Unxibelelwano phakathi kwe-Exocrine Pancreatic insufficiency kunye neCystic Fibrosis

Umxholo

• Yintoni ebangela icystic fibrosis?
• Ziziphi izinto ezinobungozi kwi-cystic fibrosis?
• I-EPI kunye necystic fibrosis zihambelana njani?
• Zeziphi iintlobo zonyango ezikhoyo ze-EPI?
• Ukuthatha

ICystic fibrosis sisifo esizuze njengelifa esibangela ukuba ulwelo lomzimba lube lukhulu kwaye lunamathele endaweni yokubhitya kunye nokubaleka. Oku kuchaphazela kakubi imiphunga kunye nenkqubo yokwetyisa.

Abantu abane-cystic fibrosis baneengxaki zokuphefumla kuba i-mucus ivalela imiphunga yabo kwaye ibenza babe sengozini yosulelo. I-mucus eshinyeneyo ikwavala iipancreas kwaye kuthintele ukukhutshwa kwee-enzymes zesisu. Phantse iipesenti ezingama-90 zabantu abane-cystic fibrosis baphinde bahlakulele ukungabikho kwe-pancreatic (EPI).

Qhubeka ufunda ukuze ufunde ngakumbi malunga nobudlelwane phakathi kwezi meko zimbini.

Yintoni ebangela icystic fibrosis?

ICystic fibrosis ibangelwa sisiphene kuhlobo lweCFTR. Utshintsho kule geni lubangela ukuba iiseli zenze ulwelo olungqingqwa, olunamathelayo. Uninzi lwabantu abane-cystic fibrosis bafunyaniswe besebancinci.

Ziziphi izinto ezinobungozi kwi-cystic fibrosis?

ICystic fibrosis sisifo semfuza. Ukuba abazali bakho banesi sifo okanye ukuba baphethe ufuzo olungalunganga, usemngciphekweni owandayo wokuba nesifo. Umntu one-cystic fibrosis kufuneka azuze ilifa zofuzo ezimbini eziguqulweyo, omnye kumzali ngamnye. Ukuba uphatha ikopi enye yemfuza, awuyi kuba ne-cystic fibrosis kodwa ungumphathi wesifo. Ukuba abathwali bemfuza babini banomntwana, kukho iipesenti ezingama-25 zamathuba okuba umntwana wabo abe ne-cystic fibrosis. Kukho ithuba leepesenti ezingama-50 lokuba umntwana wabo azokuyiphatha imfuza kodwa angabinayo i-cystic fibrosis.

ICystic fibrosis ikwaxhaphake kakhulu kubantu abavela eNyakatho Yurophu.

I-EPI kunye necystic fibrosis zihambelana njani?

I-EPI sisisombululo esikhulu se-cystic fibrosis. ICystic fibrosis sesona sizathu sixhaphakileyo se-EPI, emva kwepancreatitis engapheliyo. Kwenzeka kuba i-mucus eshinyeneyo kwi-pancreas yakho ithintela ii-enzyme zepancreatic ekungeneni emathunjini amancinci.

Ukunqongophala kwee-enzyme zepancreatic kuthetha ukuba indlela yakho yokwetyisa kufuneka idlulise ukutya okungafakwanga emzimbeni. Amafutha kunye neeproteni zinzima ngakumbi kubantu abane-EPI yokwetyisa.

Oku kugaya kunye nokutya kukutya kunokukhokelela ku:

• intlungu zesisu
• ukudumba
• ukuqhina
• urhudo
• izitulo ezinamafutha nezikhululekileyo
• ukuhla ukusinda
• ukungondleki

Nokuba utya ukutya okuqhelekileyo, icystic fibrosis inokwenza kube nzima ukugcina ubunzima obusempilweni.

Zeziphi iintlobo zonyango ezikhoyo ze-EPI?

Indlela yokuphila esempilweni kunye nokutya okunesondlo kunokukunceda ulawule i-EPI yakho. Oku kuthetha ukunciphisa ukusela utywala, ukunqanda ukutshaya, kunye nokutya ukutya okunesondlo kunye nemifuno eninzi kunye neenkozo ezipheleleyo. Uninzi lwabantu abane-cystic fibrosis banokutya ukutya okuqhelekileyo apho iipesenti ezingama-35 ukuya kuma-45 zeekhalori zivela kumanqatha.

Kuya kufuneka uthathe indawo ye-enzyme nako konke ukutya kwakho kunye nokutya okuncinci ukuze uphucule ukwetyisa. Ukusetyenziswa kwesongezo kunokunceda ekwenzeni iivithamini i-EPI ethintela umzimba wakho ekufunxeni.

Ukuba awukwazi ukugcina ubunzima obunempilo, ugqirha wakho unokucebisa ukuba usebenzise ityhubhu yokondla ebusuku ukukhusela ukungondleki kwi-EPI.

Kubalulekile ukuba ugqirha wakho abeke esweni umsebenzi wakho wepancreatic, nokuba awunamsebenzi owonileyo ngoku kuba unokuhla kwixesha elizayo. Ukwenza njalo kuyakwenza imeko yakho ilawuleke ngakumbi kwaye kunciphise amathuba akho okonzakala ngakumbi kwiipancreas zakho.

Ukuthatha

Kwixesha elidlulileyo, abantu abane-cystic fibrosis babenethemba elifutshane kakhulu lobomi. Namhlanje, iipesenti ezingama-80 zabantu abane-cystic fibrosis bafikelela ebudaleni. Oku kungenxa yenkqubela phambili enkulu kunyango kunye nolawulo lweempawu. Ke ngelixa kusekho unyango lwe-cystic fibrosis, kukho ithemba elininzi.