Ukuthintela umthambo we-Hepatic (Budd-Chiari)
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Ukuthintelwa kwemithambo ye-hepatic kukuvaleka komthambo we-hepatic, ohambisa igazi kude nesibindi.
Ukuthintela umthambo we-Hepatic kuthintela igazi ukuba lingaphumi ngaphandle kwesibindi libuyele entliziyweni. Olu vimba lunokubangela ukonakala kwesibindi. Ukuthintelwa kwalo mthambo kungabangelwa yithumba okanye kukucinezela kokukhula kwinqanawa, okanye ngengubo kwisitya (hepatic vein thrombosis).
Rhoqo, kubangelwa ziimeko ezenza ukuba amahlwili egazi abe nakho ukwenza, kubandakanya:
- Ukukhula okungaqhelekanga kweeseli kumongo wethambo (iingxaki ze-myeloproliferative)
- Umhlaza
- Izifo ezingapheliyo okanye ezivuthayo
- Usulelo
- Ilifa (ilifa) okanye iingxaki ezifunyenwe ngegazi
- Izinto zokucwangcisa ngomlomo
- Ukukhulelwa
Ukuvalwa kwemithambo ye-Hepatic sesona sizathu sixhaphakileyo sesifo sikaBudd-Chiari.
Iimpawu zibandakanya:
- Ukudumba kwesisu okanye ukuzolula ngenxa yolwelo esiswini
- Intlungu kwisisu esisekunene
- Ukuphalaza igazi
- Ubumthubi besikhumba (i-jaundice)
Olunye lweempawu kukukrala kwesisu esisuka kulwakhiwo olunamanzi (ascites). Isibindi sihlala sidumbile kwaye sithambile.
Uvavanyo lubandakanya:
- I-CT scan okanye i-MRI yesisu
- I-Doppler ultrasound yemithambo yesibindi
- Isibindi se-biopsy
- Uvavanyo lomsebenzi wesibindi
- I-Ultrasound yesibindi
Unyango luyahlukahluka, kuxhomekeka kwisizathu sokuvaleka.
Umboneleli wakho wezempilo unokucebisa la mayeza alandelayo:
- Abacoci begazi (ii-anticoagulants)
- Iziyobisi ezisebenza ngokuqhekeka kwegazi (unyango lwe-thrombolytic)
- Amayeza ukunyanga isifo sesibindi, kubandakanya i-ascites
Utyando lunokucetyiswa. Oku kunokubandakanya:
- I-Angioplasty kunye nokubekwa kwesitent
- I-transjugular intrahepatic portosystemic shunt (iingcebiso)
- Utyando lwe-venous shunt
- Ukufakelwa kwesibindi
Ukuthintela umthambo we-Hepatic kunokuba kubi ngakumbi kwaye kukhokelele kwisibindi kunye nokusilela kwesibindi. Oku kunokuba sisongelo lobomi.
Fowunela umnikezeli wakho ukuba:
- Unempawu zokuthintela umthambo we-hepatic
- Uyanyangelwa le meko kwaye ukhulisa iimpawu ezintsha
Isifo seBudd-Chiari; Isifo seHepatic veno-occlusive
Inkqubo yokwetyisa
Inkqubo yokugaya ukutya
Ukubumba kwegazi
Amahlwili egazi
IKahi CJ. Izifo zeVascular zephecana lesisu. Ku: IGoldman L, iSchafer AI, ii-eds. Amayeza eGoldman-Cecil. Ngomhla wama-26. IPhiladelphia, PA: Elsevier; 2020: isahl. 134.
UNery FG, uValla DC. Izifo zemithambo yesibindi. Ku: UFeldman M, uFriedman LS, uBrandt LJ, ii-eds. Sleisenger kunye neFordtran's Gastrointestinal and Liver Disease. Ngomhla we-11. IPhiladelphia, PA: Elsevier; 2021: isahluko 85.