Isifo sengqondo esixhalabisayo

Umxholo

• Zithini iimpawu zesifo sehyperviscosity?
• Yintoni ebangela isifo sehyperviscosity?
• Ngubani osemngciphekweni wehyperviscosity syndrome?
• Isifo sehyperviscosity syndrome sifunyanwa njani?
• Inyangwa njani i-hyperviscosity syndrome?
• Ithini imbono yexesha elide?

Yintoni isifo sehyperviscosity?

Isifo sehyperviscosity syndrome yimeko apho igazi lingenakho ukuhamba ngokukhululekileyo kwimithambo yakho.

Kule syndrome, iibhlokhi zomthambo zinokwenzeka ngenxa yeeseli ezibomvu zegazi, iiseli ezimhlophe zegazi, okanye iiproteni kwigazi lakho. Inokuthi yenzeke nangayo nayiphi na iiseli ezibomvu ezime ngokungaqhelekanga, ezinje nge-sickle cell anemia.

Hyperviscosity yenzeka kubo bobabini nakubantu abadala. Kubantwana, inokuchaphazela ukukhula kwabo ngokunciphisa ukuhamba kwegazi kumalungu abalulekileyo, anjengentliziyo, amathumbu, izintso kunye nengqondo.

Kubantu abadala, kunokwenzeka ngezifo ezizimeleyo ezifana ne-rheumatoid arthritis okanye i-systemic lupus. Inokuphinda ikhule ngomhlaza wegazi njenge-lymphoma kunye neleukemia.

Zithini iimpawu zesifo sehyperviscosity?

Iimpawu ezinxulumene nale meko zibandakanya iintloko, ukuxhuzula, kunye nebala elibomvu kulusu.

Ukuba usana lwakho lulele ngendlela engaqhelekanga okanye alufuni kondla ngesiqhelo, oku kubonisa ukuba kukho into engalunganga.

Ngokubanzi, iimpawu ezinxulumene nale meko ziziphumo zeengxaki ezenzekayo xa amalungu abalulekileyo angafumani oksijini yaneleyo ngegazi.

Ezinye iimpawu zesifo sehyperviscosity zibandakanya:

• ukopha ngokungaqhelekanga
• Ukuphazamiseka okubonakalayo
• i-vertigo
• iintlungu zesifuba
• ukuqhawukelwa ngumphefumlo
• ukuxhuzula
• ikhoma
• ubunzima bokuhamba

Yintoni ebangela isifo sehyperviscosity?

Esi sifo sifunyaniswa kwiintsana xa inqanaba leeseli ezibomvu zegazi lingaphezulu kweepesenti ezingama-65. Oku kunokubangelwa ziimeko ezininzi ezikhula ngexesha lokumitha okanye ngexesha lokuzalwa. Oku kunokubandakanya:

• Ukubambana kade kwenkaba
• izifo ezizuzwe njengelifa kubazali
• iimeko zofuzo, ezinjenge-Down syndrome
• isifo seswekile

Inokubangelwa neemeko apho kungekho oksijini yaneleyo ihanjiswa kwizicubu emzimbeni womntwana wakho. I-twin-to-twin syndrome, imeko apho amawele ngokungalingani abelana ngegazi phakathi kwawo esibelekweni, inokuba sesinye isizathu.

I-Hyperviscosity syndrome inokubangelwa ziimeko ezichaphazela ukuveliswa kweeseli zegazi, kubandakanya:

• Ileukemia, umhlaza wegazi ophumela kwiiseli ezimhlophe zegazi ezininzi kakhulu
• polycythemia vera, umhlaza wegazi ophumela kwiiseli ezibomvu ezininzi kakhulu
• thrombocytosis ebalulekileyo, imeko yegazi eyenzekayo xa umongo wethambo uvelisa iiplatelets ezininzi zegazi
• Iingxaki ze-myelodysplastic, iqela lokuphazamiseka kwegazi elibangela inani elingaqhelekanga leeseli ezithile zegazi, ukugcwala iiseli ezisempilweni kumongo wethambo kwaye zihlala zikhokelela kwi-anemia enzima

Kubantu abadala, isifo se-hyperviscosity syndrome sibangela iimpawu xa i-viscosity yegazi iphakathi kwe-6 kunye ne-7, elinganiswa ngokuhambelana nesaline, kodwa inokuba sezantsi. Amaxabiso aqhelekileyo ahlala ephakathi kwe-1.6 kunye ne-1.9.

Ngexesha lonyango, injongo kukuthoba i-viscosity kwinqanaba elifunekayo ukusombulula iimpawu zomntu.

Ngubani osemngciphekweni wehyperviscosity syndrome?

Le meko ihlala ichaphazela iintsana, kodwa inokukhula nokuba mdala. Inkqubo yale meko ixhomekeke kwisizathu sayo:

• Usana lwakho lusemngciphekweni omkhulu wokukhula kwesi sifo ukuba unembali yosapho.
• Kwakhona, abo banembali yeemeko ezinzima zomongo wethambo basemngciphekweni omkhulu wokufumana isifo sehyperviscosity.

Isifo sehyperviscosity syndrome sifunyanwa njani?

Ukuba ugqirha wakho ukrokrela ukuba usana lwakho lunesi sifo, baya kuyala uvavanyo lwegazi ukumisela inani leeseli ezibomvu kwigazi lomntwana wakho.

Olunye uvavanyo lunokuba yimfuneko ukufikelela kwisifo. Oku kunokubandakanya:

• ubalo lwegazi olupheleleyo (CBC) ukujonga onke amacandelo egazi
• Uvavanyo lwe-bilirubin ukukhangela inqanaba le-bilirubin emzimbeni
• Ukuvavanywa komchamo ukulinganisa iswekile, igazi kunye neprotein kumchamo
• uvavanyo lweswekile egazini ukujonga amanqanaba eswekile yegazi
• uvavanyo lwe-creatinine ukulinganisa ukusebenza kwezintso
• Uvavanyo lwegesi yegazi ukukhangela amanqanaba eoksijini egazini
• Uvavanyo lomsebenzi wesibindi ukujonga inqanaba leeproteni zesibindi
• uvavanyo lwekhemesti yegazi ukukhangela ibhalansi yemichiza yegazi

Kwakhona, ugqirha wakho unokufumanisa ukuba usana lwakho luhlangabezana nezinto ezinjenge-jaundice, ukusilela kwezintso, okanye iingxaki zokuphefumla ngenxa yesifo.

Inyangwa njani i-hyperviscosity syndrome?

Ukuba ugqirha womntwana wakho ugqiba ukuba umntwana wakho une-hyperviscosity syndrome, umntwana wakho uya kujongwa ngeengxaki ezinokubakho.

Ukuba imeko inzima, ugqirha wakho unokucebisa ukutshintshwa kotshintshiselwano. Ngethuba lale nkqubo, intwana yegazi isuswa kancinci. Ngelo xesha, isixa esithathiweyo sithathwa endaweni yesisombululo se-saline. Oku kwehlisa inani elipheleleyo leeseli ezibomvu zegazi, lenze igazi lingqindilili, ngaphandle kokuphulukana nomthamo wegazi.

Ugqirha wakho unokuphinda acebise ukondla rhoqo komntwana wakho ukuphucula i-hydration kunye nokunciphisa ubukhulu begazi. Ukuba umntwana wakho akaphenduli kwi-feedings, banokufuna ukufumana ulwelo ngaphakathi.

Kubantu abadala, isifo sehyperviscosity syndrome sihlala sibangelwa yimeko engaphantsi njengeleukemia. Imeko leyo kufuneka inyangwe ngokufanelekileyo kuqala ukubona ukuba oku kuyayiphucula i-hyperviscosity. Kwiimeko ezinzima, iplasmapheresis inokusetyenziswa.

Ithini imbono yexesha elide?

Ukuba umntwana wakho unetyala elincinci le-hyperviscosity syndrome kwaye akukho zimpawu, abanokufuna unyango kwangoko. Kukho ithuba elihle lokufumana kwakhona ngokupheleleyo, ngakumbi ukuba unobangela ubonakala okwethutyana.

Ukuba unobangela unxulumene nemeko yemfuza okanye yelifa, inokufuna unyango lwexesha elide.

Abanye abantwana abaye bafumanisa ukuba banesi sifo baneengxaki zokukhula okanye zemithambo-luvo kamva. Esi sisiphumo sokunqongophala kokuhamba kwegazi kunye neoksijini kwingqondo nakwamanye amalungu abalulekileyo.

Nxibelelana nogqirha wosana lwakho ukuba ubona naluphi na utshintsho kwindlela yokuziphatha kosana lwakho, iipateni zokondla, okanye indlela yokulala.

Iingxaki zinokwenzeka ukuba imeko inzima kakhulu okanye ukuba umntwana wakho akaphenduli kunyango. Ezi ngxaki zinokubandakanya:

• ukubetha
• ukusilela kwezintso
• ukuncipha kolawulo lweemoto
• ukulahleka kokuhamba
• ukufa kwamathambo emathumbu
• ukuxhuzula okuphindaphindayo

Qiniseka ukuba uxela naziphi na iimpawu umntwana wakho aya kugqirha ngoko nangoko.

Kubantu abadala, isifo se-hyperviscosity sihlala sihambelana nengxaki yonyango.

Ulawulo olululo lwazo naziphi na izifo eziqhubekayo, kunye negalelo elivela kwingcali yegazi, zezona ndlela zilungileyo zokunciphisa iingxaki kule meko.