Yazi isifo esishiya intliziyo ingqongqo

Umxholo

• Iimpawu
• Ukwazi njani ukuba yi-cardiac amyloidosis
• Unyango

I-Cardiac amyloidosis, ekwabizwa ngokuba yi-rigid heart syndrome, sisifo esinqabileyo, esibi kakhulu esichaphazela izihlunu zentliziyo ngenxa yokuqokelelwa kweeproteni ezibizwa ngokuba zii-amyloids kwiindonga zentliziyo.

Esi sifo sixhaphake kakhulu kumadoda angaphezu kweminyaka engama-40 kwaye sibangela iimpawu zokwehluleka kwentliziyo, ezinje ngokudinwa okulula kunye nobunzima bokunyuka kwizinyuko okanye ukwenza iinzame ezincinci.

Ukuqokelelwa kweeproteni kunokwenzeka kuphela kwi-septum ye-atrial, njengoko kuqhelekile kubantu abadala, okanye kwii-ventricles, ezinokubangela ukusilela kwentliziyo.

Iimpawu

Iimpawu ze-amyloidosis yentliziyo kunokuba:

• Ukufuna ngamandla ukuchama ebusuku;
• Ukwandiswa kweemvini zentamo, ngokwesayensi zibizwa ngokuba yi-jugular stasis;
• Ukubetha kwentliziyo;
• Ukwanda kolwelo emiphungeni;
• Ukwandiswa kwesibindi;
• Uxinzelelo oluphantsi xa unyuka esihlalweni, umzekelo;
• Ukudinwa;
• Ukukhohlela okungapheliyo;
• Ukunciphisa umzimba ngaphandle kwesizathu esibonakalayo, ngaphandle kokutya okanye ukwanda kokuzilolonga;
• Ukunganyamezelani kwimizamo yomzimba;
• Ukufa;
• Ukuphefumla okufutshane;
• Imilenze idumbile;
• Isisu esidumbileyo.

I-Amyloidosis entliziyweni ibonakaliswa yiprotein egqithileyo kwizihlunu zentliziyo kwaye inokubangelwa zii-myeloma ezininzi, inokuba yimvelaphi yosapho okanye inokuvela ngokwaluphala.

Ukwazi njani ukuba yi-cardiac amyloidosis

Ngokwesiqhelo, esi sifo asikrokrelwa kutyelelo lokuqala kwaye, ke, kuqhelekile ukuba oogqirha bacele iimvavanyo ezininzi zokuhlola ezinye izifo ngaphambi kokufikelela kwisifo se-amyloidosis yentliziyo.

Ukuxilongwa kwenziwa ngokujonga iimpawu kunye novavanyo olucelwe ngugqirha wezifo zentliziyo, njenge-electrocardiogram, i-echocardiogram kunye nokujonga ngemagneti yokujonga, okunokuthi kufumanise ii-arrhythmias zentliziyo, utshintsho kwimisebenzi yentliziyo kunye nokuphazamiseka kuhambo lombane lwentliziyo, kodwa isifo ye-amyloidosis yentliziyo inokungqinwa kuphela nge-biopsy yethishu yentliziyo.

Olu xilongo lunokufikelelwa xa ubukhulu bodonga lwe-ventricular lungaphezulu kwe-12 mm kwaye xa umntu engenalo uxinzelelo oluphezulu lwegazi, kodwa enesinye sezi zinto zilandelayo: ukwanda kwe-atria, ukungcola kwe-pericardial okanye ukusilela kwentliziyo.

Unyango

Unyango, unyango kunye nomchamo we-vasodilator ungasetyenziselwa ukunciphisa iimpawu zesi sifo. Ukusetyenziswa kwezixhobo zokwenza amandla kunye nezixhobo ezizenzekelayo kunokusetyenziswa njengezinye iindlela zokulawula isifo kwaye kwiimeko ezinzima kakhulu, olona nyango lufanelekileyo kukufakelwa kwentliziyo. Jonga imingcipheko kunye nendlela onokufumana ngayo kwakhona ekufakweni kwentliziyo ngokunqakraza apha.

Kuxhomekeka kubukhali besi sifo, i-anticoagulants ethintela ukwenziwa kwamahlwili egazi entliziyweni ingasetyenziswa, ukunciphisa ukubetha. I-Chemotherapy inokusetyenziswa xa unobangela we-cardiac amyloidosis ngumhlaza wohlobo lwe-myeloma

Umntu kufuneka ayiphephe ityuwa, akhethe ukutya okwe-diuretic kwaye aphephe ukwenza iinzame zokonga intliziyo. Usapho kufuneka luphephe ukunikezela ngeendaba ezimbi kuba iimvakalelo ezinzulu zinokukhokelela kutshintsho olukhulu lwentliziyo olunokukhokelela kwisifo sentliziyo.

Jonga zonke iintlobo kunye neempawu ezibangelwa yi-Amyloidosis.