Umbhali: Morris Wright
Umhla Wokudalwa: 25 Utshazimpuzi 2021
Hlaziya Umhla: 1 Utshazimpuzi 2025
Anonim
Yintoni imastocytosis, iintlobo, iimpawu kunye nonyango - Zempilo
Yintoni imastocytosis, iintlobo, iimpawu kunye nonyango - Zempilo

Umxholo

I-Mastocytosis sisifo esinqabileyo esibonakaliswa kukunyuka kunye nokuqokelelwa kweeseli zemasti kulusu kunye nezinye izicubu zomzimba, ezikhokelela ekubonakaleni kwamabala kunye neendawo ezincinci ezibomvu-zimdaka kulusu olurhawuzayo kakhulu, ngakumbi xa kukho utshintsho kubushushu kunye xa ulusu lunxibelelana nempahla, umzekelo.

Iiseli ezincinci ziiseli eziveliswe kumongo wethambo, ezifumaneka kwizicubu zomzimba ezahlukeneyo ezinokuthi zihambelane nempendulo yomzimba, ngakumbi kwi-allergen response. Nangona kunjalo, ngokungafaniyo ne-aleji, imiqondiso kunye neempawu ze-mastocytosis zihlala zingahambelani kwaye azihambelani nezinto ezibangela.

Kubalulekile ukuba i-mastocytosis ichongwe kwaye inyangwe ngokwemiyalelo kagqirha, kuba kwezinye iimeko inokunxulumana nezinye iingxaki ezinzulu zegazi, ezinje nge-leukemia ebukhali, i-lymphoma, i-neutropenia engapheliyo kunye notshintsho lwe-myeloproliferative.

Iindidi zemastocytosis

I-Mastocytosis yenzeka xa iiseli zemasti zisanda kwaye ziqokeleleka emzimbeni kwaye, ngokuxhomekeke ekubeni ezi seli ziqokelelene phi, imastocytosis inokuhlelwa ibe:


  • I-mastocytosis esisikiweyo, apho iiseli zemasti ziqokelelana khona eluswini, zikhokelela ekubonakaleni kweempawu kunye neempawu ezinqamlezileyo, ngakumbi rhoqo ebantwaneni;
  • Inkqubo yemastocytosis, apho iiseli zemasti ziqokelela kwezinye izicwili zomzimba, ikakhulu kumongo wethambo, ziphazamise ukuveliswa kweeseli zegazi. Ukongeza, kolu hlobo lwe-mastocytosis, iiseli zemasti zinokuqokelelana kwisibindi, udakada, ulusu kunye neesisu, kwaye zinokuphazamisa, kwezinye iimeko, ekusebenzeni kwelungu.

Ukusukela ngalo mzuzu xa kukho inani elikhulu leeseli zemasti esizeni, iimpawu kunye neempawu ezibonisa ukuba isifo siyabonakala, kwaye kubalulekile ukudibana nogqirha ukuze kwenziwe uvavanyo lokugqiba isifo kunye nokuqala unyango olufanelekileyo.

Iimpawu kunye neempawu zemastocytosis

Iimpawu kunye neempawu zemastocytosis zinokwahluka ngohlobo kwaye zinxulumene noxinzelelo lwe-histamine ejikelezayo. Kungenxa yokuba iiseli zemasti zenziwe ngamagrafu akhupha i-histamine. Ke, ukuphakama kokuxinana kweeseli zemasti, kokukhona uxinzelelo lwe-histamine, olukhokelela kwiimpawu kunye neempawu zemastocytosis, ezona ziphambili zezi:


  • I-urticaria enamabala, amancinci amachokoza abomvu abomdaka eluswini anokutshiza;
  • Isilonda Peptic;
  • Intloko ebuhlungu;
  • Ubambo:
  • Ukuphalaza;
  • Urhudo olungapheliyo;
  • Intlungu zesisu;
  • Ukuziva unesiyezi xa usukuma;
  • Iingono neminwe ebindayo.

Ngamanye amaxesha, iimpawu ze-mastocytosis zinokuba mandundu xa kukho utshintsho kubushushu, emva kokutya ukutya okushushu kakhulu okanye okunesonka okanye iziselo, emva kokuzilolonga, emva koqhakamshelwano neempahla okanye ngenxa yokusebenzisa amanye amayeza.

Ukuchongwa kwemastocytosis kwenziwa kusetyenziswa uvavanyo lwegazi olujolise ekuchongeni amanqanaba e-histamine kunye ne-prostaglandin D2 egazini, ekufuneka iqokelelwe kwangoko emva kwengxaki, okanye kumchamo weeyure ezingama-24.

Ukongeza, kwimeko ye-mastocytosis enqamlezileyo, kungenziwa novavanyo lwe-histological, apho kuqokelelwa khona isampulu encinci yesilonda kwaye ithunyelwe elebhu ukuba ihlolwe kwaye kujongwe ukuba kukho inani elonyukayo leeseli zemasti kwizihlunu. .


Unjani unyango

Unyango lwe-mastocytosis kufuneka lukhokelwe yi-immunoallergologist okanye ugqirha ngokubanzi ngokwamanqanaba e-histamine ejikelezayo, imbali yezempilo yomntu kunye neempawu kunye neempawu.

Kwiimeko ezininzi, ugqirha unokucebisa ukuba kusetyenziswe amayeza ukunciphisa iimpawu, ngakumbi ii-antihistamines kunye ne-corticosteroid creams kunye namafutha. Nangona kunjalo, xa iimpawu ziba nzima kakhulu, ngakumbi xa kufikwa kwinkqubo ye-mastocytosis, unyango lunokuba nzima ngakumbi, kwaye kwezinye iimeko kunokufuneka kwenziwe utyando.

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