Umbhali: Christy White
Umhla Wokudalwa: 6 Ucanzibe 2021
Hlaziya Umhla: 1 Isilimela 2025
Anonim
Phenylketonuria - causes, symptoms, diagnosis, treatment, pathology
Ividiyo: Phenylketonuria - causes, symptoms, diagnosis, treatment, pathology

Umxholo

I-Phenylalanine inokunceda kulawulo lobunzima kuba ithatha inxaxheba kwiinkqubo ezilawula ukutya kunye nokunika umzimba imvakalelo yokuhlutha. I-Phenylalanine yi-amino acid enokufumaneka ngokwendalo kukutya okunotyebileyo kwiiprotein, njengenyama, intlanzi kunye nobisi kunye neemveliso zobisi, nangohlobo lwezongezelelo ezithengiswa ezikhemesti nakwiivenkile zokutya ezempilo.

Ukusetyenziswa kwezongezo ze-phenylalanine kufuneka kumiselwe ngugqirha okanye kwisondlo kwaye kuyaphikiswa kubantu abaneengxaki ezinje ngoxinzelelo lwegazi, isifo sentliziyo kunye nabasetyhini abakhulelweyo.

Isenzo se phenylalanine kulawulo lwendlala

I-Phenylalanine isebenza kulawulo lwendlala kuba ithatha inxaxheba ekwakheni i-dopamine kunye ne-norepinephrine, izinto ezibalulekileyo kulawulo lokutya kunye nezibandakanyekayo kulawulo lokufunda, imood kunye nenkumbulo. Ukongeza, i-phenylalanine ivuselela imveliso yecholecystokinin hormone, esebenza emathunjini kwaye inike umzimba imvakalelo yokuhlutha.


Ngokwesiqhelo idosi ekucetyiswa ngayo i-phenylalanine yi-1000 ukuya kwi-2000 mg ngosuku, kodwa iyahluka ngokweempawu zomntu, ezinje ngeminyaka, umsebenzi womzimba kunye nobukho beengxaki ezinje ngoxinzelelo kunye noxinzelelo. Nangona kunjalo, ukongezwa kwe-phenylalanine kukodwa akwanelanga ukunciphisa umzimba, kuba ukunciphisa umzimba kwenzeka kuphela xa kukho ukutya okunempilo.

Ukutya okuphezulu kwi-phenylalanineUncedo lwePhenylalanine

Inkathalo ekufuneka ithathiwe ngokuxhaswa kwe phenylalanine

Kuya kufuneka ulumkele ukongezwa kwe-phenylalanine kuba ukugqitha kwale amino acid kunokuba neziphumo ebezingalindelekanga ezinjengokutsha kwentliziyo, isicaphucaphu kunye nentloko ebuhlungu. I-phenylalanine nayo iyangqinelana kwiimeko zoku:


  • Izifo zentliziyo;
  • Uxinzelelo lwegazi;
  • Abafazi abakhulelweyo okanye abancancisayo;
  • Abantu abathatha iziyobisi ukunyanga uxinzelelo okanye ezinye iingxaki zengqondo;
  • Abantu abane phenylketonuria.

Ke, ukongezwa kwe phenylalanine kufuneka kukhokelwe ngugqirha okanye isondlo sokutya ukuqinisekisa iziphumo eziluncedo.

Ukutya okuphezulu kwi-phenylalanine

I-Phenylalanine ngokwendalo ikhona kukutya okunotyebileyo kwiiproteni, njengenyama, intlanzi, ubisi kunye neemveliso zobisi, amandongomane, iimbotyi zesoya, iimbotyi kunye nombona. Ukusetyenziswa kwe-phenylalanine ekutyeni akubeki emngciphekweni wezempilo kwaye ngabantu abane-phenylketonuria kuphela abafanele bakuphephe oku kutya. Jonga uluhlu olupheleleyo lokutya okune-Phenylalanine.

Ukuba ujonge ukunciphisa umzimba, jonga kwakhona:

  • Ukuthoba umzimba ngokukhawuleza
  • Ukwenza ukutya okunempilo ukunciphisa umzimba

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