Uvavanyo lomchamo wePorphyrins

Iiporphyrins ziikhemikhali zendalo emzimbeni ezinceda ekwenzeni izinto ezininzi ezibalulekileyo emzimbeni. Enye yazo yihemoglobin, iproteni ekwiiseli ezibomvu zegazi ezithwala ioksijini egazini.

Iiporphyrins zinokulinganiswa kumchamo okanye egazini. Eli nqaku lixoxa ngovavanyo lomchamo.

Emva kokubonelela ngesampulu yomchamo, iyavavanywa elebhu. Oku kubizwa ngokuba sisampulu yomchamo.

Ukuba kuyimfuneko, umboneleli wakho wezempilo unokucela ukuba uqokelele umchamo wakho ekhaya ngaphezulu kweeyure ezingama-24. Oku kubizwa ngokuba ngumzekelo weeyure ezingama-24. Umboneleli wakho uya kukuxelela ukuba ungayenza njani le nto. Landela imiyalelo ngokuchanekileyo ukuze iziphumo zichaneke.

Umboneleli wakho angakuxelela ukuba uyeke okwexeshana amayeza anokuchaphazela iziphumo zovavanyo. Oku kunokubandakanya:

• Amayeza okubulala iintsholongwane kunye neziyobisi ezichasene nokungunda
• Iziyobisi ezichasene noxinzelelo
• Iipilisi zokulawula inzala
• Amayeza eswekile
• Amayeza entlungu
• Amayeza okulala

Sukuyeka ukuthatha nawaphi na amayeza ngaphandle kokuqala uthethe nomboneleli wakho.

Olu vavanyo lubandakanya kuphela ukuchama okuqhelekileyo kwaye akukho kungahambi kakuhle.

Umboneleli wakho uya kuyalela olu vavanyo ukuba uneempawu ze-porphyria okanye ezinye iingxaki ezinokubangela umchamo ongaqhelekanga we-porphyrins.

Iziphumo eziqhelekileyo ziyahluka ngokuxhomekeka kuhlobo lwe-porphyrin evavanyiweyo. Ngokubanzi, kuvavanyo lomchamo lweeyure ezingama-24 lwee-porphyrins zizonke, uluhlu lumalunga ne-20 ukuya kwi-120 µg / L (25 ukuya kwi-144 nmol / L).

Amaxabiso esiqhelo ahluka kancinci phakathi kweelebhu ezahlukeneyo. Ezinye iilebhu zisebenzisa imilinganiselo eyahlukeneyo okanye zinokuvavanya iisampulu ezahlukeneyo. Thetha nomboneleli wakho malunga nentsingiselo yeziphumo zakho zovavanyo.

Iziphumo ezingaqhelekanga zinokubangelwa:

• Umhlaza wesibindi
• Hepatitis
• Ityhefu yelothe
• IPorphyria (iintlobo ezininzi)

Akukho bungozi kolu vavanyo.

Umchamo uroporphyrin; Umchamo coproporphyrin; Porphyria - uroporphyrin

• Iphecana lomchamo labasetyhini
• Indoda yokuchama
• Uvavanyo lomchamo wePorphyrin

I-SJ epheleleyo, iWiley JS. I-Heme biosynthesis kunye nokuphazamiseka kwayo: i-porphyrias kunye ne-sideroblastic anemias. Ku: Hoffman R, Benz EJ, Silberstein LE, et al, ii-eds. I-Hematology: Imigaqo esisiseko kunye nokuziqhelanisa. Umhla wesi-7. IPhiladelphia, PA: Elsevier; I-2018: isahluko 38.

URiley RS, uMcPherson RA. Uvavanyo olusisiseko lomchamo. Ku: McPherson RA, Pincus MR, ii-eds. Ukuchongwa kweKlinikhi kaHenry kunye noLawulo ngeendlela zeLebhu. Umhla we-23. ISt Louis, MO: Elsevier; Ngo-2017: isahluko 28.