Umbhali: Gregory Harris
Umhla Wokudalwa: 16 Utshazimpuzi 2021
Hlaziya Umhla: 25 Isilimela 2024
Anonim
Uvavanyo lwe-hemolysis yeswekile-yamanzi - Iyeza
Uvavanyo lwe-hemolysis yeswekile-yamanzi - Iyeza

Uvavanyo lwe-hemolysis yeswekile-amanzi luvavanyo lwegazi ukufumana iiseli ezibomvu ezibuthathaka. Ikwenza oku ngokuvavanya ukuba bamelana njani nokudumba kwisisombululo seswekile (i-sucrose).

Isampulu yegazi iyafuneka.

Akukho lungiselelo lukhethekileyo olufunekayo kolu vavanyo.

Xa kufakwa inaliti ukutsala igazi, abanye abantu baziva iintlungu eziphakathi. Abanye baziva behlaba okanye behlaba kuphela. Emva koko, kunokubakho ukubetha okanye ukukrala kancinci. Oku kuya kuhamba kungekudala.

Umboneleli wakho wezempilo unokucebisa olu vavanyo ukuba uneempawu okanye iimpawu ze-paroxysmal nocturnal hemoglobinuria (PNH) okanye i-hemolytic anemia yesizathu esingaziwayo. I-hemolytic anemia yimeko apho iiseli ezibomvu zegazi zifa ngaphambi kokuba zife. Iiseli ezibomvu ze-PNH zisenokwenzeka ukuba zenzakaliswe yinkqubo yomzimba yokuxhasa. Inkqubo yokuncedisa ziiproteni ezihamba ngokuhamba kwegazi. Ezi proteni zisebenza kunye namajoni omzimba.

Iziphumo zovavanyo eziqhelekileyo zibizwa ngokuba ziziphumo ezibi. Iziphumo eziqhelekileyo zibonisa ukuba ngaphantsi kwe-5% yeeseli ezibomvu zegazi ziyehla xa kuvavanywa. Oku kwaphuka kubizwa ngokuba yihemolysis.


Uvavanyo olubi alukhupheli PNH. Iziphumo ezingalunganga zinokubakho ukuba inxenye yegazi egazini (i-serum) isilela ukuhambelana.

Amaxabiso esiqhelo ahluka kancinci phakathi kweelebhu ezahlukeneyo. Ezinye iilebhu zisebenzisa imilinganiselo eyahlukeneyo okanye ukuvavanya iisampulu ezahlukeneyo. Thetha nomboneleli wakho malunga nentsingiselo yeziphumo zakho zovavanyo.

Iziphumo zovavanyo ezakhayo zithetha ukuba iziphumo aziqhelekanga. Kuvavanyo oluqinisekileyo, ngaphezulu kwe-10% yeeseli ezibomvu zegazi ziyehla. Ingabonisa ukuba umntu une-PNH.

Iimeko ezithile zingenza ukuba iziphumo zovavanyo zibonakale zilungile (zibizwa ngokuba "bubuxoki"). Ezi meko zi-autoimmune hemolytic anemias kunye neukemia.

Akukho mngcipheko ubandakanyekileyo ekuthatheni igazi lakho. Imithambo kunye nemithambo iyahluka ngobukhulu ukusuka komnye umntu ukuya komnye nakwelinye icala lomzimba liye kwelinye. Ukuthatha igazi kwabanye abantu kunokuba nzima ngakumbi kunabanye.

Eminye imingcipheko enxulumene nokutsalwa kwegazi incinci, kodwa inokubandakanya:

  • Ukopha kakhulu
  • Ukufa isiqaqa okanye ukuziva ungenantloko
  • Ukugqobhoza okuninzi ukufumana imithambo
  • I-Hematoma (igazi elakhiweyo phantsi kolusu)
  • Usulelo (umngcipheko omncinci nangaliphi na ixesha ulusu lwaphukile)

Uvavanyo lwe-Sucrose hemolysis; Uvavanyo lwe-hemolytic anemia yeswekile yovavanyo lwamanzi; Paroxysmal ebusuku hemoglobinuria iswekile yovavanyo lwe-hemolysis; Uvavanyo lwe-PNH iswekile yovavanyo lwamanzi


UBrodsky RA. Paroxysmal ebusuku hemoglobinuria. Ku: Hoffman R, Benz EJ, Silberstein LE, ii-eds. I-Hematology: Imigaqo esisiseko kunye nokuziqhelanisa. Umhla wesi-7. IPhiladelphia, PA: Elsevier; I-2018: isahluko 31.

IChernecky CC, iBerger BJ. Uvavanyo lwe-Sucrose hemolysis-diagnostic. Ku: IChernecky CC, iBerger BJ, ii-eds. Iimvavanyo zaselebhu kunye neenkqubo zokuqonda isifo. Umhla wesi-6. ISt Louis, MO: Elsevier Saunders; Ngo-2013: 1050.

IGallagher PG. I-hemolytic anemias: inwebu ebomvu yegazi kunye neziphene kwimetabolism. Ku: IGoldman L, iSchafer AI, ii-eds. Amayeza eGoldman-Cecil. Ngomhla wama-26. IPhiladelphia, PA: Elsevier; 2020: isahluko152.

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