I-ovalocytosis yelifa

I-ovalocytosis yelifa yimeko enqabileyo edluliselwe kwiintsapho (ezizuzwe njengelifa). Iiseli zegazi zimile okweqanda okweqanda. Luhlobo lwe-elliptocytosis yelifa.
I-Ovalocytosis ifumaneka ikakhulu kubemi base mpuma mpuma Asia.
Iintsana ezisandul 'ukuzalwa ezine-ovalocytosis zinokuba ne-anemia kunye ne-jaundice. Abantu abadala bahlala bengabonisi zimpawu.
Uvavanyo ngumboneleli wakho wezempilo lunokubonisa udakada owandisiweyo.
Le meko ifunyaniswa ngokujonga imilo yeeseli zegazi phantsi kwemicroscope. Ezi mvavanyo zilandelayo zinokwenziwa:
- Gcwalisa inani legazi (CBC) ukujonga i-anemia okanye ukutshatyalaliswa kweseli ebomvu
- I-smear yegazi ukumisela ubume beseli
- Inqanaba leBilirubin (inokuba phezulu)
- Inqanaba le-Lactate dehydrogenase (inokuba phezulu)
- I-Ultrasound yesisu (isenokubonisa iinyongo)
Kwiimeko eziqatha, esi sifo sinokunyangwa ngokususa udakada (splenectomy).
Imeko inokunxulunyaniswa nenyongo okanye iingxaki zezintso.
Ovalocytosis - ilifa
Iiseli zegazi
IGallagher PG. I-hemolytic anemias: inwebu ebomvu yegazi kunye neziphene kwimetabolism. Ku: IGoldman L, iSchafer AI, ii-eds. Amayeza eGoldman-Cecil. Ngomhla wama-26. IPhiladelphia, PA: Elsevier; 2020: isahl. 152.
IGallagher PG. Ukuphazamiseka kwembala yeseli ebomvu. Ku: Hoffman R, Benz EJ, Silberstein LE, et al, ii-eds. I-Hematology: Imigaqo esisiseko kunye nokuziqhelanisa. Umhla wesi-7. IPhiladelphia, PA: Elsevier; I-2018: isahluko 45.
I-Merguerian MD, iGallagher PG. I-elliptocytosis yelifa, ifa le-pyropoikilocytosis, kunye nokuphazamiseka okunxulumene noko. Ku: Kliegman RM, St Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, ii-eds. Incwadi kaNelson yeNcwadi yePediatrics. Umhla wama-21. IPhiladelphia, PA: Elsevier; 2020: isahluko 486.