I-Evans Syndrome-Iimpawu kunye nonyango

Umxholo
I-Evans syndrome, ekwabizwa ngokuba yi-anti-phospholipid syndrome, sisifo esinqabileyo sokuzimela, apho umzimba uvelisa izilwa-buhlungu ezitshabalalisa igazi.
Abanye abaguli abanesi sifo banokuba neeseli ezimhlophe kuphela ezonakalisiweyo okanye iiseli ezibomvu kuphela, kodwa lonke ulwakhiwo lwegazi lunokonakala xa kuziwa kwi-Evans Syndrome.
Ngokukhawuleza ukuxilongwa ngokuchanekileyo kwesi sifo kwenziwa, kulula ukuba iimpawu zilawulwe kwaye ke isiguli sinomgangatho wobomi obungcono.

Yintoni ebangela
Into ekhuthaza esi sifo ayisaziwa, kwaye iimpawu kunye nokuvela kwesi sifo kunqabile kwahluke kakhulu kwimeko ngecala, kuxhomekeke kwinxalenye yegazi ehlaselwe zizilwi-buhlungu.
Iimpawu kunye neempawu
Xa iiseli ezibomvu zonzakele, zehlisa amanqanaba egazi, isigulana siba neempawu ezibonisa ukungabikho kwegazi, kwimeko apho iiplatelets kufuneka zitshatyalaliswe, isigulana sisengozini yokwenziwa kwemivumbo nokopha ukuba kwimeko ukwenzakala entloko kunokubangela ukopha kwengqondo ebulalayo kwaye xa kuyinxalenye emhlophe yegazi echaphazelekayo isigulana sisengozini yosulelo ehamba kunye nobunzima obukhulu bokubuyela kwimeko yesiqhelo.
Kuqhelekile kwizigulana ezine-Evans syndrome ukuba nezinye izifo ezizimeleyo ezifana ne-lupus okanye i-rheumatoid arthritis, umzekelo.
Ukuvela kwesi sifo akulindelwanga kwaye kwiimeko ezininzi iziqendu zentshabalalo enkulu yeeseli zegazi zilandelwa lixesha elide lokuxolelwa, ngelixa ezinye iimeko ezinzima kakhulu ziguquka ngokuqhubekayo ngaphandle kwamaxesha okuphucula.
Unyango lwenziwa njani
Unyango lujolise ekuyekiseni imveliso yeentsholongwane ezitshabalalisa igazi. Unyango asisinyangi isifo, kodwa kuyanceda ukunciphisa iimpawu zaso, ezifana neanemia okanye thrombosis.
Ukusetyenziswa kwe-steroids kuyacetyiswa njengoko becinezela amajoni omzimba kunye nokunciphisa ukuveliswa kwee-antibodies, ukuphazamisa okanye ukunciphisa inqanaba lokutshatyalaliswa kweeseli zegazi.
Olunye ukhetho kukufaka inaliti ye-immunoglobulins ukutshabalalisa ii-antibodies ezigqithisileyo eziveliswa ngumzimba okanye yichemotherapy, eqinisa isigulana.
Kwiimeko ezinzima kakhulu, ukususwa kwepeni yindlela yokonyango, njengotofelo-gazi.