.
  • Ukuba i-ACA yaziswa kukungabikho kweevithamini, unokuncedisa kwiidosi eziphezulu zevithamin E, inaliti ye-vitamin B-12, okanye i-thiamine.
  • Kwezinye iimeko, i-ACA inokuziswa ngovakalelo lwe-gluten. Kule meko, kuya kufuneka uthathe ukutya okungqongqo okungahambisani ne-gluten.

Ukuba unayo i-ACA, unokufuna uncedo kwimisebenzi yemihla ngemihla. Izixhobo zokutya ezikhethekileyo kunye nezixhobo eziguqukayo ezinje ngemijana kunye nezixhobo zokuthetha zinokunceda. Unyango lomzimba, unyango lwentetho, kunye nonyango olusebenzayo lunokunceda ukuphucula iimpawu zakho.

Abanye abantu bakwafumanisa ukuba ukwenza utshintsho oluthile kwindlela yokuphila kunokuqhubeka nokuzikhupha iimpawu. Oku kunokubandakanya ukutshintsha indlela otya ngayo okanye ukuthatha izongezo zesondlo.

Ichaphazeleka njani i-atabellia ebukhali ichaphazela abantu abadala?

Iimpawu ze-ACA kubantu abadala ziyafana nezabantwana. Njengabantwana, ukunyanga i-ACA yabantu abadala kubandakanya ukunyanga imeko ebangele oko.

Ngelixa uninzi lwemithombo ye-ACA ebantwaneni inokubangela i-ACA kubantu abadala, kukho iimeko ezithile ezinokubangela i-ACA kubantu abadala.

Iityhefu, ngakumbi ukusela kakhulu utywala, zezinye zezona zinto zibangela i-ACA kubantu abadala. Ukongeza, amayeza anje ngeziyobisi ze-antiepileptic kunye ne-chemotherapy zihlala zinxulunyaniswa ne-ACA kubantu abadala.

Iimeko eziphantsi kwe-HIV, i-multiple sclerosis (MS), kunye neengxaki zokuzimela komzimba nazo zinakho ukwandisa umngcipheko we-ACA njengomntu omdala. Nangona kunjalo, kwiimeko ezininzi, unobangela we-ACA kubantu abadala uhlala uyimfihlakalo.

Xa uxilonga i-ACA kubantu abadala, oogqirha kuqala bazame ukwahlula i-ACA kwezinye iindidi ze-cerebellar ataxias eziza kancinci kancinci. Ngelixa i-ACA ibetha ngaphakathi kwemizuzu ukuya kwiiyure, ezinye iintlobo ze-ataxia ye-cerebellar inokuthatha iintsuku ukuya kwiminyaka ukukhula.

Ii-ataxias ezinenqanaba elincinci lokuqhubela phambili zinokuba nezizathu ezahlukeneyo, ezinje ngezixhobo zofuzo, kwaye zifuna unyango olwahlukileyo.

Njengomntu omdala, kunokwenzeka ukuba ufumane ubuchopho bokucinga, njenge-MRI, ngexesha lokuqonda isifo. Lo mfanekiso ungabonisa ukungaqheleki kunokubangela i-ataxias ezinenkqubela phambili ecothayo.

Zeziphi ezinye iimeko ezifanayo neaccebellar ataxia ebukhali?

I-ACA ibonakaliswa ngokuqala ngokukhawuleza - imizuzu ukuya kwiiyure. Kukho ezinye iindlela ze-ataxia ezineempawu ezifanayo kodwa izizathu ezahlukeneyo:

Subacute ataxias

I-subacute ataxias ikhula ngaphezulu kweentsuku okanye iiveki. Ngamanye amaxesha u-ataxias we-subacute unokubonakala ngathi uza kuza ngokukhawuleza, kodwa eneneni, baye bakhula kancinci ngokuhamba kwexesha.

Izizathu zihlala zifana ne-ACA, kodwa i-ataxias ye-subacute nayo ibangelwa zizifo ezinqabileyo ezifana nezifo ze-prion, isifo se-Whipple, kunye ne-leukoencephalopathy (PML) eqhubekayo.

Ii-ataxias ezingapheliyo

Ii-ataxias ezingapheliyo ziqhubela phambili kwaye zihlala ngaphezulu kweenyanga okanye iminyaka. Zihlala zibangelwa ziimfuzo.

Ii-ataxias ezingapheliyo zinokubangelwa kukuphazamiseka kwemitochondrial okanye i-neurodegenerative. Ezinye izifo zinokubangela okanye zilingise i-ataxias ezingapheliyo ngokunjalo, ezinjengeentloko zentloko kunye ne-brainstem aura, isifo esinqabileyo apho i-ataxia ihamba kunye nentloko ye-migraine.

Ataxias ezizelwe

I-ataxias ye-Congenital ikhona ngexesha lokuzalwa kwaye ihlala isigxina, nangona ezinye zinokunyangwa ngoqhaqho. Ezi ataxias zibangelwa kukungahambelani kokumila kwengqondo.

Zeziphi iingxaki ezinxulunyaniswa neaccebellar ataxia ebukhali?

Iimpawu ze-ACA zinokuhlala ngokusisigxina xa ukuphazamiseka kubangelwa ukubetha, usulelo, okanye ukuphuma kwegazi kwi-cerebellum.

Ukuba unayo i-ACA, usemngciphekweni omkhulu wokukhula koxinzelelo kunye noxinzelelo. Oku kuyinyani ngakumbi ukuba ufuna uncedo ngemisebenzi yemihla ngemihla, okanye awukwazi ukuzenzela wedwa.

Ukujoyina iqela lenkxaso okanye ukudibana nomcebisi kunokukunceda ujongane neempawu zakho kunye nayo nayiphi na imiceli mngeni ojamelene nayo.

Ngaba kunokwenzeka ukuthintela i-ataxia ebukhali ye-cerebellar?

Kunzima ukuthintela i-ACA, kodwa ungawunciphisa umngcipheko wabantwana bakho wokufumana ngokuqinisekisa ukuba bayagonywa kwiintsholongwane ezinokukhokelela kwi-ACA, enjengeenkukhu.

Njengomntu omdala, unokunciphisa umngcipheko we-ACA ngokuphepha ukusela kakhulu utywala kunye nezinye iityhefu. Ukunciphisa umngcipheko we-stroke ngokuzilolonga, ukugcina ubunzima obunempilo, nokugcina uxinzelelo lwegazi kunye ne-cholesterol ekujongeni kunokuba luncedo ekukhuseleni i-ACA.

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