Iifuchs dystrophy

Iifuchs (ezibizwa ngokuba zi "fooks") i-dystrophy sisifo samehlo apho iiseli ezigqume umphezulu wekoralea ziqala kancinci ukusweleka. Esi sifo sihlala sichaphazela amehlo omabini.

Iifuchs dystrophy zinokufunyanwa njengelifa, oko kuthetha ukuba inokudluliselwa isuka kubazali iye ebantwaneni. Ukuba omnye wabazali bakho unesifo, unethuba lama-50% lokuphuhlisa imeko.

Nangona kunjalo, imeko inokuthi yenzeke nakubantu ngaphandle kwembali yosapho eyaziwayo yesi sifo.

Iifuchs dystrophy zixhaphake kakhulu kwabasetyhini kunamadoda. Iingxaki zombono aziveli ngaphambi kweminyaka engama-50 kwimeko ezininzi. Nangona kunjalo, umboneleli wezempilo unokukwazi ukubona iimpawu zesifo kubantu abachaphazelekayo ngama-30s okanye ama-40 abo.

I-Fuchs dystrophy ichaphazela ungqimba olucekeceke lweeseli ezibeka umva kwinxalenye ye-cornea. Ezi seli zinceda ukumpompa ulwelo olungaphezulu kolwe-cornea. Njengoko iiseli ezininzi zilahlekile, ulwelo luqala ukwakha kwi-cornea, ebangela ukudumba kunye ne-cornea enamafu.

Ekuqaleni, ulwelo lunokwakha kuphela xa ulele, xa ilihlo livaliwe. Njengokuba esi sifo sisiya sisiba mandundu, kusenokubakho amadyungudyungu amancinci. Amadyungudyungu ayakhula kwaye ekugqibeleni anokuqhekeka. Oku kubangela iintlungu zamehlo. I-Fuchs dystrophy inokubangela ukuba imeko ye-cornea itshintshe, ekhokelela kwiingxaki ezingaphezulu zombono.

Iimpawu zingabandakanya:

• Intlungu yamehlo
• Uvakalelo lwamehlo ekukhanyeni nakwilitha
• Inkungu okanye umbono ophuthileyo, ekuqaleni kuphela kusasa
• Ukubona iihalos ezinemibala ejikeleze izibane
• Umbono owandayo imini yonke

Umboneleli unokuchonga i-Fuchs dystrophy ngexesha lovavanyo lwesibane.

Olunye uvavanyo olunokwenziwa lunokubandakanya:

• I-Pachymetry -imilinganiselo yobunzima be-cornea
• Uvavanyo lwe-microscope ekhethekileyo- ivumela umboneleli ukuba ajonge kumaleko amancinci eeseli ahambelana nenxalenye yangasemva ye-cornea
• Uvavanyo lwe-acuity ebonakalayo

Amaconsi wamehlo okanye amafutha okuthambisa ulwelo kwi-cornea asetyenziselwa ukunciphisa iimpawu ze-Fuchs dystrophy.

Ukuba izilonda ezibuhlungu zikhula kwi-cornea, iilensi zonxibelelwano ezithambileyo okanye uqhaqho ukwenza i-flaps ngaphezulu kwezilonda kunokunceda ukunciphisa iintlungu.

Unyango kuphela lwe-Fuchs dystrophy kukufakelwa kwe-corneal.

Kuze kube kutshanje, uhlobo oluqhelekileyo lokufakelwa kwe-corneal lwalungena kwi-keratoplasty. Ngexesha lale nkqubo, isiziba esincinci esirhangqileyo se-cornea siyasuswa, sishiya kuvuleke phambi kweliso. Icandelo elilinganayo le-cornea elivela kumnikeli womntu lithungwa ekuvulekeni ngaphambili kwamehlo.

Inkqubo entsha ebizwa ngokuba yi-endothelial keratoplasty (i-DSEK, i-DSAEK, okanye i-DMEK) iye yaba yindlela ekhethwayo kubantu abane-Fuchs dystrophy. Kule nkqubo, kuphela ngamanqanaba angaphakathi e-cornea atshintshiwe, endaweni yawo onke amanqanaba. Oku kukhokelela ekubuyiseni ngokukhawuleza kunye neengxaki ezimbalwa. Ukuthungwa kuhlala kungafuneki.

Iifuchs dystrophy iba mandundu ngokuhamba kwexesha. Ngaphandle kofakelo lwe-corneal, umntu one-Fuchs dystrophy enzima unokuba yimfama okanye abe nentlungu ebukhali kwaye anciphise umbono.

Amatyala athambileyo e-Fuchs dystrophy ahlala esiba mandundu emva kotyando lwamehlo. Ugqirha wotyando uya kuvavanya lomngcipheko kwaye unokutshintsha ubuchwephesha okanye ixesha lotyando lwe-cataract.

Fowunela umnikezeli wakho ukuba unayo:

• Intlungu yamehlo
• Ubuntununtunu bamehlo ekukhanyeni
• Imvakalelo yokuba kukho into esweni lakho xa kungekho nto ikhoyo
• Iingxaki zombono ezinje ngokubona iihalos okanye umbono onamafu
• Umbono owandayo

Akukho sithintelo saziwayo. Ukuthintela utyando lwe-cataract okanye ukuthatha amanyathelo okhuseleko ngexesha lotyando lwe-cataract kunokubambezela isidingo sokufakelwa kwe-corneal.

Fuchs ’idystrophy; I-Fuchs 'endothelial dystrophy; I-Fuchs 'corneal dystrophy

Folberg R. Iliso. Ku: Kumar V, Abbas AK, Aster JC, ii-eds. Robbins kunye neCotran Pathologic Isiseko seZifo. Ngomhla we-10. IPhiladelphia, PA: Elsevier; 2021: isahluko 29.

IPatel SV. Ukuya kuvavanyo lweklinikhi kwii-fuchs endothelial corneal dystrophy: ukuhlelwa kunye nemilinganiselo yesiphumo I-BMJ Vula iOphthalmology. 2019; 4 (1): e000321. IINKCUKACHA: 31414054.

IRosado-Adames N, Afshari NA. Izifo ze-corneal endothelium. Ku: Yanoff M, Duker JS, ii-eds. Ophthalmology. Umhla we-5. IPhiladelphia, PA: Elsevier; I-2019: isahluko 4.21.

Isalmon JF. ICornea. Ku: Isalmon JF, ed. I-Ophthalmology yeklinikhi yaseKanski. Umhla we-9. IPhiladelphia, PA: Elsevier; 2020: isahluko 7.