Umbhali: Lewis Jackson
Umhla Wokudalwa: 5 Ucanzibe 2021
Hlaziya Umhla: 25 Isilimela 2024
Anonim
Iinketho zonyango lwe-Idiopathic Pulmonary Fibrosis (IPF) - Zempilo
Iinketho zonyango lwe-Idiopathic Pulmonary Fibrosis (IPF) - Zempilo

Umxholo

I-Idiopathic pulmonary fibrosis (IPF) sisifo semiphunga esibangelwa kukwakheka kwezicubu ezibomvu ngaphakathi kwimiphunga.

Ukuqhekeka kuya kusiba ngokuthe ngcembe. Oku kwenza kube nzima ngakumbi ukuphefumla kunye nokugcina amanqanaba afanelekileyo eoksijini kwigazi.

Ukuqhubeka kwamanqanaba eoksijini asezantsi kubangela iingxaki ezahlukeneyo emzimbeni wonke. Uphawu oluphambili kukuphefumla okuphefumlayo, oku kunokukhokelela ekudinweni nakwezinye iingxaki.

Unyango lwakwangoko lwe-idiopathic pulmonary fibrosis (IPF)

I-IPF sisifo esiqhubela phambili, oko kuthetha ukuba iimpawu ziya zisiba mandundu ngokuhamba kwexesha, kwaye unyango kwangoko lubalulekile. Okwangoku akukho nyango lwe-IPF, kwaye amanxeba akanakuguqulwa okanye asuswe.

Nangona kunjalo, unyango lukhona olukunceda:

  • ukuxhasa indlela yokuphila esempilweni
  • ukulawula iimpawu
  • ukuqhubela phambili kwesifo kancinci
  • gcina umgangatho wobomi

Zeziphi iintlobo zamayeza ezikhoyo?

Unyango olunokunyanga lubandakanya amayeza amabini avunyiweyo okubulala iintsholongwane.


IPirfenidone

I-Pirfenidone sisiyobisi esichasene ne-antifibrotic esinokucothisa ukuqhubela phambili kokonakala kwethishu yemiphunga. Inepropathi yokubulala intsholongwane, anti-ukudumba, kunye ne-antioxidant.

IPirfenidone idityaniswe ne:

  • ukuphucula amanqanaba okusinda

UNintedanib

I-Nintedanib lelinye ichiza elichasene ne-antibibrotic elifana ne-pirfenidone eboniswe kwizilingo zeklinikhi ukucothisa ukuqhubela phambili kwe-IPF.

Kubantu abaninzi abane-IPF abangenaso isifo sesibindi, i-pirfenidone okanye i-nintedanib yonyango olwamkelweyo.

Idatha yangoku ayonelanga ukukhetha phakathi kwepirfenidone kunye nintedanib.

Xa ukhetha phakathi kwezi zibini, ukhetho lwakho kunye nokunyamezelana kufuneka kuthathelwe ingqalelo, ngakumbi ngokubhekisele kwiziphumo ezibi ezinokubakho.

Oku kubandakanya urhudo kunye nokuvavanywa kokusebenza kwesibindi ngokungaqhelekanga kunye ne-nintedanib kunye ne-nausea kunye ne-rash nge-pirfenidone.

Iipilisi zeCorticosteroid

I-Corticosteroids, njenge-prednisone, inokunciphisa ukuvuvukala emiphungeni kodwa ayisekho yinxalenye eqhelekileyo yolondolozo lwesiqhelo kubantu abane-IPF njengoko bengakhange babonakalise ukuba bayasebenza okanye bakhuselekile.


N-Acetylcysteine ​​(ngomlomo okanye nge-aerosolized)

I-N-Acetylcysteine ​​yi-antioxidant eye yafundwa ukuba isetyenziswe kubantu abafumene i-IPF. Iziphumo ezivela kuvavanyo lweklinikhi zixutywe.

Ngokufana ne-corticosteroids, i-N-Acetylcysteine ​​ayisasetyenziswa njengesiqhelo kulondolozo lwesiqhelo.

Olunye unyango olunokubakho lubandakanya:

  • Iiproton pump inhibitors, esivimba isisu ekuveliseni i-asidi (inhalation yesisu esiswini esigqithileyo sinxibelelene negalelo kwi-IPF)
  • ukucinezela amajoni omzimba, njenge-mycophenolate kunye ne-azathioprine, enokuthi inyange ukuphazamiseka komzimba kunye nokunceda ukuthintela ukwaliwa kwemiphunga efakelweyo

Unyango lweoksijini lwe-IPF

Ugqirha wakho unokucebisa nezinye iindlela zonyango. Unyango lweoksijini lunokukunceda uphefumle lula, ngakumbi ngexesha lokuzilolonga kunye neminye imisebenzi.

Ukongezwa kweoksijini kunokunciphisa iingxaki ezinxulumene namanqanaba asezantsi eoksijini egazini njengokudinwa kwixesha elifutshane.


Ezinye izibonelelo zisafundwa.

Ukutshintshwa kwemiphunga ye-IPF

Unokuba ngumgqatswa wofakelo lwemiphunga. Ukufakelwa kwemiphunga kwakugcinelwe abamkeli abancinci. Kodwa ngoku zihlala zinikezelwa kubantu abangaphezu kweminyaka engama-65 abasempilweni ngenye indlela.

Unyango lovavanyo

Kukho unyango oluninzi olunokubakho lwe-IPF phantsi kophando.

Unokhetho lokufaka isicelo kwizilingo ezahlukeneyo zeklinikhi ezijonga iindlela ezintsha zokuthintela, ukufumanisa isifo, nokunyanga uluhlu lwezifo zemiphunga, kubandakanya ne-IPF.

Unokufumana uvavanyo lwezonyango kwiCentreWatch, elandelela uphando olukhulu kwizihloko ezinokukhangelwa.

Inika ulwazi malunga nokuba uvavanyo lwezonyango lusebenza njani, umngcipheko kunye nezibonelelo, kunye nokunye.

Zeziphi iindlela zongenelelo ngoncedo ezinokunceda?

Utshintsho kwindlela yokuphila kunye nolunye unyango olungenonyango kunokukunceda uhlale usempilweni kwaye uphucule umgangatho wobomi bakho.

Nazi ezinye iingcebiso.

Ukunciphisa umzimba okanye ukugcina ubunzima obunempilo

Thetha nogqirha wakho malunga neendlela ezisempilweni zokunciphisa okanye zokulawula ubunzima bakho. Ukutyeba kakhulu ngamanye amaxesha kunokuba negalelo kubunzima bokuphefumla.

Yeka ukutshaya

Ukutshaya yenye yezona zinto zimbi onokuzenza kwimiphunga yakho. Ngoku, kunanini na ngaphambili, kubalulekile ukuba uyeke lo mkhwa ungonakalisi ngakumbi.

Fumana ugonyo lonyaka

Thetha nogqirha wakho malunga nomkhuhlane waminyaka le kunye ne-pneumonia ehlaziyiweyo kunye nokugonya okukhohlela (pertussis). Oku kunokunceda ukukhusela imiphunga yakho kusulelo nakumonakalo ongaphezulu.

Jonga amanqanaba akho eoksijini

Sebenzisa i-oximeter yasekhaya yokujonga ukubonwa kweoksijini. Rhoqo injongo kukuba namanqanaba eoksijini okanye ngaphezulu kweepesenti ezingama-90.

Thatha inxaxheba kwimo yesiqhelo yokubuyisela kwimo yesiqhelo kwimiphunga

Ukuvuselelwa kwenkqubo ye-pulmonary yinkqubo emininzi eyeyona nto iphambili kunyango lwe-IPF. Ijolise ekuphuculeni ubomi bemihla ngemihla kubantu abane-IPF kunye nokunciphisa ukuphefumla kancinci ekuphumleni nasekuzilolongeni.

Iimpawu eziphambili zibandakanya:

  • ukuphefumla kunye nokuzilolonga
  • uxinzelelo kunye noxinzelelo kulawulo
  • inkxaso yemvakalelo
  • iingcebiso ngezondlo
  • imfundo yesigulana

Zeziphi iindidi zamaqela enkxaso ezikhoyo?

Kukho iinkqubo zokuxhasa. Oku kunokwenza umahluko omkhulu kumgangatho wobomi kunye nembonakalo malunga nokuhlala ne-IPF.

I-Pulmonary Fibrosis Foundation ine-database enokuphandwa yamaqela enkxaso yendawo kunye noluntu oluninzi kwi-Intanethi.

Ezi zixhobo zibaluleke kakhulu njengoko uza kumgaqo wokufumanisa isifo kunye notshintsho olunokubuzisa ebomini bakho.

Iyintoni imbono yabantu abane-IPF?

Ngelixa lungekho unyango lwe-IPF, kukho iindlela zokhetho zokulawula iimpawu zakho kunye nokuphucula umgangatho wobomi bakho. Oku kubandakanya:

  • iziyobisi
  • ungenelelo lonyango
  • utshintsho kwindlela yokuphila

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