Uyichonga njani kwaye uyiphatha njani i-pheochromocytoma

Umxholo
- Zeziphi iimpawu eziphambili
- Uxilongo lwenziwa njani
- Unyango lwenziwa njani
- Utyando lwePheochromocytoma
- Unyango lwe-pheochromocytoma enobungozi
- Iimpawu zokuphucula
- Iimpawu zokuba mandundu
I-Pheochromocytoma sisifo esibi esivela kwidlala ye-adrenal, ebekwe ngaphezulu kwezintso. Nangona olu hlobo lwethumba lungabeki ubomi emngciphekweni, lunokuvelisa iingxaki zempilo ezininzi, ngakumbi njengoko amadlala eadrenal avelisa iihomoni ezilawula ukusebenza kwawo onke amalungu omzimba.
Ke, njengoko iihomoni ziveliswa ngokuchanekileyo ngenxa yobukho bethumba, kuyinto eqhelekileyo ukuba noxinzelelo lwegazi olunganciphisi kunye nezinye iingxaki zentliziyo.
Ngesi sizathu, nangona ingesiso isifo somhlaza, kwiimeko ezininzi, i-pheochromocytoma kufuneka isuswe ngotyando ukunqanda ukwenzakala kwamanye amalungu ngokuhamba kwexesha.

Zeziphi iimpawu eziphambili
Iimpawu zolu hlobo lwethumba zihlala ziphakathi kweminyaka engama-20 nengama-50 kwaye zibandakanya:
- Igazi elonyukayo;
- Ukunyuka kwentliziyo;
- Ukubila okugqithisileyo;
- Intloko ebuhlungu;
- Iinyikima;
- Pallor ebusweni;
- Ukuziva uphefumla kancinci.
Ngokwesiqhelo ezi mpawu ze-pheochromocytoma zivela kwiingxaki ezihlala phakathi kwemizuzu eli-15 ukuya kwengama-20, kwaye zinokwenzeka ngaphezu kwesinye ngosuku. Nangona kunjalo, uxinzelelo lwegazi luhlala luhlala luphezulu kwaye kunzima ukulawula.
Ezi ngxaki zeempawu zixhaphake kakhulu emva kweemeko ezinjengokuzivocavoca umzimba, ukuba novalo kakhulu okanye ukuxhalaba, ukutshintsha imeko yomzimba, ukusebenzisa igumbi lokuhlambela okanye ukutya ukutya okutyebileyo kwi-tyrosine, ezinje ngeeshizi, iavokhado okanye inyama etshayiweyo. Jonga uluhlu olupheleleyo lokutya okune-tyrosine.
Uxilongo lwenziwa njani
Ukuqinisekisa ukuxilongwa kwe-pheochromocytoma, ugqirha unokuyalela iimvavanyo ezininzi ezinje ngeemvavanyo zegazi ezilinganisa iihomoni eziveliswa ngamadlala adrenal, anje ngeadrenaline okanye norepinephrine, kunye nekhompyuter yecomputer okanye imaging resonance imaging, evavanya ukwakheka kwe-adrenal amadlala.
Unyango lwenziwa njani
Olona hlobo lonyango lonyango lwe-pheochromocytoma kukuba kwenziwe utyando ukususa ithumba kwincindi ye-adrenal echaphazelekayo. Nangona kunjalo, ngaphambi kokwenza utyando, ugqirha unokumisela amayeza athile anceda ukulawula uxinzelelo kunye nokunciphisa umngcipheko weengxaki, ezinje:
- Iibhlokhi zeAlfa, ezinje ngeDoxazosin okanye iTerazosin: ukuphucula ukujikeleza kwegazi kunye nokunciphisa uxinzelelo lwegazi;
- Ibhlokhi yeBeta, ezinje ngeAtenolol okanye iMetoprolol: ukunciphisa ukubetha kwentliziyo kunye nokugcina uxinzelelo lwegazi phantsi kolawulo;
- Olunye ulungiso lwexinzelelo lwegazi oluphezulu, ezinje ngeCaptopril okanye iAmlodipine: zisetyenziswa xa uxinzelelo lwegazi lungehli ngokusebenzisa ii-alpha okanye ii-beta blocker.
La machiza ahlala esetyenziswa kangangesithuba seentsuku ezili-10 ngaphambi kotyando.
Xa uxinzelelo lulawulwa, kuhlala kunokwenzeka ukwenza utyando ukususa ithumba. Kwiimeko ezininzi, yonke i-adrenal gland iyasuswa ngexesha lotyando, nangona kunjalo, ukuba elinye idlala lisusiwe, ugqirha uzama ukususa kuphela ummandla ochaphazelekayo wedlala, ukuze icandelo elisempilweni liqhubeke nokusebenza ngokwesiqhelo.
Utyando lwePheochromocytoma
Unyango lwe-pheochromocytoma lwenziwa, kwiimeko ezininzi, ngoqhaqho ukuzama ukususa ithumba elininzi kwincindi ye-adrenal echaphazelekayo.
Utyando lwe-Pheochromocytoma lwenziwa phantsi kwe-anesthesia ngokubanzi kwaye, kwiimeko ezininzi, ugqirha ukhetha ukususa lonke idlala le-adrenal elichaphazelekayo, ukunciphisa umngcipheko wesisu ukubuya. Nangona kunjalo, ukuba elinye idlala lichaphazelekile okanye ukuba sele ndilisusile ngaphambili, ugqirha ususa kuphela icandelo elichaphazelekayo ledlala, egcina indawo esempilweni.
Ngokubanzi, incindi esempilweni iyakwazi ukugcina ukusebenza kwayo kwaye ivelise iihomoni ezifunekayo emzimbeni. Nangona kunjalo, xa le mveliso inyanzelisiwe, ugqirha unokuyalela ukutshintshwa kwehomoni, enokuthi yenziwe ubomi bonke.
Unyango lwe-pheochromocytoma enobungozi
Nangona i-pheochromocytoma inqabile, inokuba sisisu esibuhlungu kwaye, kwezi meko, emva kotyando kunokuba yimfuneko ukwenza i-chemotherapy okanye i-radiotherapy yokuphelisa zonke iiseli ezinobungozi okanye i-metastases, kuxhomekeke kwinqanaba lokuvela kwethumba.
Iimpawu zokuphucula
Iimpawu zokuqala zophuculo zibonakala malunga neveki enye emva kokuqalisa unyango ngamachiza kwaye zibandakanya ukwehla koxinzelelo lwegazi kunye nokubetha kwentliziyo. Emva kotyando, zonke iimpawu ziyanyamalala ngokupheleleyo. Nangona kunjalo, kwimeko yomhlaza onobungozi, ezinye iimpawu zisenokugcinwa okanye iimpawu zomhlaza ezineemastastase ezinjengeentlungu ngaphandle kwesizathu esibonakalayo okanye ukwehla kobunzima, umzekelo, kunokuvela.
Iimpawu zokuba mandundu
Iimpawu zokuba mandundu ngakumbi rhoqo ngelixa unyango lungaqalanga kwaye lunokubandakanya ukungcangcazela okwandayo, intloko ebuhlungu kunye nokuphefumla okufutshane, kunye nokunyuka okuphawulekayo koxinzelelo lwegazi kunye nokubetha kwentliziyo.