Ioli yeLorenzo yokunyanga iAdrenoleukodystrophy

Umxholo

• Iimpawu zeoyile yeLorenzo
• Uyisebenzisa kanjani ioyile kaLorenzo
• Iziphumo ebezingalindelekanga zeoyile yeLorenzo
• Ukungqinisisa ioyile yeLorenzo

Ioyile kaLorenzo sisongezelelo sokutya kunye glycero kathathul kunyeglycerol trierucate,sasidla ngokunyanga iadrenoleukodystrophy, isifo esinqabileyo esikwabizwa ngokuba sisifo sikaLorenzo.

I-Adrenoleukodystrophy ibangelwa kukuqokelelwa kwee-acid ezinamaxesha amade kakhulu kwingqondo nakwincindi ye-adrenal kwaye ibangela ukudanjiswa komzimba kwee-neurons. Ioyile ka-Lorenzo inceda ekumiseni amanqanaba e-asidi enamafutha kwaye xa isetyenziswa kwizigulana ezingenasifo, yehlisa umngcipheko wokuba nesifo esiqhekezayo kwaye, kwezinye izigulana ezinempawu, zinokuphucula umgangatho wobomi.

Iimpawu zeoyile yeLorenzo

Ioyile kaLorenzo ibonakalisiwe kunyango lwe-adrenoleukodystrophy, inceda ukuthintela iingxaki kwinkqubo yeemvakalelo kubantwana abane-adrenoleukodystrophy, kodwa abangekabonisi zimpawu. Kubantwana ababonisa iimpawu zesi sifo, ioyile kaLorenzo ibonakaliswa njengonyango lokuphucula nokwandisa umgangatho wobomi.

Uyisebenzisa kanjani ioyile kaLorenzo

Ukusetyenziswa kweoyile kaLorenzo kubandakanya ukuthatha i-2 ukuya kwi-3 ml / ngosuku ukunceda ukunyanga abantwana abane-adrenoleukodystrophy. Nangona kunjalo, idosi kufuneka yanele ngokwemeko yempilo yesigulana.

Iziphumo ebezingalindelekanga zeoyile yeLorenzo

Iziphumo ebezingalindelekanga zeoyile kaLorenzo zinqabile, kodwa zinokubandakanya ukugruzuka okanye ukopha.

Ukungqinisisa ioyile yeLorenzo

Ioyile kaLorenzo iyaphikiswa kwabasetyhini abakhulelweyo nabancancisayo kuba akukho zifundo zibonisa ukusebenza kunye nokhuseleko.

Akufanele isetyenziswe kwizigulana ezinokuhla kwenani leeplatelets egazini, i-thrombocytopenia, okanye ukwehla kweeseli ezimhlophe zegazi, i-neutropenia.