Umbhali: Joan Hall
Umhla Wokudalwa: 26 Eyomdumba 2021
Hlaziya Umhla: 1 Eyekhala 2024
Anonim
Isifo seGianotti-Crosti - Iyeza
Isifo seGianotti-Crosti - Iyeza

Isifo i-Gianotti-Crosti syndrome yimeko yesikhumba yabantwana enokuthi ihambisane neempawu ezinobushushu zomkhuhlane kunye nokuqaqamba komzimba. Inokudibaniswa ne-hepatitis B kunye nezinye izifo zentsholongwane.

Ababoneleli ngononophelo lwempilo abayazi eyona nto ibangela esi sifo. Bayazi ukuba inxulunyaniswa nolunye usulelo.

Kubantwana base-Italiya, i-Gianotti-Crosti syndrome ibonwa rhoqo nge-hepatitis B. Kodwa eli khonkco alifane libonwe e-United States. Intsholongwane ka-Epstein-Barr (i-EBV, i-mononucleosis) yintsholongwane ehlala inxulunyaniswa ne-acrodermatitis.

Ezinye iintsholongwane ezinxulumene nazo zibandakanya:

  • Cytomegalovirus
  • Iintsholongwane zeCoxsackie
  • Intsholongwane yeParainfluenza
  • Intsholongwane yokuphefumla intsholongwane (RSV)
  • Ezinye iintlobo zokugonya iintsholongwane eziphilayo

Iimpawu zolusu zingabandakanya nayiphi na kwezi zilandelayo:

  • I-Rash okanye i-patch elukhumbeni, ngokuqhelekileyo kwiingalo nasemilenzeni
  • Umbala o-brownish-obomvu okanye umbala wobhedu oqinileyo kwaye ucabalele ngaphezulu
  • Umtya wamaqhuma ungavela kumgca
  • Ngokubanzi ayirhawuzeli
  • Irash ijongeka ngokufanayo kumacala omabini omzimba
  • Irhash inokubonakala ezintendeni nasezintendeni, kodwa hayi ngasemva, esifubeni, okanye kwindawo yesisu (yenye yeendlela ezichongiweyo, ngokungabikho komqubu esiqwini somzimba)

Ezinye iimpawu ezinokubonakala zibandakanya:


  • Isisu esidumbileyo
  • I-lymph nodes ezidumbileyo
  • Iimpawu zeethenda zeethenda

Umboneleli unokuyiqonda le meko ngokujonga ulusu kunye nerhashalala. Isibindi, udakada, kunye ne-lymph node zinokudumba.

Olu vavanyo lulandelayo lunokwenziwa ukuqinisekisa ukuxilongwa okanye ukukhutshwa kwezinye iimeko:

  • Inqanaba leBilirubin
  • I-hepatitis virus serology okanye i-hepatitis B kumphezulu we-antigen
  • Ii-enzyme zesibindi (iimvavanyo zomsebenzi wesibindi)
  • Ukuvavanywa kwee-antibodies ze-EBV
  • Ulusu lwe-biopsy

Ingxaki yona ayinyangwa. Izifo ezinxulumene nale meko, ezinje nge-hepatitis B kunye no-Epstein-Barr, ziyanyangwa. Iicortisone creams kunye ne-antihistamines yomlomo zinokunceda ukurhawuzelela kunye nokucaphuka.

Irhashalala linyamalala lodwa malunga neeveki ezi-3 ukuya kwezi-8 ngaphandle konyango okanye ingxaki. Iimeko ezihambelanayo kufuneka zijongwe ngononophelo.

Iingxaki zenzeka ngenxa yeemeko ezinxulumene noko, kunokuba zibekho ngokungxamiseka.

Fowunela umboneleli wakho ukuba umntwana wakho uneempawu zale meko.


I-papular acrodermatitis yobuntwana; Usana lwe-acrodermatitis; IAcrodermatitis - lichenoid yabantwana; IAcrodermatitis - usana lwepapile; Isifo se-acro-akro syndrome

  • Isifo seGianotti-Crosti emlenzeni
  • I-mononucleosis echaphazelekayo

IBender NR, Chiu YE. Ukuphazamiseka kwe-eczematous. Ku: Kliegman RM, St Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, ii-eds. Incwadi kaNelson yeNcwadi yePediatrics. Umhla wama-21. IPhiladelphia, PA: Elsevier; 2020: isahluko 674.

Isifo seGelmetti C. Gianotti-Crosti Ku: Lebwohl MG, Heymann WR, Berth-Jones J, Coulson IH, ii-eds. Unyango lwezifo zolusu: Amacandelo oBuchule oNyango. Umhla we-5. IPhiladelphia, PA: Elsevier; I-2018: isahluko 91.

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