Umbhali: Clyde Lopez
Umhla Wokudalwa: 23 Eyekhala 2021
Hlaziya Umhla: 1 Eyekhala 2025
Anonim
Spinocerebellar ataxia - causes, symptoms, diagnosis, treatment, pathology
Ividiyo: Spinocerebellar ataxia - causes, symptoms, diagnosis, treatment, pathology

I-acute ye-cerebellar ataxia ngequbuliso, intshukumo yemisipha engalungelelananga ngenxa yesifo okanye ukwenzakala kwi-cerebellum. Le yindawo kwingqondo elawula ukuhamba kwemisipha. I-Ataxia kuthetha ukuphulukana nolungelelwaniso lwezihlunu, ngakumbi izandla nemilenze.

I-acerebellar ataxia ebukekayo ebantwaneni, ngakumbi abangaphantsi kweminyaka emi-3, inokwenzeka kwiintsuku okanye kwiiveki ezimbalwa emva kokugula okubangelwa yintsholongwane.

Usulelo lwentsholongwane olunokubangela oku kubandakanya inkukhu, isifo seCoxsackie, i-Epstein-Barr, i-echovirus, phakathi kwabanye.

Ezinye izizathu ze-ataxia ebukhali ye-cerebellar zibandakanya:

  • Ithumba le-cerebellum
  • Utywala, amayeza, kunye nokubulala izinambuzane, kunye neziyobisi ezingekho mthethweni
  • Ukopha kwi-cerebellum
  • Isifo sokugubhuka
  • Ukubetha kwe-cerebellum
  • Ugonyo
  • Umothuko entloko nasentanyeni
  • Izifo ezithile ezinxulunyaniswa nomhlaza othile (ukuphazamiseka kweparoplastic)

I-Ataxia inokuchaphazela ukuhamba kwenxalenye ephakathi yomzimba ukusuka entanyeni ukuya kwindawo yehip (trunk) okanye iingalo nemilenze (imilenze).


Xa umntu ehleli, umzimba unokuhamba-ngecala, ukubuyela-ngaphambili, okanye zombini. Emva koko umzimba ubuyela ngokukhawuleza kwindawo efanelekileyo.

Xa umntu one-ataxia yeengalo efikelela kwinto, isandla sinokujikeleza sibuye sijikeleze.

Iimpawu eziqhelekileyo ze-ataxia zibandakanya:

  • Iphethini yentetho emnandi (idysarthria)
  • Ukuhamba okuphindaphindiweyo kwamehlo (nystagmus)
  • Ukungahambelani kwamehlo
  • Iingxaki zokuhamba (ukungazinzi) ezinokukhokelela ekuweni

Umboneleli wokhathalelo lwempilo uya kubuza ukuba ngaba lo mntu usandula ukugula kwaye uyakuzama ukukhupha naziphi na ezinye izizathu zengxaki. Ubuchopho kunye novavanyo lwenkqubo yemithambo-luvo luyakwenziwa ukuze kuchongwe imimandla yenkqubo yeemvakalelo echaphazeleka kakhulu.

Ezi mvavanyo zilandelayo zinoku-odolwa:

  • Ukuvavanywa kwentloko kwe-CT
  • Ukuvavanywa kwentloko ye-MRI
  • Impompo yomqolo
  • Uvavanyo lwegazi ukufumanisa usulelo olubangelwa yintsholongwane okanye ibhaktiriya

Unyango luxhomekeke kwisizathu:

  • Ukuba i-ataxia ebukhali ye-cerebellar ngenxa yokopha, kunokufuneka kwenziwe utyando.
  • Ukubetha, kunokunikwa iyeza lokunciphisa igazi.
  • Usulelo lunokufuna ukunyangwa ngamayeza okubulala iintsholongwane okanye ii-antivirals.
  • I-Corticosteroids inokufuneka ukuze idumbe (ukudumba) kwe-cerebellum (enjenge-multiple sclerosis).
  • I-ataxia ye-Cerebellar ebangelwe lusulelo lwentsholongwane lwamva nje isenokungafuneki unyango.

Abantu imeko yabo ibangelwe lusulelo lwentsholongwane lwamva nje kufuneka bachache ngokupheleleyo ngaphandle konyango kwiinyanga ezimbalwa. Ukubetha, ukuphuma kwegazi, okanye usulelo kunokubangela iimpawu ezingapheliyo.


Kwiimeko ezinqabileyo, intshukumo okanye ukuphazamiseka kokuziphatha kunokuqhubeka.

Tsalela umnxeba umboneleli wakho ukuba ngaba zikhona iimpawu ze-ataxia.

ICerebellar ataxia; Ataxia - cerebellar etsolo; Intsholongwane; I-post-varicella acute cerebellar ataxia; IPVACA

IMink JW. Ukuphazamiseka kwentshukumo. Ku: Kliegman RM, Stanton BF, St Geme JW, Schor NF, ii-eds. Incwadi kaNelson yeNcwadi yePediatrics. Umhla we-20. IPhiladelphia, PA: Elsevier; Ngo-2016: isahluko 597.

I-Subramony SH, i-Xia G. Ukuphazamiseka kwe-cerebellum, kubandakanya ne-ataxias eguqukayo. Ku: Daroff RB, Jankovic J, Mazziotta JC, Pomeroy SL, ii-eds. I-Neurology kaBradley kwiKlinikhi yokuziqhelanisa. Umhla wesi-7. IPhiladelphia, PA: Elsevier; Ngo-2016: isahluko 97.

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