Umbhali: Charles Brown
Umhla Wokudalwa: 6 Eyomdumba 2021
Hlaziya Umhla: 29 Eyokwindla 2025
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Uyichonga njani kwaye uyiphatha njani iCaroli Syndrome - Zempilo
Uyichonga njani kwaye uyiphatha njani iCaroli Syndrome - Zempilo

Umxholo

ICaroli Syndrome sisifo esinqabileyo nesifa esichaphazela isibindi, esathi safumana igama laso kuba yayingugqirha wase-France u-Jacques Caroli owasifumanisayo ngo-1958. Sisifo esaziwa ngokuphuma kwemijelo ethwala inyongo, ibangela iintlungu ngenxa ukudumba.iziteshi ezifanayo. Inokuvelisa ii-cysts kunye nosulelo, ukongeza ekubeni unxulunyaniswa nesifo se-fibrosis yesibindi, esisifo esibi nangakumbi.

Iimpawu zeCaroli Syndrome

Esi sifo sinokuhlala ngaphandle kokubonisa naziphi na iimpawu ngaphezulu kweminyaka engama-20, kodwa xa ziqala ukubonakala zinokuba:

  • Iintlungu kwicala lasekunene lesisu;
  • Ifiva;
  • Ukutshisa ngokubanzi;
  • Ukukhula kwesibindi;
  • Isikhumba esimthubi namehlo.

Esi sifo sinokuzibonakalisa nangaliphi na ixesha ebomini kwaye sinokuchaphazela amalungu aliqela osapho, kodwa sisifumana njengesiqhelo, oko kuthetha ukuba bobabini utata nomama kufuneka babe ngabathwali bemfuza eguqulweyo ukuze umntwana azalwe enesi sifo, yiyo loo nto kunqabile kakhulu.


Ukuxilongwa kunokwenziwa ngokwenza iimvavanyo ezibonisa ukungxola kwemisipha ye-intrahepatic bile ducts, enje nge-ultrasound yesisu, i-computed tomography, i-endoscopic retrograde cholangiopancreatography kunye ne-percutaneous transcholaryngeal cholangiography.

Unyango lweCaroli Syndrome

Unyango lubandakanya ukuthatha amayeza okubulala iintsholongwane, utyando ukususa amaqhakuva (cysts) ukuba isifo sichaphazela inye kuphela yesibindi, kwaye ukufakelwa isibindi kungafuneka kwezinye iimeko. Ngokwesiqhelo, umntu kufuneka alandelwe ngoogqirha ubomi emva kokuxilongwa.

Ukuphucula umgangatho wobomi bomntu, kuyacetyiswa ukuba kulandelwe yingcali yesondlo ukuze kulungiswe ukutya, kuthintelwe ukutya okufuna amandla amaninzi esibindini, atyebile kwiityhefu kwaye atyebile kumanqatha.

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