Umbhali: Roger Morrison
Umhla Wokudalwa: 18 Eyomsintsi 2021
Hlaziya Umhla: 1 Eyekhala 2024
Anonim
I-Shy-Drager syndrome: yintoni, iimpawu kunye nonyango - Zempilo
I-Shy-Drager syndrome: yintoni, iimpawu kunye nonyango - Zempilo

Umxholo

I-Shy-Drager syndrome, ekwabizwa ngokuba yi "multiple atrophy system with orthostatic hypotension" okanye "MSA" sisizathu esinqabileyo, esibi nesingaziwayo, esibonakaliswa kukuwohloka kweeseli kumbindi kunye nokuzimela kwenkqubo yemithambo-luvo, elawula imisebenzi utshintsho olungazenzisiyo kwi umzimba.

Uphawu olukhoyo kuzo zonke iimeko, kukuhla koxinzelelo lwegazi xa umntu ephakama okanye elele phantsi, nangona kunjalo abanye banokubandakanyeka kwaye ngenxa yesi sizathu yahlulwe yaziintlobo ezi-3, umahluko wazo:

  • I-Parkinsonian shy-drager syndrome: ibonisa iimpawu zesifo sika-Parkinson, ezinje, apho ukuhamba kancinci, ukuqina kwemisipha kunye nokungcangcazela;
  • I-Cerebellar shy-drager syndrome: ukulungelelaniswa kokulungelelaniswa kweemoto, ubunzima ekulinganiseni nasekuhambeni, kugxila kumbono, ukuginya nokuthetha;
  • Idibene ne-shy-drager syndrome: igubungela iifominsinsky kunye ne-cerebellar form, eyona inamandla kuzo zonke.

Nangona oonobangela bengaziwa, kukho urhano lokuba i-shy-drager syndrome ifunyenwe njengelifa.


Iimpawu eziphambili

Iimpawu eziphambili zeSy-Drager syndrome zezi:

  • Nciphisa ukubila, iinyembezi kunye namathe;
  • Kunzima ukubona;
  • Ubunzima bokuchama;
  • Ukuqunjelwa;
  • Ukungabi namandla ngokwesondo;
  • Ukunyamezelana nobushushu;
  • Ukulala ngokungapheliyo.

Le syndrome ixhaphake kakhulu kumadoda emva kweminyaka engama-50 ubudala. Kwaye ngenxa yokuba ingenazo iimpawu ezithile, kungathatha iminyaka ukufikelela kwisifo esifanelekileyo, kungoko kulibaziseka unyango olufanelekileyo, oluthi, nangona lunganyangeki, luncede ekuphuculeni umgangatho wobomi bomntu.

Uxilongo lwenziwa njani

I-syndrome ihlala iqinisekiswa siskena se-MRI ukubona ukuba loluphi utshintsho olunokubakho kwingqondo. Nangona kunjalo, olunye uvavanyo lunokwenziwa ukuvavanya ukungazibandakanyi komzimba, njengokulinganisa uxinzelelo lwegazi ulele kwaye umile, uvavanyo lokubila ukuvavanya ukubila, isinyi kunye nolusu, ukongeza kwi-electrocardiogram yokulandela umkhondo wombane osuka entliziyweni.


Unyango lwenziwa njani

Unyango lwe-Shy-Drager syndrome luqukethe ukukhulula iimpawu ezibekiweyo, kuba esi sifo asinonyango. Ihlala ibandakanya ukusetyenziswa kwamayeza afana ne-seleginin, ukunciphisa ukuveliswa kwe-dopamine kunye ne-fludrocortisone yokunyusa uxinzelelo lwegazi, kunye nonyango lwengqondo ukuze umntu akwazi ukujongana ngcono novavanyo kunye neeseshoni ze-physiotherapy, ukunqanda ukulahleka kwemisipha.

Ukongeza ukunceda ukukhulula iimpawu, kunokuboniswa la manyathelo alandelayo:

  • Ukunqunyanyiswa kokusetyenziswa kokuchama;
  • Phakamisa intloko yebhedi;
  • Ukuhlala kwindawo yokulala;
  • Ukwanda kokusetyenziswa kwetyuwa;
  • Sebenzisa imitya yelastiki kumalungu asezantsi nasesiswini, ukunciphisa ukungahambi kakuhle okubangelwa kukungcangcazela.

Kubalulekile ukuba uqaphele ukuba unyango lwe-Shy-Drager Syndrome kukuba umntu akwazi ukufumana intuthuzelo enkulu, kuba ayithinteli ukuqhubela phambili kwesi sifo.

Esi sisifo ekunzima ukusinyanga kwaye sinesimo esiqhubela phambili, kuqhelekile ukuba ukufa kubangelwe ziingxaki zentliziyo okanye zokuphefumla, ukusuka kwiminyaka esi-7 ukuya kweli-10 emva kokuqala kweempawu.


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