Konke malunga ne-Antiphospholipid Syndrome (i-Hughes Syndrome)

Umxholo

• Iimpawu Hughes syndrome
• Oonobangela Hughes syndrome
• Ukuchongwa kwesifo seHughes
• Unyango lwe-Hughes syndrome
• Ukutya kunye nokuzilolonga kwesifo seHughes
• Imbonakalo

Ushwankathelo

I-Hughes syndrome, ekwabizwa ngokuba yi "sticky syndrome" okanye isifo se-antiphospholipid (APS), sisimo sokuzimela komzimba esichaphazela indlela iiseli zegazi zakho ezidibana ngayo, okanye ezijiyileyo. Hughes syndrome ithathwa ezinqabileyo.

Abasetyhini abaphulukana nokulahleka kwesisu kunye nabantu abane-stroke ngaphambi kweminyaka engama-50 ngamanye amaxesha bafumanisa ukuba i-Hughes syndrome yayingunobangela oyintloko. Kuqikelelwa ukuba isifo i-Hughes sichaphazela amatyeli amathathu ukuya kwamahlanu abasetyhini kunamadoda.

Nangona unobangela we-Hughes syndrome engacacanga, abaphandi bakholelwa ukuba ukutya, indlela yokuphila, kunye nemfuzo zinokuba nefuthe ekuphuhliseni imeko.

Iimpawu Hughes syndrome

Iimpawu ze-Hughes syndrome kunzima ukuzibona, kuba amahlwili egazi ayisiyonto onokuyichonga ngokulula ngaphandle kweminye imeko yezempilo okanye iingxaki. Ngamanye amaxesha isifo i-Hughes sibangela irhashalala ebomvu okanye ukuphuma kwegazi empumlweni nasezintsinini.

Ezinye iimpawu ezinokuthi ube ne-Hughes syndrome zibandakanya:

• ukuphuma kwesisu okanye ukuzala umntwana oswelekileyo
• amahlwili egazi emilenzeni
• Ukuhlaselwa kwe-ischemic okwethutyana (i-TIA) (ngokufana nokubetha, kodwa ngaphandle kwemiphumo esisigxina ye-neurologic)
• ukubetha, ngakumbi ukuba ungaphantsi kweminyaka engama-50
• ubalo lwegazi olusezantsi
• ukuhlaselwa yintliziyo

Abantu abane-lupus abane-Hughes syndrome.

Kwiimeko ezinqabileyo, i-Hughes syndrome enganyangekiyo inokunyuka ukuba unezihlo zokunqakumba ngaxeshanye kuwo wonke umzimba. Oku kubizwa ngokuba yintlekele ye-antiphospholipid syndrome, kwaye kunokubangela umonakalo omkhulu kwizitho zakho kunye nokufa.

Oonobangela Hughes syndrome

Abaphandi basasebenza ukuqonda izizathu ze-Hughes syndrome. Kodwa bazimisele ukuba kukho into yemfuzo edlalayo.

I-Hughes syndrome ayidluliswanga ngokuthe ngqo kumzali, ngendlela ezinye iimeko zegazi, ezinjenge-hemophilia, ezinokuba njalo. Kodwa ukuba nelungu losapho kunye ne-Hughes syndrome kuthetha ukuba kunokwenzeka ukuba uphuhle imeko.

Kungenzeka ukuba i-gene exhunywe kwezinye iimeko ezizimeleyo nayo ibangela i-Hughes syndrome. Oko kungachaza ukuba kutheni abantu abanale meko behlala benezinye iimeko zokuzimela.

Ukuba nosulelo oluthile lwentsholongwane okanye ibacteria, njenge E. coli okanye i-parvovirus, inokubangela ukuba i-Hughes syndrome ikhule emva kokosuleleka kosulelo. Amayeza okulawula isifo sokuwa, kunye nezinto zokucwangcisa ngomlomo, nazo zinokudlala indima ekuvuseleleni imeko.

Ezi meko zokusingqongileyo zinokunxibelelana nezinto zokuphila-njengokungafumani umthambo ngokwaneleyo kunye nokutya ukutya okuphezulu kwi-cholesterol- kunye ne-Hughes syndrome.

Kodwa abantwana kunye nabantu abadala ngaphandle kolunye lwezi zifo, izinto zokuphila, okanye ukusetyenziswa kwamachiza banokufumana i-Hughes syndrome nanini na.

Izifundo ezingakumbi ziyafuneka ukulungisa izizathu zeHughes syndrome.

Ukuchongwa kwesifo seHughes

I-Hughes syndrome ifunyanwa kuthotho lweemvavanyo zegazi. Olu vavanyo lwegazi luhlalutya izilwa-buhlungu ezenziwa ngamaseli akho omzimba ukuze abone ukuba aziphatha kakuhle na okanye ajolise kwezinye iiseli ezisempilweni.

Uvavanyo lwegazi oluqhelekileyo oluchaza i-Hughes syndrome ibizwa ngokuba yi-antibody immunoassay. Ungadinga ukuba kwenziwe okuninzi kwezi zinto ngaphandle kweminye imiqathango.

I-Hughes syndrome inokuchazwa gwenxa njenge-multiple sclerosis kuba iimeko ezimbini zineempawu ezifanayo. Uvavanyo olucokisekileyo kufuneka luchonge isifo oluchanekileyo, kodwa kungathatha ixesha.

Unyango lwe-Hughes syndrome

I-Hughes syndrome inokunyangwa ngegazi elincinci (amayeza anciphisa umngcipheko wegazi).

Abanye abantu abane-Hughes syndrome ababonisi zimpawu zegazi kwaye abayi kufuna naluphi na unyango olungaphaya kwe-aspirin ukuthintela umngcipheko wokuvela kwamahlwili.

Amayeza e-Anticoagulant, njenge-warfarin (Coumadin) anokumiselwa, ngakumbi ukuba unembali ye-vein thrombosis enzulu.

Ukuba uzama ukuthwala ukukhulelwa ukuya kwikota kwaye une-Hughes syndrome, unokumiselwa i-aspirin yedosi ephantsi okanye idosi yemihla ngemihla yegazi le-heparin.

Abasetyhini abane-Hughes syndrome banama-80 eepesenti kunokwenzeka ukuba baphathe usana ukuya kwikota ukuba bafumanekile kwaye baqala unyango olulula.

Ukutya kunye nokuzilolonga kwesifo seHughes

Ukuba ufunyaniswe une-Hughes syndrome, ukutya okusempilweni kunokuwunciphisa umngcipheko weengxaki ezinokubakho, njenge-stroke.

Ukutya ukutya okutyebileyo kwiziqhamo kunye nemifuno kunye namafutha asezantsi kunye neeswekile kuya kukunika inkqubo esempilweni yentliziyo, wenze amahlwili egazi mancinci.

Ukuba uphatha i-Hughes syndrome nge-warfarin (Coumadin), ikliniki yaseMayo ikucebisa ukuba ungqinelane nobungakanani bevithamini K oyityayo.

Ngelixa inani elincinci levithamini K linokungaluchaphazeli unyango lwakho, ukwahluka rhoqo kokutya kwakho ivithamin K kunokwenza ukuba unyango lwakho lutshintshe ngendlela eyingozi. I-Broccoli, ihlumelo laseBrussels, iimbotyi ze-garbanzo, kunye neavokhado zezinye zokutya okuphezulu ku-vitamin K.

Ukufumana umthambo rhoqo kunokuba yinxalenye yokulawula imeko yakho. Kunqande ukutshaya kwaye ugcine ubunzima obuphilileyo kuhlobo lomzimba wakho ukugcina intliziyo yakho kunye nemithambo yomelele kwaye iyakwazi ukumelana nomonakalo.

Imbonakalo

Uninzi lwabantu abane-Hughes syndrome, iimpawu kunye neempawu zinokulawulwa ngamagazi kunye namayeza e-anticoagulant.

Kukho iimeko ezithile apho olu nyango alusebenzi, kwaye ezinye iindlela kufuneka zisetyenziselwe ukugcina igazi lakho lingonakali.

Ukuba ayishiywanga inganyangwa, i-Hughes syndrome ingonakalisa inkqubo ye-cardiovascular system kwaye inyuse umngcipheko kwezinye iimeko zempilo, njengokukhulelwa kwesisu kunye nokubetha. Unyango lwe-Hughes syndrome luphela ubomi, njengoko kungekho nonyango kule meko.

Ukuba unayo nayiphi na kwezi zinto zilandelayo, thetha nogqirha wakho malunga nokuvavanywa kwesifo i-Hughes syndrome:

• ngaphezulu kwegazi elinye eliqinisekisiweyo elibangele iingxaki
• Ukuphulukana nesisu esinye okanye nangaphezulu emva kweveki ye-10 yokukhulelwa
• Ukuphulukana kwesithathu okanye nangaphezulu kwangoko kwinyanga yokuqala yokukhulelwa