Iimpawu zeHugles-Stovin Syndrome kunye nonyango

Umxholo

• Iimpawu
• Unyango
• Iingxaki

I-Hugles-stovin syndrome sisifo esinqabileyo kwaye esibi esibangela ii-aneurysms ezininzi kwimithambo ye-pulmonary kunye neemeko ezininzi ze-vein thrombosis enzulu ngexesha lobomi. Ukusukela kwinkcazo yokuqala yesi sifo kwihlabathi liphela, abantu abangaphantsi kwama-40 sele befumanekile ngonyaka we-2013.

Esi sifo sinokuzibonakalisa ngokwamanqanaba ama-3 ahlukeneyo, apho esokuqala sihlala siveliswa yi-thrombophlebitis, inqanaba lesibini nge-pulmonary aneurysms, kwaye inqanaba lesithathu nelokugqibela libonakaliswa kukophuka kwe-aneurism kunokubangela ukukhohlela kwegazi kunye nokufa.

Owona gqirha ufanelekileyo ukuba asichaze kwaye asinyange esi sifo yingcali ye-rheumatologist kwaye nangona unobangela wayo ungekaziwa ngokupheleleyo, kukholelwa ukuba inokuba inxulumene ne-vasculitis yenkqubo.

Iimpawu

Iimpawu ze-Hugles-stovin zibandakanya:

• Ukukhohlela igazi;
• Ubunzima bokuphefumla;
• Ukuziva uphefumla kancinci;
• Intloko ebuhlungu;
• Umkhuhlane ophezulu, oqhubekayo;
• Ukuphulukana ne-10% yesisindo ngaphandle kwesizathu esibonakalayo;
• I-Papillidema, okuthoba i-optic papilla emele ukwanda koxinzelelo ngaphakathi kwengqondo;
• Ukudumba kunye neentlungu ezinzima ithole;
• Umbono ophindwe kabini kunye
• Ukuxhuzula.

Ngokwesiqhelo umntu one-Hugles-stovin syndrome uneempawu zeminyaka emininzi kwaye isifo sinokudideka nesifo sika-Behçet kwaye abanye abaphandi bakholelwa ukuba esi sifo sisigulo esingaphelelanga sesifo sika-Behçet.

Esi sifo kunqabile ukuba sifunyanwe ebuntwaneni kwaye sinokufunyanwa kwinqanaba lokufikisa okanye ebudaleni emva kokubonisa iimpawu esele zikhankanyiwe kunye nokwenza iimvavanyo ezinje ngovavanyo lwegazi, i-X-ray yesifuba, ii-MRIs okanye i-computed tomography yentloko nesifuba, ukongeza kwi-doppler ultrasound ukujonga ukujikeleza kwegazi nentliziyo. Akukho sikhombisi sokuchonga isifo kwaye ugqirha kufuneka ayirhanele le syndrome ngenxa yokufana kwayo nesifo sika-Behçet, kodwa ngaphandle kwazo zonke iimpawu zayo.

Iminyaka yabantu abafunyaniswe ukuba banesi sifo iyahluka phakathi kweminyaka eyi-12 ukuya kuma-48.

Unyango

Unyango lwe-Hugles-Stovin syndrome aluchazi ngokuthe ngqo, kodwa ugqirha unokucebisa ukuba kusetyenziswe ii-corticosteroids ezinje ngehydrocortisone okanye i-prednisone, ii-anticoagulants ezifana ne-enoxaparin, unyango lwe-pulse kunye ne-immunosuppressants ezinje nge-Infliximab okanye i-Adalimumab enokunciphisa umngcipheko kunye neziphumo ye-aneurysms kunye ne-thrombosis, ngaloo ndlela kuphuculwe umgangatho wobomi kunye nokunciphisa umngcipheko wokufa.

Iingxaki

Isifo i-Hugles-Stovin sinokuba nzima ukunyangwa kwaye sinokusweleka okuphezulu kuba unobangela wesifo awaziwa kwaye ke unyango alunakwanela ukugcina impilo yomntu ochaphazelekayo. Njengoko zimbalwa iimeko ezinokuchongwa kwihlabathi liphela, oogqirha bahlala bengasiqhelanga esi sifo, esinokwenza ukuba ukuxilongwa kunye nonyango kube nzima ngakumbi.

Ukongeza, ii-anticoagulants kufuneka zisetyenziswe ngononophelo olukhulu kuba kwezinye iimeko zinokunyusa umngcipheko wokopha emva kokuqhekeka kwe-aneurysm kunye nokuvuza kwegazi kunokuba kukhulu kangangokuba kuthintela ukugcinwa kobomi.