Bartter's syndrome: yintoni na, iimpawu eziphambili kunye nonyango

Umxholo

• Iimpawu eziphambili
• Unyango lwenziwa njani

Isifo sikaBartter sisifo esinqabileyo esichaphazela izintso kwaye sibangela ukulahleka kwe potassium, isodiyam kunye neklorine kumchamo. Esi sifo sinciphisa uxinzelelo lwe-calcium egazini kwaye sonyusa imveliso ye-aldosterone kunye ne-renin, iihormoni ezichaphazelekayo kulawulo lwexinzelelo lwegazi.

Unobangela weBartter's Syndrome yemfuza kwaye sisifo esidlula kubazali siye ebantwaneni, sichaphazele abantu ukusukela ebuntwaneni. Esi sifo asinanyango, kodwa ukuba sifunyenwe kwangethuba, sinokulawulwa ngamayeza kunye nangamachiza ezimbiwa.

Iimpawu eziphambili

Iimpawu zeBartter's Syndrome zivela ebuntwaneni, eyona iphambili yile:

• Ukungondleki;
• Ukudodobala kokukhula;
• Buthathaka kwezihlunu;
• Ukudodobala kwengqondo;
• Ukwanda komthamo womchamo;
• Ukunxanwa kakhulu;
• Ukuphelelwa ngamanzi emzimbeni;
• Ifiva;
• Urhudo okanye ukugabha.

Abantu abaneBartter's Syndrome banamanqanaba asezantsi e-potassium, iklorini, isodiyam kunye necalcium egazini labo, kodwa abanalutshintsho kumanqanaba oxinzelelo lwegazi. Abanye abantu banokuba neempawu ezibonakalayo zesifo, njengobuso obunxantathu, ibunzi elibonakalayo, amehlo amakhulu kunye neendlebe ezijonge phambili.

Ukuchongwa kweBartter's Syndrome kwenziwa ngugqirha womchamo, ngokuvavanya iimpawu zesigulana kunye novavanyo lwegazi olufumanisa amanqanaba angafaniyo kuxinaniso lwe potassium neehomoni, ezinje ngealdosterone kunye ne renin.

Unyango lwenziwa njani

Unyango lwe-Bartter's Syndrome lwenziwa kusetyenziswa izongezo zepotassium okanye ezinye izimbiwa, ezinje ngemagniziyam okanye ikhalsiyam, ukunyusa uxinizelelo lwezi zinto egazini, kunye nokungeniswa kwamanzi amaninzi, ukubuyisela ilahleko enkulu yamanzi umchamo.

Unyango lwe-diuretic olugcina i-potassium, enje nge-spironolactone, nayo iyasetyenziswa kunyango lwesi sifo, kunye ne-non-steroidal anti-inflammatory drugs such as indomethacin, ekufuneka ithathwe de kube sekupheleni kokukhula ukwenza ukukhula komntu .

Izigulana kufuneka zibe novavanyo lomchamo, igazi kunye nezintso. Oku kusebenza ekubekeni iliso ekusebenzeni kwezintso kunye neendlela zesisu, ukuthintela iimpembelelo zonyango kula malungu.