Rhabdomyosarcoma: yintoni, iimpawu, iintlobo kunye nendlela yokunyanga

Umxholo
IRhabdomyosarcoma luhlobo lomhlaza olukhula kwizicubu ezithambileyo, ezichaphazela ikakhulu abantwana kunye nolutsha ukuya kwiminyaka eli-18 ubudala. Olu hlobo lomhlaza lunokubonakala phantse kuwo onke amalungu omzimba, kuba lukhula apho kukho umsipha wamathambo, nangona kunjalo, unokubonakala nakwamanye amalungu afana nesinyi, iprostate okanye ubufazi.
Ngokwesiqhelo, i-rhabdomyosarcoma yenziwa ngexesha lokukhulelwa, nokuba kukwisigaba se-embryonic, apho iiseli eziya kuthi zivelise imisipha yamathambo ziba mandundu kwaye ziqale ukuphindaphindeka ngaphandle kolawulo, zibangele umhlaza.
I-Rhabdomyosarcoma iyanyangeka xa isifo kunye nonyango lwenziwa kwinqanaba lokuqala lokukhula kwesisu, kunye nethuba lokunyanga xa unyango luqalwa kwakamsinya emva kokuzalwa komntwana.

Iindidi zeradiomyosarcoma
Zimbini iintlobo eziphambili ze-rhabdomyosarcoma:
- Umbindi we-rhabdomyosarcoma, lolona hlobo luqhelekileyo lomhlaza kwaye kwenzeka kakhulu kwiintsana nasebantwaneni. I-embryonic rhabdomyosarcoma ithambekele ekuphuculweni kwindawo yentloko, intamo, isinyi, ubufazi, iprostate kunye namasende;
- IAlveolar rhabdomyosarcoma, eyenzeka rhoqo kubantwana abadala nakwishumi elivisayo, echaphazela ikakhulu izihlunu zesifuba, iingalo nemilenze. Lo mhlaza ufumana igama lawo ngenxa yokuba iiseli zethumba zenza iindawo ezincinci ezixhotyiweyo kwimisipha, ebizwa ngokuba yialveoli.
Ukongeza, xa i-rhabdomyosarcoma ikhula kumasende, yaziwa ngokuba yi-parabesticular rhabdomyosarcoma, exhaphake kakhulu ebantwini ukuya kuthi ga kwi-20 yeminyaka kwaye ihlala ikhokelela ekudumbeni kunye neentlungu kwi-testicle. Zazi ezinye izizathu zokudumba kwamasende
Iimpawu zerhabdomyosarcoma
Iimpawu zerhabdomyosarcoma ziyahluka ngokobungakanani kunye nendawo yethumba, enokuba:
- Ubunzima obunokubonwa okanye ukuziva kwingingqi kwimilenze, entloko, esiqwini okanye emgodini;
- Ukudinwa, ukuba ndindisholo kunye nentlungu emilenzeni;
- Intloko rhoqo;
- Ukopha empumlweni, emqaleni, kwilungu lobufazi okanye kwilayini;
- Ukugabha, iintlungu zesisu kunye nokuqhinwa emathunjini, kwimeko yamathumba esiswini;
- Amehlo atyheli kunye nolusu, kwimeko yamathumba kwimibhobho yenyongo;
- Intlungu yethambo, ukukhohlela, ubuthathaka kunye nokwehla kobunzima, xa i-rhabdomyosarcoma ikwinqanaba eliphambili.
Ukuxilongwa kwe-rhabdomyosarcoma kwenziwa ngokuvavanywa kwegazi kunye nomchamo, ii-X-reyi, ikhompyuter yecomputer, imaging resonance imaging kunye ne-tumor biopsy ukujonga ubukho beeseli zomhlaza kunye nokuchonga ubungakanani besifo sethumba. Ukuxelwa kwangaphambili kwe-rhabdomyosarcoma kuyahluka ukusuka komnye umntu ukuya komnye, nangona kunjalo, kwangoko ukuxilongwa kwenziwa kwaye unyango luqala, kokukhona amathuba okunyanga kunye nokuncipha kwento yokuba eli thumba liza kuvela xa sele umdala.
Unyango lwenziwa njani
Unyango lwe-rhabdomyosarcoma kufuneka luqale ngokukhawuleza, kucetyiswa ngugqirha oqhelekileyo okanye ugqirha wabantwana, kwimeko yabantwana nakwishumi elivisayo. Ngokwesiqhelo, utyando lokususa ithumba luye lubonakaliswe, ngakumbi xa isifo singekafiki kwamanye amalungu.
Ukongeza, ichemotherapy kunye nonyango lwemitha zingasetyenziswa ngaphambi okanye emva kotyando ukuzama ukunciphisa ubungakanani be-tumor kunye nokuphelisa i-metastases emzimbeni.
Unyango lwe-rhabdomyosarcoma, xa lwenziwa ebantwaneni okanye kulutsha, lunokuba neziphumo ezithile ekukhuleni nasekukhuleni, kubangele iingxaki zemiphunga, ukulibaziseka ekukhuleni kwethambo, utshintsho kuphuhliso lwezesondo, ukungachumi okanye iingxaki zokufunda.