Umbhali: John Pratt
Umhla Wokudalwa: 15 Eyomdumba 2021
Hlaziya Umhla: 1 Eyekhala 2024
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Yintoni i-angiomyolipoma yezintso, ziziphi iimpawu kunye nendlela yokunyanga - Zempilo
Yintoni i-angiomyolipoma yezintso, ziziphi iimpawu kunye nendlela yokunyanga - Zempilo

Umxholo

I-renal angiomyolipoma sisifo esinqabileyo nesinobungozi esichaphazela izintso kwaye sinamafutha, imithambo yegazi kunye nezihlunu. Izizathu azichazwanga ngokuthe ngqo, kodwa ukubonakala kwesi sifo kunokunxulunyaniswa notshintsho lwemfuza kunye nezinye izifo kwizintso. Nangona i-angiomyolipoma ixhaphake kakhulu kwizintso, inokwenzeka nakwamanye amalungu omzimba.

Uninzi lwexesha, i-angiomyolipoma yezintso ayibangeli zimpawu, kodwa ukuba inkulu kune-4 cm inokubangela ukopha kwizintso kwaye kwezi meko iintlungu zomqolo, isicaphucaphu, ukonyuka koxinzelelo lwegazi kunye negazi kumchamo.

Ukuxilongwa kuhlala kwenzeka ngamabona-ndenzile, emva kokwenza uvavanyo lwe-imaging ukuphanda esinye isifo, kwaye unyango luchazwa ngugqirha wezonyango emva kokuqinisekisa ubungakanani be-angiomyolipoma kwizintso.

Iimpawu eziphambili

Kwiimeko ezininzi, i-angiomyolipoma ayibangeli zimpawu. Nangona kunjalo, xa i-angiomyolipoma ithathwa ngokuba inkulu, oko kukuthi, ingaphezulu kwe-4 cm, inokuvelisa iimpawu ezinje:


  • Intlungu kwingingqi yesisu;
  • Umchamo wegazi;
  • Usulelo rhoqo lomchamo;
  • Ukunyusa uxinzelelo lwegazi.

Ukongeza, iimpawu zixhaphake xa olu hlobo lwethumba lubangela ukopha kwizintso. Kwiimeko ezinjalo, iimpawu zinokubandakanya ukwehla ngesiquphe koxinzelelo lwegazi, iintlungu zesisu esibuhlungu, ukuziva utyhafile kunye nolusu olukhanyayo.

Indlela yokuqinisekisa ukuxilongwa

Ukuqinisekisa ukuxilongwa kwe-angiomyolipoma ye-renal, i-nephrologist inokuyalela iimvavanyo ezithile ze-imaging ezinje nge-angiography, i-ultrasound, i-computed tomography kunye ne-magnetic resonance.

Ukudumba kwe-angiomyolipoma ye-renal kulula ukuyixilonga xa yenziwe ngamanqatha, kwaye kwimeko apho kukho umxholo wamafutha asezantsi okanye ukopha okwenza kube nzima ukubona kwiimviwo zokucinga, i-nephrologist inokucela i-biopsy. Fumanisa ngakumbi malunga nokuba yintoni kunye nendlela eyenziwa ngayo i-biopsy.

Unyango lwenziwa njani

Emva kokwenza iimviwo, i-nephrologist iya kuchaza unyango ngokweempawu zezilonda zezintso. Xa i-tumor ye-angiomyolipoma ye-renal incinci kune-4 cm, ukubeka esweni ukukhula kuhlala kwenziwa ngeemviwo zokucinga ngonyaka.


Amachiza abonakaliswe kakhulu kunyango lwe-angiomyolipoma yezintso zii-immunosuppressants ze-everolimus kunye ne-sirolimus ethi, ngezenzo zabo, incede ukunciphisa ubungakanani besisu.

Nangona kunjalo, ukuba i-angiomyolipoma yezintso inkulu kune-4 cm okanye ukuba ibangela iimpawu ezibi kakhulu, ukubethelwa kuhlala kubonisiwe, eyinkqubo yokunciphisa ukuhamba kwegazi kunye nokunceda ukunciphisa ithumba. Ukongeza, utyando lokususa ithumba kunye nenxalenye echaphazelekayo yezintso inokubonakaliswa ukuze kuthintelwe eli thumba ukuba lingaphuli kwaye libangele ukopha.

Xa i-angiomyolipoma yezintso ivelisa iimpawu zokopha ezinje ngokuhla koxinzelelo lwegazi, ulusu olukhanyayo kunye nokuziva utyhafile, kuya kufuneka uye esibhedlele kwangoko ukuya kuqinisekisa isifo kwaye, ukuba kukho imfuneko, kufuneka wenze utyando olungxamisekileyo ukunqanda ukopha kwizintso.

Izizathu ezinokubangela

Izizathu ze-angiomyolipoma yezintso azichazwanga ngokucacileyo, kodwa ukuqala kuhlala kunxulunyaniswa nesinye isifo, esifana nesifo sokuqina kwemithambo. Qonda ukuba yintoni i-tuberous sclerosis kunye neempawu zayo.


Ngokubanzi, i-angiomyolipoma yezintso inokukhula nakubani na, kodwa abantu basetyhini banokuphuhlisa amathumba amakhulu ngenxa yokutshintshwa kwehomoni yabasetyhini okanye ukukhutshwa kwehomoni ngexesha lokukhulelwa.

Iimpapasho Ezinomdla

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