Umbhali: William Ramirez
Umhla Wokudalwa: 20 Eyomsintsi 2021
Hlaziya Umhla: 1 Eyekhala 2024
Anonim
Hereditary Hemorrhagic Telangiectasia - HHT Center of Excellence at UCLA
Ividiyo: Hereditary Hemorrhagic Telangiectasia - HHT Center of Excellence at UCLA

I-Telangiectasias zincinci, zandisiwe yimithambo yegazi kulusu. Zihlala zingenabungozi, kodwa zinokunxulunyaniswa nezifo ezininzi.

I-Telangiectasias inokukhula naphina emzimbeni. Kodwa zibonakala ngokulula kulusu, inwebu yangaphakathi, kunye nabamhlophe ngamehlo. Ngokwesiqhelo, azibangeli zimpawu. Ezinye i-telangiectasias zopha kwaye zibangela iingxaki ezinkulu. I-Telangiectasias nayo inokwenzeka kwingqondo okanye emathunjini kwaye ibangele iingxaki ezinkulu ekuphumeni kwegazi.

Izizathu zingabandakanya:

  • I-rosacea (ingxaki yolusu ebangela ubuso bujike bubomvu)
  • Ukwaluphala
  • Ingxaki ngemfuza
  • Ukukhulelwa
  • Ukuvezwa lilanga
  • Iimvumba ze-Varicose
  • Ukusetyenziswa gwenxa kweoyile ye-steroid
  • Ukuxhwaleka kwindawo

Izifo ezinxulumene nale meko zibandakanya:

  • I-Ataxia-telangiectasia (isifo esichaphazela ulusu, ibhalansi kunye nokulungelelanisa, kunye nezinye iindawo zomzimba)
  • Isifo seBloom (isifo esizuzwe njengelifa esibangela ubude obufutshane, ubuntununtunu besikhumba kwimitha yelanga, kunye nobomvu ebusweni)
  • I-Cutis marmorata telangiectatica congenita (isifo solusu esibangela ubomvu)
  • I-telangiectasia ene-hemorrhagic hemorrhagic (i-Osler-Weber-Rendu syndrome)
  • I-Klippel-Trenaunay-Weber syndrome (isifo esibangela i-port-wine stain, varicose veins, kunye neengxaki zeethishu ezithambileyo)
  • I-Nevus flammeus enjengebala lewayini-port
  • I-rosacea (imeko yolusu ebangela ukuba bomvu kobuso)
  • Isifo se-Sturge-Weber (isifo esibandakanya ibala lewayini kunye neengxaki zenkqubo)
  • I-Xeroderma pigmentosa (isifo apho ulusu kunye nezicubu ezigqume iliso zibuthathaka kakhulu kukukhanya kwe-ultraviolet)
  • I-Lupus (isifo samajoni omzimba)
  • I-CREST syndrome (uhlobo lwe-scleroderma olubandakanya ukwakheka kwezicubu ezinjengezikhumba kulusu nakwezinye iindawo emzimbeni kunye nokonakalisa iiseli ezihambelana nodonga lweemithambo ezincinci)

Tsalela umnxeba ukhathalelo lwempilo ukuba ubona iinqanawa ezandisiweyo kulusu, inwebu yeliso okanye amehlo.


Umboneleli uya kwenza uvavanyo lomzimba kwaye abuze malunga neempawu zakho, kubandakanya:

  • Ifumaneka phi imithambo yegazi?
  • Ngaba bayopha ngokulula nangaphandle kwesizathu?
  • Zeziphi ezinye iimpawu ezikhoyo?

Iimvavanyo zinokufuneka ukuze kufunyanwe okanye kuphume imeko yonyango. Uvavanyo lunokubandakanya:

  • Uvavanyo lwegazi
  • Ukuskena kweCT
  • Izifundo zomsebenzi wesibindi
  • Ukuskena iMRI
  • X-reyi

I-Sclerotherapy yonyango lwe-telangiectasias emilenzeni. Kule nkqubo, isisombululo se-saline (ityuwa) okanye enye imichiza ifakwa ngqo kwimithambo yesigcawu emilenzeni. Unyango lwe-Laser luhlala lusetyenziselwa ukunyanga i-telangiectasias yobuso.

Ii-ectasias zeVascular; Isigcawu angioma

  • I-Angioma serpiginosum
  • I-Telangiectasia - imilenze
  • I-Telangiectasias - ingalo ephezulu

UKelly R, uBaker C. Olunye uhlobo lokuphazamiseka kwemithambo. Ku: I-Bolognia JL, uSchaffer JV, uCerroni L, ii-eds. Dermatology. Ngomhla we-4. IPhiladelphia, PA: Elsevier; Ngo-2018: isahluko 106.


IPatterson JW. Amathumba eVascular. Ku: Patterson JW, ed. Weedon's Ulusu lwezifo. Ngomhla we-4. IPhiladelphia, PA: Elsevier Churchill Livingstone; 2016: isahluko 38.

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