Idysplasia emnandi

I-Fibrous dysplasia sisifo samathambo esitshabalalisa kwaye sithathe indawo yethambo eliqhelekileyo elinethambo elinethambo. Elinye okanye amaninzi amathambo anokuchaphazeleka.

I-Fibrous dysplasia ihlala ivela ebuntwaneni. Uninzi lwabantu baneempawu ngexesha abaneminyaka engama-30 ubudala. Esi sifo senzeka rhoqo kubantu basetyhini.

I-Fibrous dysplasia inxulunyaniswa nengxaki yemfuza (uguquko) elawula iiseli ezivelisa amathambo. Ukutshintsha kwenzeka xa umntwana ekhula esibelekweni. Le meko ayidluliswanga ukusuka kumzali iye emntwaneni.

Iimpawu zinokubandakanya nayiphi na kwezi zinto zilandelayo:

• Intlungu yethambo
• Izilonda zamathambo (izilonda)
• Iingxaki ze-Endocrine (hormone)
• Ukuqhekeka okanye ukukhubazeka kwethambo
• Umbala wesikhumba ongaqhelekanga (i-pigmentation), eyenzeka ngeMcCune-Albright syndrome

Izilonda zamathambo zinokuyeka xa umntwana efikisa.

Umboneleli wezempilo uya kwenza uvavanyo lomzimba. I-X-ray yamathambo ithathwa. Kunokucetyiswa iMRI.

Akukho lonyango lwe-dysplasia enemicu. Ukuqhekeka kwamathambo okanye ukukhubazeka kuphathwa xa kufuneka njalo. Iingxaki zeHormone ziya kufuna ukunyangwa.

Imbonakalo ixhomekeke kubukhali bemeko kunye neempawu ezenzekayo.

Kuxhomekeka kumathambo achaphazelekayo, iingxaki zempilo ezinokubangela zibandakanya:

• Ukuba ithambo lokakayi liyachaphazeleka, kunokubakho umbono okanye ilahleko yokuva
• Ukuba ithambo lomlenze lichaphazelekayo, kunokubakho ubunzima bokuhamba kunye neengxaki zokudibanisa ezifana nesifo samathambo

Biza umnikezeli wakho ukuba umntwana wakho uneempawu zale meko, njengokuphindaphindeka kwethambo kunye nokungaqondakali kwethambo.

Iingcali kwi-orthopedics, endocrinology, kunye ne-genetics zingabandakanyeka ekuxilongweni nasekunyamekeleni umntwana wakho.

Akukho ndlela yaziwayo yokuthintela i-fibrous dysplasia. Unyango lujolise ekuthinteleni iingxaki, ezinje ngokuqhekeka kwamathambo okuphindaphindayo, ukunceda ukwenza imeko ingaphantsi.

Ukudumba hyperplasia fibrous; Idiopathic fibrous hyperplasia; Isifo seMcCune-Albright

• Ngaphambili i-anatomy yamathambo

I-Czerniak B. I-Fibrous dysplasia kunye nezilonda ezinxulumene noko. Ku: Czerniak B, ed. Amathambo kaDorfman noCzerniak. Ngomhla wesi-2. IPhiladelphia, PA: Elsevier Saunders; 2016: isahl 8.

Heck RK, PC yokudlala. Izilonda zethambo zeBenign kunye neemeko ezingafakwanga zeplastiki zilinganisa izicubu zethambo. Ku: Azar FM, Beaty JH, Kanale ST, ii-eds. Umsebenzi weCampbell's Orthopedics. Umhla we-13. IPhiladelphia, PA: Elsevier; Ngo-2017: isahluko 25.

Umthengisi SN, uNadol JB. Ukubonakaliswa kwe-Otologic yesifo se-systemic. Ku: Flint PW, Haughey BH, Lund V, et al, ii-eds. I-Cummings Otolaryngology: Utyando lweNtloko kunye neNtamo. Umhla wesi-6. IPhiladelphia, PA: Elsevier Saunders; 2015: isahluko 149.

UShiflett JM, uPerez AJ, uMzali AD. Izilonda zokhakhayi ebantwaneni: i-dermoids, i-langerhans cell histiocytosis, i-fibrous dysplasia, kunye ne-lipomas. Ku: Winn HR, ed. Ugqirha we-Youmans kunye no-Winn Neurological. Umhla wesi-7. IPhiladelphia, PA: Elsevier; Ngo-2017: isahluko 219.