I-angioedema yelifa: yintoni, iimpawu kunye nonyango

Umxholo
- Ziintoni iimpawu
- Izizathu ezinokubangela
- Zeziphi iingxaki ezinokuvela
- Yintoni isifo
- Unyango lwenziwa njani
- Kufuneka wenze ntoni ngexesha lokukhulelwa?
I-angioedema yelifa sisifo semfuza esidala iimpawu ezifana nokudumba emzimbeni wonke, kunye neentlungu zesisu eziphindaphindayo ezinokuhamba nesicaphucaphu kunye nokugabha. Ngamanye amaxesha, ukudumba kunokuchaphazela amalungu afana nepancreas, isisu kunye nengqondo.
Ngokubanzi, ezi zimpawu zibonakala ngaphambi kweminyaka yobudala be-6 kunye nokuhlaselwa kokudumba kuhlala malunga neentsuku ezi-1 ukuya kwezi-2, ngelixa iintlungu zesisu zinokuhlala ukuya kwiintsuku ezi-5. Esi sifo sinokuhlala ixesha elide ngaphandle kokubangela iingxaki okanye ukungonwabi kwisigulana, de kufike iingxaki ezintsha.
I-angiedema yelifa sisifo esinqabileyo, esinokuvela nokuba asikho kusapho lwale ngxaki, sihlelwa kwiindidi ezi-3 ze-angiedema: uhlobo 1, uhlobo 2 kunye nohlobo 3, ngokweprotein echaphazelekayo emzimbeni.

Ziintoni iimpawu
Ezinye zezona mpawu zixhaphakileyo ze-angioedema kukudumba emzimbeni wonke, ngakumbi ebusweni, ezandleni, ezinyaweni nakumalungu esini, iintlungu esiswini, isicaphucaphu, ukugabha kwaye, kwiimeko ezinzima kakhulu, ukudumba kwamalungu anjengepancreas, isisu nengqondo.
Izizathu ezinokubangela
I-Angioedema ibangelwa kukutshintsha kwemfuza kwimfuza evelisa iproteni enxulumene nenkqubo yomzimba yokuzikhusela, ekhokelela ekubonakaleni kokudumba nanini na xa amajoni omzimba esebenza.
Iingxaki zinokubandezeleka kwimeko yengozi, uxinzelelo, okanye ngexesha lokuzilolonga. Ukongeza, abasetyhini bachaphazeleka lula ekuthinjweni ngexesha lokuya exesheni kunye nokukhulelwa.
Zeziphi iingxaki ezinokuvela
Eyona ngxaki iphambili ye-angiedema yelifa kukudumba emqaleni, kunokubangela ukusweleka ngenxa yokuphefumla. Ukongeza, xa kukho ukudumba kwamalungu athile, esi sifo sinokuphazamisa nokusebenza kwaso.
Ezinye iingxaki zinokubakho ngenxa yeziphumo ebezingalindelekanga zamachiza asetyenziselwa ukulawula isifo, kunye neengxaki ezinje:
- Ukutyeba kwakho;
- Intloko ebuhlungu;
- Utshintsho kwiimvakalelo;
- Ukwanda kwamabala;
- Uxinzelelo lwegazi;
- Cholesterol ephezulu;
- Utshintsho lokuya exesheni;
- Igazi kumchamo;
- Iingxaki zesibindi.
Ngexesha lonyango, abaguli kufuneka kuvavanyo lwegazi rhoqo kwiinyanga ezintandathu ukuvavanya ukusebenza kwesibindi, kwaye abantwana kufuneka benze iimvavanyo rhoqo kwiinyanga ezi-2 ukuya kwezi-3, kubandakanya ukuskena kwesisu esiswini rhoqo kwiinyanga ezi-6.
Yintoni isifo
Ukuchongwa kwesi sifo kwenziwa kwiimpawu kunye novavanyo lwegazi olulinganisa iprotein ye-C4 emzimbeni, ekumanqanaba asezantsi kwimeko ye-angiedema yelifa.
Ukongeza, ugqirha unokuyalela umlinganiso wobungakanani kunye nomgangatho weC1-INH, kwaye kunokuba yimfuneko ukuphinda kuvavanyo ngexesha lesifo.
Unyango lwenziwa njani
Unyango lwe-angiedema yelifa lwenziwa ngokobunzima kunye nokuhamba rhoqo kweempawu, kunye neziyobisi ezisekwe kwihomoni, ezinje nge-danazol, stanozolol kunye ne-oxandrolone, okanye amayeza e-antifibrinolytic, anje nge-epsilon-aminocaproic acid kunye ne-tranexamic acid. iingxaki.
Ngexesha leengxaki, ugqirha unokunyusa ithamo lamayeza kwaye acebise ukusetyenziswa kwamachiza ukulwa iintlungu zesisu kunye nesicaphucaphu.
Nangona kunjalo, ukuba ingxaki ibangela ukudumba emqaleni, isigulana kufuneka sithathwe ngokukhawuleza sisiwe kwigumbi likaxakeka, kuba ukudumba kungathintela indlela yomoya kwaye kuthintele ukuphefumla, okunokubangela ukufa.
Kufuneka wenze ntoni ngexesha lokukhulelwa?
Ngexesha lokukhulelwa, abaguli abane-angiedema yelifa kufuneka bayeke ukusebenzisa amayeza, ngakumbi ngaphambi kokuba bakhulelwe, njengoko kunokubangela ukungalunganga kwimveku. Ukuba kuvela iingxaki, unyango kufuneka lwenziwe ngokwesikhokelo sikagqirha.
Ngexesha lokuzalwa komntwana ngesiqhelo, ukuqala kohlaselo kunqabile, kodwa xa kuvela, kuhlala kunzima. Kwimeko yokuhanjiswa kwe-cesarean, kuphela ukusetyenziswa kwe-anesthesia yendawo kuyacetyiswa, kuthintela i-anesthesia ngokubanzi.