Umbhali: Virginia Floyd
Umhla Wokudalwa: 8 Eyethupha 2021
Hlaziya Umhla: 22 Isilimela 2024
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Ukunganyamezelani kwe-fructose - Iyeza
Ukunganyamezelani kwe-fructose - Iyeza

Ukunganyamezelani ngenxa ye-fructose sisifo apho umntu engenayo iprotein efunekayo yokuphula i-fructose. IFructose sishukela esisiqhamo esivela ngokwendalo emzimbeni. I-fructose eyenziwe ngumntu isetyenziswa njengeswiti kukutya okuninzi, kubandakanya ukutya kosana kunye neziselo.

Le meko yenzeka xa umzimba ulahlekile i-enzyme ebizwa ngokuba yi-aldolase B. Le nto iyafuneka ukwaphula i-fructose.

Ukuba umntu ongenayo le nto utya i-fructose okanye i-sucrose (i-cane okanye i-beet iswekile, iswekile yetafile), utshintsho olunzima lweekhemikhali lwenzeka emzimbeni. Umzimba awukwazi ukutshintsha uhlobo olugciniweyo lweswekile (glycogen) kwi-glucose. Ngenxa yoko, iswekile yegazi iyawa kwaye izinto ezinobungozi ziyakha esibindini.

Ukunganyamezelani kwe-fructose efunyanwa kwilifa, okuthetha ukuba inokudluliselwa kwiintsapho. Ukuba bobabini abazali baphethe ikopi engasebenziyo yohlobo lwe-aldolase B, umntwana ngamnye kubo une-25% (1 in 4) ithuba lokuchaphazeleka.

Iimpawu zinokubonwa emva kokuba umntwana eqale ukutya ukutya okanye ifomula.


Iimpawu zokuqala zokunganyamezelani kwe-fructose ziyafana nezo ze-galactosemia (ukungakwazi ukusebenzisa iswekile galactose). Iimpawu zexesha elizayo zihambelana ngakumbi nesifo sesibindi.

Iimpawu zingabandakanya:

  • Ukuxhuzula
  • Ukulala kakhulu
  • Ukucaphuka
  • Isikhumba esimthubi okanye abamhlophe bamehlo (i-jaundice)
  • Ukutya okungalunganga kunye nokukhula njengomntwana, ukusilela ukukhula
  • Iingxaki emva kokutya iziqhamo kunye nokunye ukutya okuqukethe i-fructose okanye i-sucrose
  • Ukuhlanza

Uviwo lomzimba lunokubonisa:

  • Ukwandiswa kwesibindi kunye ne-spleen
  • I-jaundice

Uvavanyo oluqinisekisa ukuxilongwa lubandakanya:

  • Uvavanyo lokunqanda igazi
  • Uvavanyo lweswekile yegazi
  • Izifundo ze-enzyme
  • Uvavanyo lwemfuzo
  • Uvavanyo lwezintso
  • Uvavanyo lomsebenzi wesibindi
  • Isibindi se-biopsy
  • Uric acid uvavanyo lwegazi
  • Uhlalutyo lomchamo

Iswekile yegazi iya kuba sezantsi, ngakumbi emva kokufumana i-fructose okanye i-sucrose. Amanqanaba eUric acid aya kuba phezulu.

Ukususa i-fructose kunye ne-sucrose kukutya kunyango olusebenzayo kubantu abaninzi. Iingxaki zinokunyangwa. Umzekelo, abanye abantu banokuthatha iyeza ukuthoba inqanaba le-uric acid egazini labo kunye nokunciphisa umngcipheko wegawuthi.


Ukunganyamezelani kwe-fructose enokuba lilifa kunokuba nobulali okanye buqatha.

Ukuphepha i-fructose kunye ne-sucrose kunceda uninzi lwabantwana abakule meko. Ukuxela kwangaphambili kulungile kwiimeko ezininzi.

Abantwana abambalwa abanesifo esiqatha baya kuphuhlisa isifo sesibindi. Nokuba ususa i-fructose kunye ne-sucrose ekudleni ayinakuthintela isifo sesibindi esibi kwaba bantwana.

Ukusebenza kakuhle komntu kuxhomekeke:

  • Kungekudala uxilongo lwenziwa
  • Kungekudala i-fructose kunye ne-sucrose ingasuswa njani kukutya
  • Isebenza kakuhle njani i-enzyme emzimbeni

Ezi ngxaki zinokwenzeka:

  • Ukuthintela ukutya okuqulathe i-fructose ngenxa yeziphumo zazo
  • Ukopha
  • Igawuthi
  • Ukugula kukutya ukutya okune-fructose okanye i-sucrose
  • Ukungaphumeleli kwesibindi
  • Iswekile esezantsi yegazi (hypoglycemia)
  • Ukuxhuzula
  • Ukufa

Fowunela umboneleli wakho wokhathalelo lwempilo ukuba umntwana wakho uvela kwiimpawu zale meko emva kokutya. Ukuba umntwana wakho unale meko, iingcali zicebisa ukuba ubonane nogqirha ogxile kwimfuza okanye kwimetabolism.


Amaqabane anembali yosapho yokunganyamezelani kwe-fructose onqwenela ukuba nosana angajonga ingcebiso ngemfuzo.

Uninzi lweziphumo zesifo ezinokuthintelwa ngokunciphisa i-fructose kunye ne-sucrose intake.

Fructosemia; Ukunganyamezelani kweFructose; Ukusilela kwe-Fructose aldolase B; Ukusilela kwe-Fructose-1, 6-bisphosphate aldolase

IBonnardeaux A, iBichet DG. Ukuphazamiseka okuzelwe njengelifa kwisifo sezintso. Ku: Skorecki K, Chertow GM, Marsden PA, Taal MW, Yu ASL, ii-eds. Brenner kunye noMphathi weZintso. Ngomhla we-10. IPhiladelphia, PA: Elsevier; 2016: isahluko 45.

IKishnani PS, u-Chen YT. Iziphene kwimetabolism ye-carbohydrate. Ku: Kliegman RM, St Geme JW, Schor NF, Blum NJ, Shah SS, Tasker RC, Wilson KM, ii-eds. Incwadi kaNelson yeNcwadi yePediatrics. Umhla wama-21. IPhiladelphia, PA: Elsevier; 2020: isahl. 105.

UNadkarni P, Weinstock RS. IiCarbohydrate. Ku: McPherson RA, Pincus MR, ii-eds. Ukuchongwa kweKlinikhi kaHenry kunye noLawulo ngeendlela zeLebhu. Umhla we-23. ISt Louis, MO: Elsevier; I-2017: isahluko 16.

Scheinman SJ. Ukuphazamiseka kwezithuthi kwizintso. Ku: Gilbert SJ, Weiner DE, ii-eds. Isiseko seZintso seSizwe seZintso. Umhla wesi-7. IPhiladelphia, PA: Elsevier; I-2018: isahluko 38.

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