Ukuphazamiseka kwiLipid Metabolism
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Umxholo
Isishwankathelo
I-Metabolism yinkqubo oyisebenzisayo umzimba wakho ukwenza amandla kukutya okutyayo. Ukutya kwenziwa ngeeproteni, ii-carbohydrate kunye namafutha. Iikhemikhali kwinkqubo yakho yokwetyisa (ii-enzymes) ziqhekeza iindawo zokutya zibe ziiswekile neeasidi, amafutha omzimba wakho. Umzimba wakho ungawasebenzisa la mafutha ngoko nangoko, okanye unokugcina amandla kwizicwili zomzimba wakho. Ukuba unengxaki yokuphazamiseka emzimbeni, kukho into ehamba gwenxa ngale nkqubo.
Iingxaki ze-Lipid metabolism, ezifana nesifo seGaucher kunye nesifo seTay-Sachs, zibandakanya i-lipids. I-Lipids ngamafutha okanye izinto ezinjengeoli. Babandakanya iioyile, iiasidi ezinamanqatha, iinyithi, kunye necholesterol. Ukuba unesinye sezi ngxaki, awunakho ukufumana i-enzyme eyaneleyo yokuphula i-lipids. Okanye ii-enzymes zisenokungasebenzi kakuhle kwaye umzimba wakho awunako ukuguqula amanqatha abe ngamandla. Zibangela inani eliyingozi leepids ukwakha emzimbeni wakho. Ixesha elingaphezulu, elinokonakalisa iiseli zakho kunye nezicubu, ngakumbi kwingqondo, inkqubo ye-neripheral nervous, isibindi, udakada, kunye nomongo wethambo. Uninzi lwezi ngxaki lunokuba lubi kakhulu, okanye ngamanye amaxesha lubulale.
Ezi ngxaki zizuzwe njengelifa. Iintsana ezisandul 'ukuzalwa zivavanywa ezinye zazo, kusetyenziswa iimvavanyo zegazi. Ukuba kukho imbali yosapho yenye yezi ngxaki, abazali banokufumana uvavanyo lwemfuzo ukubona ukuba bayayiphatha na imfuza. Olunye uvavanyo lwezofuzo lunokuxela ukuba ngaba umntwana okhulelweyo unesifo okanye uphethe ufuzo lwesifo.
Unyango olungena endaweni ye-enzyme lunokunceda ezimbalwa kwezi ngxaki. Kwabanye, akukho lonyango. Amayeza, utofelo-gazi, kunye nezinye iinkqubo zinokunceda kwiingxaki.