Isifo seAortic arch syndrome
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I-aortic arch yeyona ndawo iphambili yomthambo ophambili ophethe igazi kude nentliziyo. Isifo iAortic arch syndrome sibhekisa kwiqela leempawu kunye neempawu ezinxulunyaniswa neengxaki zokwakha kwimithambo yegazi ekhupha iarortic arch.
Iingxaki zesifo se-aortic arch zinokubangelwa kukuqaqanjelwa ngumzimba, amahlwili egazi, okanye ukungalunganga okukhulayo ngaphambi kokuzalwa. Ezi ziphene zibangela ukuhamba kwegazi okungaqhelekanga entloko, entanyeni, okanye kwiingalo.
Kubantwana, zininzi iintlobo ze-aortic arch syndromes, kubandakanya:
- Ukungabikho kokuzalwa kwesebe le-aorta
- Ukubekwa ecaleni kwemithambo ye-subclavia
- Amakhonkco nemithambo
Isifo esivuthayo esibizwa ngokuba yi-Takayasu syndrome sinokubangela ukunciphisa (stenosis) yeenqanawa ze-aortic arch. Oku kwenzeka kakhulu kubafazi nakumantombazana. Esi sifo sibonakala rhoqo kubantu abanemvelaphi yaseAsia.
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Iimpawu ziyahluka ngokokutsho komthambo okanye olunye ulwakhiwo oluchaphazelekayo. Iimpawu zingabandakanya:
- Uxinzelelo lwegazi luyatshintsha
- Iingxaki zokuphefumla
- Ukuba nesiyezi, ukungaboni kakuhle, ubuthathaka, kunye nolunye uhlobo lwengqondo kunye neenkqubo zemithambo-luvo
- Ubungqongqo bengalo
- Ukunciphisa ukubetha
- Ukuginya iingxaki
- Ukuhlaselwa kweschemic okwethutyana (TIA)
Ugqirha luyafuneka rhoqo ukunyanga oyena nobangela wesifo se-aortic arch.
Umthambo we-Subclavian syndrome; Isifo seCarotid artery occlusion syndrome; I-Subclavian iba nesifo; I-Vertebral-basilar artery occlusive syndrome; Isifo seTayasu; Isifo esingaqhuliyo
Icandelo lentliziyo phakathi embindini
Isangqa semithambo
IBraverman AC, iShermerhorn M. Izifo ze-aorta. Ku: Zipes DP, Libby P, Bonow RO, Mann DL, Tomaselli GF, Braunwald E, ii-eds. Isifo sentliziyo seBraunwald: Incwadi yesifundo seMpilo yeNtliziyo. Ngomhla we-11. IPhiladelphia, PA: Elsevier; I-2019: isahluko 63.
UJames WD, u-Elston DM, nyanga i-JR, i-Rosenbach MA, i-IM ye-Neuhaus. Izifo zemithambo yegazi. Ku: James WD, Elston DM, Phatha uJR, Rosenbach MA, Neuhaus IM, ii-eds. Izifo zikaAndrews zolusu: Unyango lweKlinikhi. Umhla we-13. IPhiladelphia, PA: Elsevier; 2020: isahluko 35.
ILangford CA. Takayasu arteritis. Ku: Hochberg MC, Gravallese EM, Silman AJ, Smolen JS, Weinblatt ME, Weisman MH, ii-eds. Rheumatology. Umhla wesi-7. IPhiladelphia, PA: Elsevier; I-2019: isahluko 165.