Isifo seKlippel-Trenaunay

I-Klippel-Trenaunay syndrome (i-KTS) yimeko enqabileyo ehlala ikhona ngexesha lokuzalwa. Esi sifo sihlala sibandakanya amabala ewayine yezibuko, ukukhula okungaphaya kwamathambo kunye nezicwili ezithambileyo, kunye nemithambo yevaricose.

Uninzi lweziganeko ze-KTS zenzeka ngaphandle kwesizathu esicacileyo. Nangona kunjalo, iimeko ezimbalwa kucingelwa ukuba zidluliselwe kwiintsapho (ezizuzwe njengelifa).

Iimpawu ze-KTS zibandakanya:

• Uninzi lwebala leewayini lezibuko okanye ezinye iingxaki zemithambo yegazi, kubandakanya amabala amnyama kulusu
• Iimvumba ze-Varicose (zinokubonwa kwasebusaneni, kodwa kunokwenzeka ukuba zibonwe kamva ebuntwaneni okanye ebusheni)
• Ukungaqiniseki ngenxa yokwahluka kobude belungu (ilungu elibandakanyekayo lide)
• Ithambo, umthambo, okanye iintlungu zentliziyo

Ezinye iimpawu ezinokubakho:

• Ukopha kwi-rectum
• Igazi kumchamo

Abantu abakule meko banokuba nokukhula okugqithisileyo kwamathambo kunye nezicubu ezithambileyo. Oku kwenzeka kakhulu emilenzeni, kodwa kunokuchaphazela iingalo, ubuso, intloko, okanye amalungu angaphakathi.

Iindlela ezahlukeneyo zokucinga zinokusetyenziselwa ukufumana naluphi na utshintsho kulwakhiwo lomzimba ngenxa yale meko. Oku kunceda ekuthathweni kwesicwangciso sonyango. Oku kunokubandakanya:

• I-MRA
• Unyango lwe-Endoscopic thermal ablation
• X-reyi
• Ukuskena i-CT okanye i-CT venography
• IMRI
• Umbala weduplex ultrasonography

I-Ultrasound ngexesha lokukhulelwa inokunceda ekuchongeni imeko.

Le mibutho ilandelayo ibonelela ngolwazi oluthe kratya kwi-KTS:

• Iqela leNkxaso yeSifo seKlippel-Trenaunay - k-t.org
• Isiseko seVascular Birthmark Foundation- www.birthmark.org

Uninzi lwabantu abane-KTS benza kakuhle, nangona imeko inokuchaphazela ukubonakala kwabo. Abanye abantu baneengxaki zengqondo ezivela kwimeko.

Ngamanye amaxesha kunokubakho imithambo yegazi engaqhelekanga esiswini, enokufuna ukuvavanywa.

Isifo seKlippel-Trenaunay-Weber; KTS; Angio-osteohypertrophy; Hemangiectasia hypertrophicans; Nevus verucosus hypertrophicans; I-capillary-lymphatico-venous malformation (CLVM)

UGreene AK, uMulliken JB. Ukungafani kwemithambo. Ku: URodriguez ED, uLosee JE, uNeligan PC, ii-eds. Utyando lweplastiki: Umqulu 3: Utyando lwe-Craniofacial, iNtloko kunye neNtamo kunye noPhando lwePlastiki lwabantwana. Ngomhla we-4. IPhiladelphia, PA: Elsevier; I-2018: isahluko 39.

Iqela leNkxaso yeKT iwebhusayithi. Izikhokelo zokuziqhelanisa neklinikhi zeKlippel-Trenaunaysyndrome (KTS). k-t.org/assets/images/content/BCH-Klippel-Trenaunay-Syndrome-Ulawulo- lweZikhokelo-1-6-2016.pdf. Ukuhlaziywa ngoJanuwari 6, 2016. Ifikeleleke ngoNovemba 5, 2019.

Longman RE. Isifo seKlippel-Trenaunay-Weber. Ku: ICopel JA, D'Alton ME, uFeltovich H, et al, ii-eds. UkuThintela ukuThintela. Ngomhla wesi-2. IPhiladelphia, PA: Elsevier; I-2018: isahluko 131.

UMcCormick AA, uGrundwaldt LJ. Ukungafani kwemithambo. Ku: Zitelli BJ, McIntire SC, Nowalk AJ, ii-eds. UZitelli no-Davis ’Atlas of Pediatric Physical Diagnosis. Umhla wesi-7. IPhiladelphia, PA: Elsevier; I-2018: isahluko 10.