Lunjani unyango lwe-hemophilia

Umxholo

• Iindidi zonyango
• Unyango kwimeko ye-hemophilia ene-inhibitor
• Ukunyamekela ngexesha lonyango

Unyango lwe-hemophilia lwenziwa ngokutshintsha izinto ezi-clotting ezingenanto emntwini, eyi-factor VIII, kwimeko yohlobo lwe-hemophilia A, kunye ne-factor IX, kwimeko yohlobo lwe-hemophilia B, njengoko kunokwenzeka ukuthintela ukopha kakhulu.

IHemophilia sisifo semfuza apho kukho ukwehla kwemisebenzi okanye ukungabikho kwezinto ezijiyisayo, eziziiproteni ezikhoyo egazini ezenziwa xa kukho ukophuka komthambo wegazi, othintela ukopha kakhulu. Ke, xa kusetyenziswa ukutshintshwa kwezinto ezijiyayo, kunokwenzeka ukuba umntu one-hemophilia aphile ubomi obuqhelekileyo, ngaphandle kwemiqobo emininzi. Funda ngakumbi malunga ne-hemophilia.

Iindidi zonyango

Nangona lungekho unyango, unyango lwe-hemophilia lunceda ukuthintela ukopha kungenzeki rhoqo, kwaye kufuneka lukhokelwe yi-hematologist kwaye lunokwenziwa ngeendlela ezimbini ezahlukeneyo:

• Unyango lokuthintela: kubandakanya ukutshintshwa okwenzeka rhoqo kwamaxesha kwezinto ezijiyisayo, ukuze zihlale zinamanqanaba anyukayo emzimbeni, kwaye kuthintele ukopha okunokwenzeka. Olu hlobo lonyango alunakuba yimfuneko kwimeko ye-haemophilia ethambileyo, kwaye kunokucetyiswa ukwenza unyango kuphela xa kukho uhlobo oluthile lokopha.
• Unyango emva kokopha: lunyango kwimfuno, lwenziwe kuwo onke amatyala, kunye nokusetyenziswa kwento ekujiyelwa yingqondo xa kukho isiqendu sokopha, esivumela ukuba isonjululwe ngokukhawuleza.

Ngalo naluphi na unyango, iidosi kufuneka zibalwe ngokobunzima bomzimba, ubungqongqo be-hemophilia kunye nenqanaba lomsebenzi we-clotting factor umntu ngamnye egazini lakhe. I-Factor VIII okanye i-IX igxila kwi-ampoule eyimpuphu ehlanjululwa ngamanzi afakwe kwisicelo.

Ukongeza, ezinye iindidi ze-hemostatic arhente egxila zingasetyenziselwa ukunceda ekuxinaneni, njenge-cryoprecipitate, prothrombin complex kunye ne-desmopressin, umzekelo. Olu nyango lwenziwa simahla yi-SUS, kumaziko e-hematology, ngokuthunyelwa ngugqirha oqhelekileyo okanye ugqirha wegazi.

Unyango kwimeko ye-hemophilia ene-inhibitor

Ezinye iihemophiliacs zinokuvelisa ii-antibodies ngokuchasene ne-VIII okanye i-IX concentrate esetyenziselwa unyango, ebizwa ngokuba zii-inhibitors, ezinokuthintela impendulo kunyango.

Kule meko, kunokuba yimfuneko ukwenza unyango ngeedosi eziphezulu, okanye ngokudityaniswa kwamanye amacandelo egazi.

Ukunyamekela ngexesha lonyango

Abantu abane-hemophilia kufuneka bathathe la manyathelo alandelayo:

• Ziqhelanise nemisebenzi yomzimba, ukomeleza izihlunu kunye namalungu, ukunciphisa amathuba okopha. Nangona kunjalo, kubalulekile ukunqanda ifuthe lezemidlalo okanye unxibelelwano lobundlobongela;
• Jonga ukuvela kweempawu ezintsha, ngakumbi ebantwaneni, kunye nokwehla kunyango;
• Soloko unamayeza kufutshane, ikakhulu kwimeko yohambo;
• Yiba nesazisi, Njengesongo, esibonisa isifo, kwimeko kaxakeka;
• Yazisa imeko ngalo lonke ixesha usenza nayiphi na inkqubo, ezinje ngesicelo sokugonya, utyando lwamazinyo okanye iinkqubo zonyango;
• Gwema amayeza ahambisa ukopha, ezinje nge-aspirin, anti-inflammatories kunye nee-anticoagulants, umzekelo.

Ukongeza, unyango lomzimba kufuneka lube yinxalenye yonyango lwe-hemophilia, njengoko ikhuthaza ukuphuculwa kokusebenza kweemoto, ukunciphisa umngcipheko weengxaki, ezinje nge-acute hemolytic synovitis, kukudumba kwelungu ngenxa yokopha, kwaye kuphucula ithoni yezihlunu, kwaye ke isenokunciphisa isidingo sokuthatha izinto ezijija igazi kunye nokuphucula umgangatho wobomi.