Uxinzelelo lwegazi lwePulmonary Arterial Hypertension: Ubomi bokulindelwa kunye ne-Outlook

Umxholo

• Ukulindelwa kobomi kubantu abane-PAH
• Inqanaba lokusebenza kwePAH
• Iklasi 1
• Iklasi 2
• Iklasi 3
• Iklasi 4
• Iinkqubo zokuvuselelwa kweCardiopulmonary
• Ungasebenza njani ngePAH
• Inkxaso kunye nenkathalo ye-PAH
• Ubomi kunye ne-PAH

Uxinzelelo lwegazi lwe-pulmonary arterial (PAH) luhlobo olunqabileyo loxinzelelo lwegazi olubandakanya icala lasekunene lentliziyo yakho kunye nemithambo ehambisa igazi kwimiphunga yakho. Le mithambo ibizwa ngokuba yimithambo yegazi yemiphunga.

I-PAH yenzeka xa imithambo yakho yemiphunga iyakhula okanye iqine kwaye icuthe ngaphakathi apho igazi lihamba khona. Oku kwenza ukuhamba kwegazi kube nzima ngakumbi.

Ngesi sizathu, intliziyo yakho kufuneka isebenze nzima ukutyhala igazi kwimithambo yakho yemiphunga. Ngokulandelayo, le mithambo ayinakukwazi ukuhambisa igazi elaneleyo kwimiphunga yakho yokutshintshiselana okwaneleyo komoya.

Xa oku kusenzeka, umzimba wakho awukwazi ukufumana ioksijini oyifunayo. Ngenxa yoko, uyadinwa ngokulula.

Ezinye iimpawu zingabandakanya:

• ukuqhawukelwa ngumphefumlo
• iintlungu esifubeni okanye uxinzelelo
• ukubetha kwentliziyo
• isiyezi
• isiqaqa
• ukudumba ezingalweni nasemilenzeni
• ukubetha kwentliziyo

Ukulindelwa kobomi kubantu abane-PAH

Uphononongo olwenziwe yiRegistry lokuVavanya uLawulo lweZifo lwe-PAH lwakwangoko kunye nexesha elide (UKUVULA) lufumanise ukuba abathathi-nxaxheba abafunda nePAH banala manqanaba okusinda alandelayo:

• Ipesenti ezingama-85 kunyaka omnye
• Iipesenti ezingama-68 kwiminyaka emi-3
• Iipesenti ezingama-57 kwiminyaka emi-5

Kubalulekile ukuba uqaphele ukuba amazinga okusinda akakho kwindalo iphela. Ezi ntlobo zezibalo azinakho ukuqikelela isiphumo sakho.

Umbono womntu wonke uhlukile kwaye unokuhluka ngokubanzi, kuxhomekeke kuhlobo lwe-PAH onalo, ezinye iimeko, kunye nokhetho lonyango.

Nangona i-PAH ingenalo unyango lwangoku, inokunyangwa. Unyango lunokunciphisa iimpawu kwaye lunokulibazisa ukuqhubela phambili kwale meko.

Ukufumana unyango olufanelekileyo, abantu abane-PAH bahlala bethunyelwa kwiziko elikhethekileyo loxinzelelo lwegazi kwimvavanyo kunye nolawulo.

Ngamanye amaxesha, ukufakelwa kwemiphunga kunokwenziwa njengonyango. Nangona oku akunakuphucula indlela ojonga ngayo, ukufakelwa kwemiphunga kunokuba luncedo kwi-PAH engaphenduliyo kwezinye iintlobo zonyango.

Inqanaba lokusebenza kwePAH

Ukuba unayo i-PAH, ugqirha wakho uya kuthi asebenzise inkqubo esemgangathweni yokubeka "inqanaba lokusebenza" kwakho. Oku kuxelela ugqirha wakho okuninzi malunga nobukrakra be-PAH.

Ukuqhubela phambili kwe-PAH kwahlulwe kwaba. Inombolo eyabelwe i-PAH yakho ichaza ukuba kulula kangakanani ukwenza imisebenzi yemihla ngemihla kunye nokuba isifo sichaphazele njani usuku lwakho.

Iklasi 1

Kule klasi, i-PAH ayikhawuleli kwimisebenzi yakho yesiqhelo. Ukuba wenza imisebenzi yomzimba eqhelekileyo, awuzukukhulisa naziphi na iimpawu zePAH.

Iklasi 2

Kwiklasi yesibini, i-PAH ichaphazela kuphela imisebenzi yakho yomzimba. Awunazo iimpawu ze-PAH xa uphumle. Kodwa isenzo sakho esiqhelekileyo somzimba sinokubangela ngokukhawuleza iimpawu, kubandakanya iingxaki zokuphefumla kunye nentlungu esifubeni.

Iklasi 3

Iiklasi ezimbini zokugqibela ezisebenzayo zibonisa ukuba i-PAH ikhula ngokuthe ngcembe.

Okwangoku, awuzukuphazamiseka xa uphumle. Kodwa ayithathi msebenzi omninzi wokubangela iimpawu kunye noxinzelelo lomzimba.

Iklasi 4

Ukuba uneklasi IV PAH, ngekhe wenze imisebenzi yomzimba ngaphandle kokufumana iimpawu ezinzima. Ukuphefumla kuyasebenza, nokuba uphumle. Usenokudinwa lula. Inani elincinci lomsebenzi womzimba linokwenza ukuba iimpawu zakho zibe mandundu.

Iinkqubo zokuvuselelwa kweCardiopulmonary

Ukuba ufumene ukuxilongwa kwe-PAH, kubalulekile ukuba uhlale usebenza ngokusemandleni akho njengoko unako.

Nangona kunjalo, umsebenzi onzima unokuwonakalisa umzimba wakho. Ukufumana indlela elungileyo yokuhlala usebenza nge-PAH kunokuba ngumceli mngeni.

Ugqirha wakho unokucebisa iiseshoni zokuvuselela i-cardiopulmonary zokukunceda ufumane ibhalansi elungileyo.

Abaqeqeshi bezempilo abaqeqeshiweyo banokukunceda ukuba wenze inkqubo ebonelela ngokuzivocavoca ngokwaneleyo ngaphandle kokukutyhalela ngaphaya kwezinto ezinokuphathwa ngumzimba wakho.

Ungasebenza njani ngePAH

Ukuxilongwa kwe-PAH kuthetha ukuba uya kujongana nezithintelo ezithile. Umzekelo, uninzi lwabantu abane-PAH akufuneki baphakamise nantoni na enzima. Ukuphakamisa okunzima kunokunyusa uxinzelelo lwegazi, olunokuthi lube nzima kwaye lukhawuleze iimpawu.

Inani lamanyathelo anokukunceda ulawule uxinzelelo lwexinzelelo lwe-pulmonary, kubandakanya i-PAH:

• Yiya kuzo zonke iindawo zonyango kwaye ufune iingcebiso ukuba iimpawu ezintsha ziyavela okanye iimpawu ziba mandundu.
• Yiba nokugonywa ukukhusela umkhuhlane kunye nesifo se-pneumococcal.
• Buza malunga nenkxaso yeemvakalelo nezentlalo ukunceda ukulawula uxinzelelo kunye noxinzelelo.
• Yenza uvavanyo lomzimba kwaye uhlale usebenza kangangoko.
• Sebenzisa ioksijini eyongezelelweyo ngexesha leenqwelo moya okanye kwindawo ephezulu.
• Gwema i-anesthesia jikelele kunye ne-epidurals, ukuba kunokwenzeka.
• Gwema iibhafu ezishushu kunye nee-saunas, ezinokuthi zibeke uxinzelelo emiphungeni okanye entliziyweni.
• Yitya ukutya okunezondlo ukukhulisa impilo kunye nokuba sempilweni.
• Kuphephe ukutshaya. Ukuba uyatshaya, thetha nogqirha wakho malunga nokuseta isicwangciso sokuyeka.

Nangona kuyi nyaniso ukuba izigaba eziphambili ze-PAH zingakhula ngakumbi ngomsebenzi womzimba, ukuba ne-PAH akuthethi ukuba kufuneka ugweme umsebenzi ngokupheleleyo. Ugqirha wakho unokukunceda uqonde ukusikelwa umda kwakho kwaye ufumane izisombululo.

Ukuba ucinga ukukhulelwa, thetha nogqirha wakho kuqala. Ukukhulelwa kunokubeka uxinzelelo olongezelelweyo kwimiphunga nakwintliziyo yakho.

Inkxaso kunye nenkathalo ye-PAH

Njengoko i-PAH iqhubeka, ubomi bemihla ngemihla bunokuba ngumceli mngeni, nokuba kungenxa yeentlungu, ukuphefumla kancinci, ukukhathazeka ngekamva, okanye ezinye izinto.

Amanyathelo enkxaso anokukunceda wandise umgangatho wobomi bakho ngeli xesha.

Unokufuna olu nyango luxhasayo lulandelayo, kuxhomekeka kwiimpawu zakho:

• womchamo kwimeko ukusilela ventricular ekunene
• Unyango lwe-anemia, ukuswela i-iron, okanye zombini
• ukusetyenziswa kwamayeza avela kwiklasi ye-endothelin receptor antagonist (ERA), efana ne-ambrisentan

Njengoko i-PAH iqhubeka, kuya kuba kufanelekile ukuxoxa ngezicwangciso zokhathalelo lokuphela kobomi nabantu obathandayo, abanonopheli, kunye nabanikezeli bezempilo. Iqela lakho lokhathalelo lwempilo lunokukunceda wenze isicwangciso osifunayo.

Ubomi kunye ne-PAH

Umdibaniso wotshintsho kwindlela yokuphila, amayeza kunye notyando lunokutshintsha ukuqhubekeka kwe-PAH.

Nangona unyango lungenakuguqula iimpawu ze-PAH, uninzi lonyango lunokongeza iminyaka ebomini bakho.

Thetha nogqirha wakho malunga nokufumana unyango olufanelekileyo kwi-PAH yakho. Bangasebenza nawe ukulibazisa ukuqhubela phambili kwe-PAH kunye nokugcina umgangatho wobomi.