Umbhali: Clyde Lopez
Umhla Wokudalwa: 23 Eyekhala 2021
Hlaziya Umhla: 1 Eyomdumba 2025
Anonim
Uvavanyo lweDonath-Landsteiner - Iyeza
Uvavanyo lweDonath-Landsteiner - Iyeza

Uvavanyo lweDonath-Landsteiner luvavanyo lwegazi ukufumanisa ii-antibodies ezinobungozi ezinxulumene nengxaki enqabileyo ebizwa ngokuba yi-paroxysmal cold hemoglobinuria. Ezi antibodies zenza kwaye zitshabalalise iiseli ezibomvu zegazi xa umzimba ubhencekile kubushushu obubandayo.

Isampulu yegazi iyafuneka.

Akukho lungiselelo lukhethekileyo luyafuneka.

Xa kufakwa inaliti ukutsala igazi, abanye abantu baziva iintlungu eziphakathi. Abanye baziva behlaba okanye behlaba kuphela. Emva koko, kunokubakho ukubetha okanye ukukrala kancinci. Oku kuya kuhamba kungekudala.

Olu vavanyo lwenziwa ukuqinisekisa ukuxilongwa kwe-paroxysmal kubanda hemoglobinuria.

Uvavanyo luthathwa njengesiqhelo ukuba akukho zintsholongwane zeDonath-Landsteiner ezikhoyo. Oku kubizwa ngokuba sisiphumo esibi.

Amaxabiso esiqhelo ahluka kancinci phakathi kweelebhu ezahlukeneyo. Ezinye iilebhu zisebenzisa imilinganiselo eyahlukeneyo okanye ukuvavanya iisampulu ezahlukeneyo. Thetha nomboneleli wakho wezempilo malunga nentsingiselo yeziphumo zakho zovavanyo.

Iziphumo ezingaqhelekanga zithetha ukuba ii-antibodies zeDonath-Landsteiner zikhona. Olu luphawu hemoglobinuria paroxysmal ebandayo.


Akukho mngcipheko ubandakanyekileyo ekuthatheni igazi lakho. Imithambo kunye nemithambo iyahluka ngobukhulu ukusuka komnye umntu ukuya komnye nakwelinye icala lomzimba liye kwelinye. Ukuthatha igazi kwabanye abantu kunokuba nzima ngakumbi kunabanye.

Eminye imingcipheko enxulumene nokutsalwa kwegazi incinci, kodwa inokubandakanya:

  • Ukopha kakhulu
  • Ukufa isiqaqa okanye ukuziva ungenantloko
  • Ukugqobhoza okuninzi ukufumana imithambo
  • I-Hematoma (igazi elakhiweyo phantsi kolusu)
  • Usulelo (umngcipheko omncinci nangaliphi na ixesha ulusu lwaphukile)

Unyango-anti-P; Paroxysmal hemoglobinuria ebandayo - IDonath-Landsteiner

I-Elghetany MT, i-Schexneider KI, i-Banki K.Ukuphazamiseka kwe-Erythrocytic. Ku: McPherson RA, Pincus MR, ii-eds. Ukuchongwa kweKlinikhi kaHenry kunye noLawulo ngeendlela zeLebhu. Umhla we-23. ISt Louis, MO: Elsevier; Ngo-2017: isahluko 32.

UMichel M. Ukuzenzekelayo kunye ne-intravascular hemolytic anemias. Ku: IGoldman L, iSchafer AI, ii-eds. Amayeza eGoldman-Cecil. Ngomhla wama-26. IPhiladelphia, PA: Elsevier; 2020: isahl. 151.


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