Umbhali: Clyde Lopez
Umhla Wokudalwa: 21 Eyekhala 2021
Hlaziya Umhla: 1 Eyekhala 2024
Anonim
Retroperitoneal fibrosis
Ividiyo: Retroperitoneal fibrosis

I-Retroperitoneal fibrosis sisifo esinqabileyo esivimba iityhubhu (ureters) ezihambisa umchamo kwizintso ukuya kwisinyi.

I-Retroperitoneal fibrosis yenzeka xa iifom zezicubu ezongeziweyo kwindawo engasemva kwesisu kunye namathumbu. Izicubu zenza ubunzima (okanye ubunzima) okanye izicwili ezinzima. Ingavala iityhubhu ezihambisa umchamo kwizintso ukuya kwisinyi.

Unobangela wale ngxaki akaziwa. Ixhaphake kakhulu kubantu abaneminyaka engama-40 ukuya kwengama-60. Amadoda anokuphinda-phinda amathuba okuba imeko ibe njengabafazi.

Iimpawu zokuqala:

  • Intlungu ebuthathaka esiswini eyonyuka ngokuhamba kwexesha
  • Ubuhlungu kunye notshintsho lombala emilenzeni (ngenxa yokuhla kwegazi)
  • Ukudumba komlenze omnye

Iimpawu kamva:

  • Ukuncipha kwemveliso yomchamo
  • Akukho mveliso yomchamo (anuria)
  • Isicaphucaphu, ukugabha, utshintsho kubume bengqondo obubangelwa kukusilela kwezintso nokwakhiwa kweekhemikhali eziyityhefu egazini
  • Ubuhlungu obukhulu besisu kunye negazi kwi-stool (ngenxa yokufa kwezicubu zamathumbu)

Isisombululo se-CT esiswini yeyona ndlela ifanelekileyo yokufumana ubunzima be-retroperitoneal.


Olunye uvavanyo olunokunceda ukufumanisa le meko lubandakanya:

  • I-BUN kunye ne-creatinine yovavanyo lwegazi
  • Intravenous pyelogram (IVP), hayi njengesiqhelo
  • Isifo sezintso
  • I-MRI yesisu
  • Ukuskena i-CAT esiswini kunye ne-retroperitoneum

I-biopsy yobunzima inokwenziwa kwakhona ukukhupha umhlaza.

Iicorticosteroids zizanywa kuqala. Abanye ababoneleli ngezempilo bamisela iyeza elibizwa ngokuba yi-tamoxifen.

Ukuba unyango lwe-corticosteroid alusebenzi, kufuneka kwenziwe i-biopsy ukuqinisekisa isifo. Amanye amayeza okucinezela amajoni omzimba anokumiselwa.

Xa iyeza lingasebenzi, kufuneka kwenziwe utyando kunye namafutha (ukukhupha iityhubhu).

Imbonakalo iya kuxhomekeka kubungakanani bengxaki kunye nenani lomonakalo kwizintso.

Umonakalo wezintso unokuba wethutyana okanye isigxina.

Ukuphazamiseka kunokukhokelela ku:

  • Ukuvaleka okuqhubekayo kwemibhobho ekhokelela kwizintso kwelinye okanye macala omabini
  • Ukusilela kwezintso okungapheliyo

Fowunela umnikezeli wakho ukuba unesisu esisezantsi okanye iintlungu zeplanti kunye nemveliso encinci yomchamo.


Zama ukunqanda ukusetyenziswa kwexesha elide kwamayeza ane-methysergide. Eli chiza libonakalisiwe ukuba libangela i-retroperitoneal fibrosis. Ngamanye amaxesha iMethysergide isetyenziselwa ukunyanga iintloko zentloko.

Idiopathic retroperitoneal fibrosis; Isifo sika-Ormond

  • Inkqubo yomchamo wamadoda

Ukuthelekisa i-E, i-Bonsib SM, i-Cheng L.I-renal pelvis kunye ne-ureter. Ku: Cheng L, MacLennan GT, Bostwick DG, ii-eds. I-Urology yokuNyanga iPathology. Ngomhla we-4. IPhiladelphia, PA: Elsevier; 2020: isahluko 3.

I-Nakada SY, eyona SL. Ulawulo lokuphazamiseka kwendlela ephezulu yomchamo. Ku: Wein AJ, Kavoussi LR, Partin AW, Peters, CA, ii-eds. UCampbell-Walsh Urology. Ngomhla we-11. IPhiladelphia, PA: Elsevier; 2016: isahluko 49.

O'Connor OJ, Maher MM. Iphecana lokuchama: ukujonga ngokubanzi i-anatomy, ubuchwephesha kunye nemicimbi yemitha. Ku: UAdam A, uDixon AK, uGillard JH, uSchaefer-Prokop CM, ii-eds. I-Grainger kunye ne-Allison's Diagnostic Radiology: Incwadi ebhaliweyo yoNyango lwezoNyango. Umhla wesi-6. IPhiladelphia, PA: Elsevier Churchill Livingstone; 2015: isahluko 35.


IShanmugam VK. I-Vasculitis kunye nezinye ii-arteriopathies ezingaqhelekanga. Ku: Sidawy AN, Perler BA, ii-eds. Utshintsho lukaRutherford lweeVascular and Therapy ze-Endovascular Therapy. Umhla we-9. IPhiladelphia, PA: Elsevier; I-2019: isahluko 137.

Ukujika kweRH, uMizell J, uBadgwell B.Udonga lwesisu, umbilicus, i-peritoneum, i-mesenteries, i-omentum kunye ne-retroperitoneum. Ku: Townsend CM Jr, Beauchamp RD, Evers BM, Mattox KL, ii-eds. Incwadi yeSabiston yoNyango. Umhla we-20. IPhiladelphia, PA: Elsevier Saunders; Ngo-2017: isahluko 43.

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