I-porphyria yesikhumba

Umxholo

• Iimpawu ze-porphyria ezinqamlekileyo
• Unyango lwe-porphyria enqamlezileyo

Ulusu emva kwexesha lolona hlobo luqhelekileyo lwe-porphyria ebangela ukuba izilonda ezincinci zivele kulusu olubonakaliswe elangeni, njengasemva kwesandla, ebusweni okanye entlonzeni, ngenxa yokunqongophala kwe-enzyme eveliswa sisibindi esikhokelela ingqokelela yentsimbi eluswini.igazi kunye nolusu. I-porphyria enqamlezileyo ayinalo unyango, kodwa inokulawulwa ngokusetyenziswa kwamayeza amiselwe ngugqirha wesikhumba.

Ngokubanzi, ukulibaziseka kwesikhumba i-porphyria ibonakala xa sele umdala, ngakumbi kwizigulana ezihlala zisela utywala okanye ezineengxaki zesibindi, njenge-hepatitis C, umzekelo.

Ukuphela kwesikhumba i-porphyria ihlala ingeyoyofuzo, nangona kunjalo, kwezinye iimeko inokudlula isuka kubazali iye ebantwaneni, kwaye ingcebiso ngemfuzo iyacetyiswa ngaphambi kokukhulelwa, ukuba kukho iimeko ezininzi kusapho.

Iimpawu ze-porphyria ezinqamlekileyo

Uphawu lokuqala lwe-porphyria enqamlezileyo kukuvela kwamadyungudyungu kulusu olubonakaliswe elangeni, oluthatha ixesha ukuphilisa, nangona kunjalo, ezinye iimpawu zibandakanya:

• Ukukhula okugqithisileyo kweenwele ebusweni;
• Ulusu oluqinileyo kwezinye iindawo, njengeengalo okanye ubuso;
• Umchamo omnyama.

Emva kokuba i-blister inyamalale, amabala okanye iindawo ezikhanyayo zinokubonakala zithatha ixesha elide ukuphola.

Ukuchongwa kwe-porphyria esikiweyo kufuneka kwenziwe ngugqirha wesikhumba ngokusebenzisa uvavanyo lwegazi, umchamo kunye nelindle ukuqinisekisa ubukho be-porphyrin kwiiseli, njengoko iyinto eveliswa sisibindi ngexesha lesi sifo.

Unyango lwe-porphyria enqamlezileyo

Unyango lwe-porphyria enqamlezileyo kufuneka ikhokelwe ngugqirha wesikhumba ngokusebenzisana ne-hepatologist, kuba kufuneka kulawulwe amanqanaba e-porphyrin eveliswa sisibindi. Ke, kuxhomekeka kwiimpawu zesigulana, unyango lunokwenziwa ngamayeza epherphyria esikiweyo, enje nge-chloroquine okanye i-hydroxychloroquine, ukurhoxiswa kwegazi rhoqo ukunciphisa amanqanaba e-iron kwiiseli okanye ukudityaniswa kwazo zombini.

Ukongeza, ngexesha lonyango kuyacetyiswa ukuba isigulana sikuphephe ukusela utywala kunye nokuvezwa lilanga, nkqu ne-sunscreen, kwaye eyona ndlela yokukhusela ulusu elangeni kukusebenzisa iblukhwe, ijezi ezinemikhono emide, umnqwazi kunye neiglavu, umzekelo .