Ukukhubazeka kwamaxesha ngamaxesha

I-Hypokalemic periodic paralysis (hypoPP) sisifo esibangela amaxesha athile obuthathaka bemisipha kwaye ngamanye amaxesha asezantsi kwinqanaba eliqhelekileyo le potassium egazini. Igama lonyango kwinqanaba eliphantsi le-potassium yi-hypokalemia.

I-HypoPP yenye yeqela lokuphazamiseka kwemfuza okubandakanya ukukhubazeka kwamaxesha ngamaxesha kunye ne-thyrotoxic periodic paralysis.

I-HypoPP yeyona ndlela ixhaphakileyo yokukhubazeka kwamaxesha. Ichaphazela amadoda rhoqo.

IHypPP izalwe ngokuzalwa. Oku kuthetha ukuba ikhona ekuzalweni. Kwiimeko ezininzi, idluliswa kwiintsapho (ezizuzwe njengelifa) njengesifo esinegunya lokulawula isifo. Ngamanye amagama, ngumzali omnye kuphela ekufuneka eyidlulisile imfuza enxulumene nale meko emntwaneni wakhe ukuze umntwana achaphazeleke.

Ngamanye amaxesha, imeko inokuba sisiphumo sengxaki yemfuza engafumanwanga njengelifa.

Ngokungafaniyo nezinye iindlela zokukhubazeka ngamaxesha athile, abantu abane-hypoPP banomsebenzi oqhelekileyo we-thyroid. Kodwa banenqanaba eliphantsi kakhulu legazi le potassium ngexesha leziganeko zobuthathaka. Oku kubangelwa kukuhamba kwe potassium egazini ukuya kwiiseli zemisipha ngendlela engaqhelekanga.

Imiba yomngcipheko ibandakanya ukuba namanye amalungu osapho anokukhubazeka ngamaxesha athile. Umngcipheko uphakame kancinci kumadoda aseAsia nawo aneengxaki ze-thyroid.

Iimpawu zibandakanya ukuhlaselwa kobuthathaka bemisipha okanye ukulahleka kokuhamba kwemisipha (ukukhubazeka) okuza kuhamba. Kukho amandla esihlunu aqhelekileyo phakathi kohlaselo.

Uhlaselo luhlala luqala kwiminyaka yeshumi elivisayo, kodwa lunokwenzeka ngaphambi kweminyaka eyi-10. Abanye abantu bahlaselwa mihla le. Abanye banazo kanye ngonyaka. Ngexesha lokuhlaselwa umntu uhlala ethe qwa.

Ubuthathaka okanye ukukhubazeka:

• Eyona nto ixhaphakileyo ivela emagxeni nasezinqeni
• Inokuthi ichaphazele iingalo, imilenze, izihlunu zamehlo, kunye nezihlunu ezinceda ngokuphefumla nokuginya
• Iqhubeka kwaye iqhubeke
• Ngokuqhelekileyo kwenzeka ekuvukeni okanye emva kokulala okanye ukuphumla
• Inqabile ngexesha lokuzilolonga, kodwa inokubangelwa kukuphumla emva kokuzilolonga
• Ingabangelwa kukutya okuneswekile eninzi, ukutya okunetyuwa eninzi, uxinzelelo, ukukhulelwa, umthambo onzima kunye nokubanda
• Uhlaselo luhlala luhlala iiyure ezininzi ukuya kuthi ga kwimini

Olunye uphawu lunokubandakanya ijwabu le-myotonia (imeko apho emva kokuvula nokuvala amehlo, azinakuvulwa ixesha elifutshane).

Umboneleli wezempilo unokukrokrela i-hypoPP esekwe kwimbali yosapho yokuphazamiseka. Eminye imikhondo yokuphazamiseka zizimpawu zobuthathaka bemisipha eza kunye neziphumo eziqhelekileyo okanye eziphantsi zovavanyo lwe potassium.

Phakathi kokuhlaselwa, uvavanyo lomzimba alubonisi nto ingaqhelekanga. Phambi kohlaselo, kunokubakho ukuqina kwemilenze okanye ubunzima emilenzeni.

Ngexesha lokuhlaselwa kobuthathaka bemisipha, inqanaba le-potassium yegazi liphantsi. Oku kuqinisekisa ukuxilongwa. Akukho kuncipha kwi-potassium yomzimba iyonke. Inqanaba le-potassium yegazi liqhelekileyo phakathi kokuhlaselwa.

Ngethuba lokuhlaselwa, i-reflexes ye-muscle iyancipha okanye ayikho. Kwaye izihlunu ziyaqhwalela kunokuhlala ziqinile. Amaqela emisipha akufuphi nomzimba, njengamagxa kunye nesinqe, ayabandakanyeka rhoqo kuneengalo nemilenze.

Uvavanyo olunokwenziwa lunokubandakanya:

• I-Electrocardiogram (ECG), enokuthi ibe yinto engaqhelekanga ngexesha lokuhlaselwa
• I-Electromyography (EMG), eqhelekileyo ngesiqhelo phakathi kohlaselo kunye nokungaqhelekanga ngexesha lokuhlaselwa
• I-biopsy yemisipha, enokubonisa ukungaqheleki

Olunye uvavanyo lunokuyalelwa ukuba lukhuphe ezinye izizathu.

Iinjongo zonyango kukukhululeka kweempawu kunye nokuthintela uhlaselo oluthe kratya.

Ubuthathaka bemisipha obubandakanya ukuphefumla okanye ukugwinya kwezihlunu yimeko engxamisekileyo. Ukubetha kwentliziyo okungaqhelekanga (i-arrhythmias yentliziyo) nako kunokwenzeka ngexesha lokuhlaselwa. Nayiphi na kwezi kufuneka inyangwe kwangoko.

I-Potassium enikwe ngexesha lokuhlaselwa inokumisa uhlaselo. I-Potassium ingathathwa ngomlomo. Kodwa ukuba ubuthathaka bunzima, i-potassium inokufuna ukunikezelwa nge-vein (IV).

Ukuthatha izongezo zepotassium kunganceda ukuthintela ubuthathaka bemisipha.

Ukutya ukutya okune-carbohydrate encinci kunokunceda ukunciphisa iimpawu.

Iyeza elibizwa ngokuba yi-acetazolamide linokumiselwa ukuthintela uhlaselo. Umboneleli wakho unokukuxelela ukuba uthathe izongezo zepotassium ngenxa yokuba iacetazolamide inokubangela ukuba umzimba wakho ulahlekelwe yipotassium.

Ukuba i-acetazolamide ayisebenzi kuwe, amanye amayeza anokumiselwa.

I-HypoPP iphendula kakuhle kunyango. Unyango lunokuthintela, kwaye lude luye umva, buthathaka buthathaka kwimisipha. Nangona amandla emisipha eqala ngesiqhelo phakathi kohlaselo, uhlaselo oluphindaphindiweyo lunokuthi ekugqibeleni lubangele ukomelela kunye nobuthathaka besihlunu esisigxina phakathi kohlaselo.

Iingxaki zempilo ezinokubangelwa yile meko zibandakanya:

• Izintso zamatye (umphumo wecala le-acetazolamide)
• Ukubetha kwentliziyo ngokungaqhelekanga ngexesha lokuhlaselwa
• Kunzima ukuphefumla, ukuthetha, okanye ukuginya ngexesha lokuhlaselwa (kunqabile)
• Ubuthathaka bemisipha obuba mandundu ngokuhamba kwexesha

Shayela umnikezeli wakho ukuba wena okanye umntwana wakho unobuthakathaka obuthakathaka obuza kwaye buhamba, ngakumbi ukuba unamalungu entsapho anokukhubazeka ngamaxesha athile.

Yiya kwigumbi likaxakeka okanye fowunela inombolo yongxamiseko yendawo (enje nge-911) ukuba wena okanye umntwana wakho uphelelwa ngamandla, unengxaki yokuphefumla, ukuthetha, okanye ukuginya.

IHypPP ayikwazi kuthintelwa. Kuba inokuba lilifa, iingcebiso ngemfuzo zinokucetyiswa kwizibini ezisemngciphekweni wokuphazamiseka.

Unyango luthintela ukuhlaselwa kobuthathaka. Phambi kohlaselo, kunokubakho ukuqina kwemilenze okanye ubunzima emilenzeni. Ukwenza umthambo omncane xa ezi mpawu ziqala kunokunceda ukunqanda uhlaselo olupheleleyo.

Ukukhubazeka kwamaxesha - i-hypokalemic; Usapho oluqhelekileyo lokukhubazeka ngamathuba athile; HOKPP; HypoKPP; HypoPP

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