Ukutya kwePhenylketonuria: Ukuvunyelwa, Ukutya okungavumelekanga kunye neMenyu

Umxholo

• Ukutya kuvunyelwe kwi-phenylketonuria
• Ukutya kungavumelekanga kwi-phenylketonuria
• Inani le phenylalanine elivunyelweyo ngokobudala
• Imenyu yesampulu
• Imenyu yemizekelo yomntwana oneminyaka emi-3 ubudala ene-phenylketonuria:

Ekutyeni kwabantu abane-phenylketonuria kubaluleke kakhulu ukulawula ukutya kwe-phenylalanine, eyi-amino acid ekhoyo ikakhulu kukutya okune-protein, njengenyama, intlanzi, amaqanda, ubisi kunye neemveliso zobisi. Ke, abo bane-phenylketonuria kufuneka babe novavanyo lwegazi rhoqo ukuvavanya ubungakanani be-phenylalanine egazini kwaye, kunye nogqirha, babale inani le-phenylalanine abanokuyitya emini.

Kuba kunyanzelekile ukunqanda ukutya okuninzi okune-protein, i-phenylketonurics kufuneka isebenzise iiprotein ngaphandle kwe-phenylalanine, kuba iiproteni zizakha mzimba ezibaluleke kakhulu emzimbeni, ezingenakupheliswa ngokupheleleyo.

Ukongeza, xa kungekho phenylalanine, umzimba ufuna iidosi eziphezulu ze-tyrosine, eyenye i-amino acid ebaluleke kakhulu kuphuhliso xa kungekho phenylalanine. Ngesi sizathu, kuhlala kufanelekile ukongeza nge-tyrosine ukongeza kukutya. Jonga ukuba ezinye iindlela zokuthintela zibalulekile kunyango lwe-phenylketonuria.

Ukutya kuvunyelwe kwi-phenylketonuria

Ukutya okuvunyelweyo kubantu abane-phenylketonuria zezi:

• Iziqhamo:iapile, ipere, imelon, iidiliya, iacerola, ilamuni, ijabuticaba, currant;
• Ezinye iintlobo: isitashi, icassava;
• Iilekese: iswekile, ijeli yeziqhamo, ubusi, i-sago, i-cremogema;
• Amafutha: ioyile yemifuno, iikhrimu zemifuno ngaphandle kobisi kunye nezinye izinto;
• Abanye: iilekese, iilolipop, iziselo ezihlwahlwazayo, iziqhamo zepopu ngaphandle kobisi, ikofu, iti, ijelatin yemifuno eyenziwe ngolwandle, isardard, ipepile.

Kukho okunye ukutya okuvunyelweyo kwi-phenylketonurics, kodwa oko kufuneka kulawulwe. Oku kutya zezi:

• Imifuno ngokubanzi, enje ngesipinatshi, i-chard, iitumato, ithanga, i-yam, iitapile, iitapile, okra, ii-beet, icauliflower, iminqathe, ichayote.
• Abanye: irayisi noodles ngaphandle kwamaqanda, irayisi, amanzi ecoconut.

Ukongeza, kukho iinguqulelo ezizodwa zezithako ezinenani elincinci le-phenylalanine, njengerayisi, umgubo wengqolowa okanye ipasta, umzekelo.

Nangona izithintelo ekudleni zilungile kwi-phenylketonurics, zininzi iimveliso zeshishini ezingenayo i-phenylalanine ekwakhiweni kwazo okanye ezihlwempuzekileyo kule amino acid. Nangona kunjalo, kuzo zonke iimeko kubaluleke kakhulu ukuba kufundwe kwiphakheji yemveliso ukuba iqulethe i-phenylalanine.

Jonga uluhlu olupheleleyo lokutya okuvunyelweyo kunye nexabiso le-phenylalanine.

Ukutya kungavumelekanga kwi-phenylketonuria

Ukutya okungavumelekanga kwi-phenylketonuria zezo zityebileyo kwi-phenylalanine, ikakhulu ukutya okune-protein, njengoku:

• Ukutya kwezilwanyana: inyama, intlanzi, ukutya kwaselwandle, ubisi kunye nemveliso yenyama, amaqanda, kunye neemveliso zenyama ezifana nesoseji, isoseji, ibhekoni, ham.
• Ukutya kwemvelaphi yezityalo: ingqolowa, iichickpeas, iimbotyi, ii-ertyisi, iilentile, iimveliso zesoya kunye neemveliso zesoya, ii-chestnuts, ii-walnuts, amandongomane, ii-hazelnuts, ii-almonds, iipistachios, iipine nuts
• Iiswiti kunye ne-aspartame okanye ukutya okuqulethe esi sinandi;
• Iimveliso ezinokutya okungavumelekanga, njengeikeyiki, iicookies kunye nesonka.

Njengokuba ukutya kwe-phenylketonurics kusezantsi kwiprotein, aba bantu kufuneka bathathe izongezo ezizodwa zee-amino acid ezingenayo i-phenylalanine yokuqinisekisa ukukhula okukuko nokusebenza komzimba.

Inani le phenylalanine elivunyelweyo ngokobudala

Inani le-phenylalanine elinokutyiwa yonke imihla liyahluka ngokobudala nangobunzima, kunye nokondliwa kwe-phenylketonurics kufuneka kwenziwe ngendlela engagqithiyo kwixabiso le-phenylalanine. Uluhlu olungezantsi lubonisa amaxabiso avunyelweyo e-amino acid ngokweqela leminyaka:

• Phakathi kweenyanga ezi-0 ukuya kwezi-6: 20 ukuya kuma-70 mg / kg ngosuku;
• Phakathi kweenyanga ezisixhenxe kunye nonyaka omnye: 15 ukuya kuma-50 mg / kg ngosuku;
• Ukusuka kwi-1 ukuya kwi-4 yeminyaka ubudala: 15 ukuya ku-40 mg / kg ngosuku;
• Ukusuka kwiminyaka emi-4 ukuya kweli-7 ubudala: 15 ukuya ku-35 mg / kg ngosuku;
• Ukususela kwi-7 ukubheka phambili: 15 ukuya kwi-30 mg / kg ngosuku.

Ukuba umntu one-phenylketonuria ofaka i-phenylalanine kuphela kwiimali ezivunyelweyo, iimoto zabo kunye nophuhliso lwengqondo alusayi kuphazamiseka. Ukuze ufunde okungakumbi jonga: Qonda ngcono ukuba yintoni iPhenylketonuria kunye nokuba inyangwa njani.

Imenyu yesampulu

Imenyu yokutya ye-phenylketonuria kufuneka ibe yeyomntu kwaye ilungiselelwe ngumdli wesondlo, njengoko kufuneka ithathele ingqalelo ubudala bomntu, inani le-phenylalanine elivunyelweyo kunye neziphumo zovavanyo lwegazi.

Imenyu yemizekelo yomntwana oneminyaka emi-3 ubudala ene-phenylketonuria:

Ukunyamezelana: 300 mg ye-phenylalanine ngosuku

Kukwabalulekile ukuba umntu kunye namalungu osapho lwabo bajonge iilebheli zemveliso nokuba ukutya akunayo i-phenylalanine kunye nokuba yintoni umxholo wayo, ngaloo ndlela kulungelelaniswa inani lokutya okunokusetyenziswa.